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Vulvar carcinoma

MedGen UID:
146159
Concept ID:
C0677055
Neoplastic Process
Synonyms: Cancer of the Vulva; Cancer of Vulva; carcinoma of mammalian vulva; Carcinoma of the Vulva; carcinoma of the vulva; Carcinoma of Vulva; Carcinoma of vulva; carcinoma of vulva; mammalian vulva carcinoma; Vulva Cancer; Vulva Carcinoma; vulva carcinoma; Vulvar Cancer; Vulvar Carcinoma; vulvar carcinoma
 
Monarch Initiative: MONDO:0005215
Orphanet: ORPHA494418

Definition

A group of rare tumors of the vulva comprising HPV-associated and HPV-independent squamous cell carcinomas as the most frequent malignant vulvar tumors, basal cell carcinomas, adenocarcinomas, and Bartholin gland carcinomas. Depending on the type of tumor and disease stage, patients may present with a painless vulvar mass or ulcer, or with pruritus, a burning sensation, pain, or bleeding. [from ORDO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVVulvar carcinoma

Professional guidelines

PubMed

Gaffney DK, King B, Viswanathan AN, Barkati M, Beriwal S, Eifel P, Erickson B, Fyles A, Goulart J, Harkenrider M, Jhingran A, Klopp A, Koh WJ, Lim K, Petersen I, Portelance L, Small W Jr, Stewart A, Wiebe E, Wolfson A, Yashar C, Bosch W
Int J Radiat Oncol Biol Phys 2016 Jul 15;95(4):1191-200. Epub 2016 Feb 21 doi: 10.1016/j.ijrobp.2016.02.043. PMID: 27130794Free PMC Article
Shrivastava SB, Agrawal G, Mittal M, Mishra P
Rev Recent Clin Trials 2015;10(4):289-97. doi: 10.2174/1574887110666150923112958. PMID: 26411952
Klemba A, Kowalewska M, Kukwa W, Tonska K, Szybinska A, Mossakowska M, Scinska A, Golik P, Koper K, Radziszewski J, Kukwa A, Czarnecka AM, Bartnik E
J Biomed Sci 2010 Sep 8;17(1):73. doi: 10.1186/1423-0127-17-73. PMID: 20825678Free PMC Article

Curated

NCCN Clinical Practice Guidelines in Oncology (NCCN Guidelines®), Vulvar Cancer, 2024

Recent clinical studies

Etiology

Thuijs NB, van Beurden M, Duin S, Heideman DAM, Berkhof J, Steenbergen RDM, Bleeker MCG
Histopathology 2024 Jan;84(2):301-314. Epub 2023 Sep 19 doi: 10.1111/his.15050. PMID: 37726173
Berenson AB, Chang M, Hawk ET, Ramondetta LM, Hoang T
Cancer Prev Res (Phila) 2022 Nov 1;15(11):777-784. doi: 10.1158/1940-6207.CAPR-22-0086. PMID: 35969832
Schleiss-Andreassen JL, Kristensen E, Frøding LP, Stæhr E, Høgdall C, Christiansen AP, Høgdall E, Schnack TH
Gynecol Oncol 2022 Mar;164(3):543-549. Epub 2021 Dec 29 doi: 10.1016/j.ygyno.2021.12.020. PMID: 34973843
Menczer J
Arch Gynecol Obstet 2017 Jan;295(1):9-15. Epub 2016 Oct 6 doi: 10.1007/s00404-016-4212-9. PMID: 27714462
Anderson JM, Cassady JR, Shimm DS, Stea B
Int J Radiat Oncol Biol Phys 1995 Jul 30;32(5):1351-7. doi: 10.1016/0360-3016(95)00090-L. PMID: 7635775

Diagnosis

Thuijs NB, van Beurden M, Duin S, Heideman DAM, Berkhof J, Steenbergen RDM, Bleeker MCG
Histopathology 2024 Jan;84(2):301-314. Epub 2023 Sep 19 doi: 10.1111/his.15050. PMID: 37726173
Grabinski E, Dunsmoor-Su R
Curr Opin Obstet Gynecol 2023 Apr 1;35(2):160-163. doi: 10.1097/GCO.0000000000000859. PMID: 36924411
Schleiss-Andreassen JL, Kristensen E, Frøding LP, Stæhr E, Høgdall C, Christiansen AP, Høgdall E, Schnack TH
Gynecol Oncol 2022 Mar;164(3):543-549. Epub 2021 Dec 29 doi: 10.1016/j.ygyno.2021.12.020. PMID: 34973843
Vaupel P, Piazena H, Müller W, Notter M
Int J Hyperthermia 2018;35(1):26-36. Epub 2018 May 10 doi: 10.1080/02656736.2018.1469169. PMID: 29745269
Gaffney DK, King B, Viswanathan AN, Barkati M, Beriwal S, Eifel P, Erickson B, Fyles A, Goulart J, Harkenrider M, Jhingran A, Klopp A, Koh WJ, Lim K, Petersen I, Portelance L, Small W Jr, Stewart A, Wiebe E, Wolfson A, Yashar C, Bosch W
Int J Radiat Oncol Biol Phys 2016 Jul 15;95(4):1191-200. Epub 2016 Feb 21 doi: 10.1016/j.ijrobp.2016.02.043. PMID: 27130794Free PMC Article

Therapy

Grabinski E, Dunsmoor-Su R
Curr Opin Obstet Gynecol 2023 Apr 1;35(2):160-163. doi: 10.1097/GCO.0000000000000859. PMID: 36924411
Berenson AB, Chang M, Hawk ET, Ramondetta LM, Hoang T
Cancer Prev Res (Phila) 2022 Nov 1;15(11):777-784. doi: 10.1158/1940-6207.CAPR-22-0086. PMID: 35969832
Naumann RW, Hollebecque A, Meyer T, Devlin MJ, Oaknin A, Kerger J, López-Picazo JM, Machiels JP, Delord JP, Evans TRJ, Boni V, Calvo E, Topalian SL, Chen T, Soumaoro I, Li B, Gu J, Zwirtes R, Moore KN
J Clin Oncol 2019 Nov 1;37(31):2825-2834. Epub 2019 Sep 5 doi: 10.1200/JCO.19.00739. PMID: 31487218Free PMC Article
Vaupel P, Piazena H, Müller W, Notter M
Int J Hyperthermia 2018;35(1):26-36. Epub 2018 May 10 doi: 10.1080/02656736.2018.1469169. PMID: 29745269
Gormley RH, Kovarik CL
Curr HIV/AIDS Rep 2009 Aug;6(3):130-8. doi: 10.1007/s11904-009-0018-8. PMID: 19589298

Prognosis

Chargari C, Wasserman J, Gabro A, Canlobre G, Spano JP, Uzan C, Maingon P
J Clin Oncol 2024 Mar 10;42(8):961-972. Epub 2024 Feb 5 doi: 10.1200/JCO.23.01187. PMID: 38315939
Berenson AB, Chang M, Hawk ET, Ramondetta LM, Hoang T
Cancer Prev Res (Phila) 2022 Nov 1;15(11):777-784. doi: 10.1158/1940-6207.CAPR-22-0086. PMID: 35969832
Clancy AA, Spaans JN, Weberpals JI
Ann Oncol 2016 Sep;27(9):1696-705. Epub 2016 Jun 20 doi: 10.1093/annonc/mdw242. PMID: 27329249
Kozakiewicz B, Dmoch-Gajzlerska E, Roszkowska-Purska K
Eur J Gynaecol Oncol 2014;35(3):243-9. PMID: 24984535
de Melo Maia B, Fontes AM, Lavorato-Rocha AM, Rodrigues IS, de Brot L, Baiocchi G, Stiepcich MM, Soares FA, Rocha RM
Hum Pathol 2014 May;45(5):917-25. Epub 2014 Jan 31 doi: 10.1016/j.humpath.2014.01.015. PMID: 24746196

Clinical prediction guides

Thuijs NB, van Beurden M, Duin S, Heideman DAM, Berkhof J, Steenbergen RDM, Bleeker MCG
Histopathology 2024 Jan;84(2):301-314. Epub 2023 Sep 19 doi: 10.1111/his.15050. PMID: 37726173
Dryden SM, Reshko LB, Gaskins JT, Silva SR
Cancer Rep (Hoboken) 2022 Oct;5(10):e21591. Epub 2022 Jan 24 doi: 10.1002/cnr2.1591. PMID: 35075817Free PMC Article
Schleiss-Andreassen JL, Kristensen E, Frøding LP, Stæhr E, Høgdall C, Christiansen AP, Høgdall E, Schnack TH
Gynecol Oncol 2022 Mar;164(3):543-549. Epub 2021 Dec 29 doi: 10.1016/j.ygyno.2021.12.020. PMID: 34973843
Naumann RW, Hollebecque A, Meyer T, Devlin MJ, Oaknin A, Kerger J, López-Picazo JM, Machiels JP, Delord JP, Evans TRJ, Boni V, Calvo E, Topalian SL, Chen T, Soumaoro I, Li B, Gu J, Zwirtes R, Moore KN
J Clin Oncol 2019 Nov 1;37(31):2825-2834. Epub 2019 Sep 5 doi: 10.1200/JCO.19.00739. PMID: 31487218Free PMC Article
Vaupel P, Piazena H, Müller W, Notter M
Int J Hyperthermia 2018;35(1):26-36. Epub 2018 May 10 doi: 10.1080/02656736.2018.1469169. PMID: 29745269

Recent systematic reviews

Lancellotta V, Macchia G, Garganese G, Fionda B, Fragomeni SM, D'Aviero A, Casà C, Gui B, Gentileschi S, Corrado G, Inzani F, Rovirosa A, Morganti AG, Gambacorta MA, Tagliaferri L
Clin Transl Oncol 2021 Aug;23(8):1611-1619. Epub 2021 Mar 1 doi: 10.1007/s12094-021-02557-1. PMID: 33650029
Te Grootenhuis NC, Pouwer AW, de Bock GH, Hollema H, Bulten J, van der Zee AGJ, de Hullu JA, Oonk MHM
Gynecol Oncol 2018 Mar;148(3):622-631. Epub 2017 Nov 12 doi: 10.1016/j.ygyno.2017.11.006. PMID: 29137809
Sznurkowski JJ
Eur J Cancer Care (Engl) 2016 Jul;25(4):638-46. Epub 2016 Feb 16 doi: 10.1111/ecc.12455. PMID: 26880231
van Seters M, van Beurden M, de Craen AJ
Gynecol Oncol 2005 May;97(2):645-51. doi: 10.1016/j.ygyno.2005.02.012. PMID: 15863172

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

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      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Curated

    • NCCN, 2024
      NCCN Clinical Practice Guidelines in Oncology (NCCN Guidelines®), Vulvar Cancer, 2024

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