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Epstein-Barr virus-associated malignant lymphoproliferative disorder

MedGen UID:
797800
Concept ID:
C2363744
Disease or Syndrome
Synonyms: EBV-associated lymphoproliferative disorder; EBV-Related Lymphoproliferative Disorder; Epstein-Barr Virus-Associated Lymphoproliferative Disorder; Epstein-Barr Virus-Related Lymphoproliferative Disorder
 
Monarch Initiative: MONDO:0017343
Orphanet: ORPHA289644

Definition

A lymphoproliferative disorder associated with Epstein-Barr virus. This category includes, but is not limited to, Burkitt lymphoma, classic Hodgkin lymphoma, and lymphomas arising in immunocompromised individuals. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVEpstein-Barr virus-associated malignant lymphoproliferative disorder
Follow this link to review classifications for Epstein-Barr virus-associated malignant lymphoproliferative disorder in Orphanet.

Professional guidelines

PubMed

Malpica L, Marques-Piubelli ML, Beltran BE, Chavez JC, Miranda RN, Castillo JJ
Am J Hematol 2022 Jul;97(7):951-965. Epub 2022 May 3 doi: 10.1002/ajh.26579. PMID: 35472248
Crombie J, LaCasce A
Blood 2021 Feb 11;137(6):743-750. doi: 10.1182/blood.2019004099. PMID: 33171490
Violeta Filip P, Cuciureanu D, Sorina Diaconu L, Maria Vladareanu A, Silvia Pop C
J Med Life 2018 Jul-Sep;11(3):187-193. doi: 10.25122/jml-2018-0035. PMID: 30364585Free PMC Article

Recent clinical studies

Etiology

Quintanilla-Martinez L, Swerdlow SH, Tousseyn T, Barrionuevo C, Nakamura S, Jaffe ES
Virchows Arch 2023 Jan;482(1):227-244. Epub 2022 Oct 11 doi: 10.1007/s00428-022-03414-4. PMID: 36216980Free PMC Article
Malpica L, Marques-Piubelli ML, Beltran BE, Chavez JC, Miranda RN, Castillo JJ
Am J Hematol 2022 Jul;97(7):951-965. Epub 2022 May 3 doi: 10.1002/ajh.26579. PMID: 35472248
Carbone A, Vaccher E, Gloghini A
Blood 2022 Feb 17;139(7):995-1012. doi: 10.1182/blood.2020005469. PMID: 34469512
Thandra KC, Barsouk A, Saginala K, Padala SA, Barsouk A, Rawla P
Med Sci (Basel) 2021 Jan 30;9(1) doi: 10.3390/medsci9010005. PMID: 33573146Free PMC Article
Hue SS, Oon ML, Wang S, Tan SY, Ng SB
Pathology 2020 Jan;52(1):111-127. Epub 2019 Nov 22 doi: 10.1016/j.pathol.2019.09.011. PMID: 31767131

Diagnosis

Quintanilla-Martinez L, Swerdlow SH, Tousseyn T, Barrionuevo C, Nakamura S, Jaffe ES
Virchows Arch 2023 Jan;482(1):227-244. Epub 2022 Oct 11 doi: 10.1007/s00428-022-03414-4. PMID: 36216980Free PMC Article
Zhang H, Zhao S, Cao Z
Front Immunol 2022;13:1001055. Epub 2022 Oct 28 doi: 10.3389/fimmu.2022.1001055. PMID: 36389673Free PMC Article
Thandra KC, Barsouk A, Saginala K, Padala SA, Barsouk A, Rawla P
Med Sci (Basel) 2021 Jan 30;9(1) doi: 10.3390/medsci9010005. PMID: 33573146Free PMC Article
Hue SS, Oon ML, Wang S, Tan SY, Ng SB
Pathology 2020 Jan;52(1):111-127. Epub 2019 Nov 22 doi: 10.1016/j.pathol.2019.09.011. PMID: 31767131
Borie R, Wislez M, Antoine M, Cadranel J
Respiration 2017;94(2):157-175. Epub 2017 Jun 14 doi: 10.1159/000477740. PMID: 28609772

Therapy

Salmerón-Villalobos J, Castrejón-de-Anta N, Guerra-García P, Ramis-Zaldivar JE, López-Guerra M, Mato S, Colomer D, Diaz-Crespo F, Menarguez J, Garrido-Pontnou M, Andrés M, García-Fernández E, Llavador M, Frigola G, García N, González-Farré B, Martín-Guerrero I, Garrido-Colino C, Astigarraga I, Fernández A, Verdú-Amorós J, González-Muñíz S, González B, Celis V, Campo E, Balagué O, Salaverria I
Blood 2023 Aug 3;142(5):434-445. doi: 10.1182/blood.2022019543. PMID: 37053555
Martinez OM, Krams SM
Transplantation 2017 Sep;101(9):2009-2016. doi: 10.1097/TP.0000000000001767. PMID: 28376031Free PMC Article
Hatton O, Martinez OM, Esquivel CO
Pediatr Transplant 2012 May;16(3):220-9. Epub 2012 Feb 21 doi: 10.1111/j.1399-3046.2012.01656.x. PMID: 22353174Free PMC Article
Dharnidharka VR, Araya CE
Pediatr Nephrol 2009 Apr;24(4):731-6. Epub 2007 Sep 19 doi: 10.1007/s00467-007-0582-3. PMID: 17891420Free PMC Article
Navarro WH, Kaplan LD
Blood 2006 Jan 1;107(1):13-20. Epub 2005 Aug 11 doi: 10.1182/blood-2004-11-4278. PMID: 16099881

Prognosis

Bednarska K, Chowdhury R, Tobin JWD, Swain F, Keane C, Boyle S, Khanna R, Gandhi MK
Br J Haematol 2024 Feb;204(2):415-433. Epub 2023 Dec 28 doi: 10.1111/bjh.19255. PMID: 38155519
Quintanilla-Martinez L, Swerdlow SH, Tousseyn T, Barrionuevo C, Nakamura S, Jaffe ES
Virchows Arch 2023 Jan;482(1):227-244. Epub 2022 Oct 11 doi: 10.1007/s00428-022-03414-4. PMID: 36216980Free PMC Article
Zhang H, Zhao S, Cao Z
Front Immunol 2022;13:1001055. Epub 2022 Oct 28 doi: 10.3389/fimmu.2022.1001055. PMID: 36389673Free PMC Article
Kimura H
Adv Exp Med Biol 2018;1045:459-475. doi: 10.1007/978-981-10-7230-7_21. PMID: 29896680
Borie R, Wislez M, Antoine M, Cadranel J
Respiration 2017;94(2):157-175. Epub 2017 Jun 14 doi: 10.1159/000477740. PMID: 28609772

Clinical prediction guides

Zhou T, Cheng J, Karrs J, Davies-Hill T, Pack SD, Xi L, Tyagi M, Kim J, Jaffe ES, Raffeld M, Pittaluga S
Am J Surg Pathol 2022 Oct 1;46(10):1364-1379. Epub 2022 Jun 1 doi: 10.1097/PAS.0000000000001923. PMID: 35650679Free PMC Article
Malpica L, Marques-Piubelli ML, Beltran BE, Chavez JC, Miranda RN, Castillo JJ
Am J Hematol 2022 Jul;97(7):951-965. Epub 2022 May 3 doi: 10.1002/ajh.26579. PMID: 35472248
Wong Y, Meehan MT, Burrows SR, Doolan DL, Miles JJ
J Cancer Res Clin Oncol 2022 Jan;148(1):31-46. Epub 2021 Oct 27 doi: 10.1007/s00432-021-03824-y. PMID: 34705104Free PMC Article
Okuno Y, Murata T, Sato Y, Muramatsu H, Ito Y, Watanabe T, Okuno T, Murakami N, Yoshida K, Sawada A, Inoue M, Kawa K, Seto M, Ohshima K, Shiraishi Y, Chiba K, Tanaka H, Miyano S, Narita Y, Yoshida M, Goshima F, Kawada JI, Nishida T, Kiyoi H, Kato S, Nakamura S, Morishima S, Yoshikawa T, Fujiwara S, Shimizu N, Isobe Y, Noguchi M, Kikuta A, Iwatsuki K, Takahashi Y, Kojima S, Ogawa S, Kimura H
Nat Microbiol 2019 Mar;4(3):404-413. Epub 2019 Jan 21 doi: 10.1038/s41564-018-0334-0. PMID: 30664667
Richtsmeier WJ, Wittels EG, Mazur EM
Crit Rev Clin Lab Sci 1987;25(2):105-36. doi: 10.3109/10408368709105879. PMID: 3038469

Recent systematic reviews

Honar N, Shahramian I, Imanieh MH, Ataollahi M, Tahani M, Rakhshaninasab S, Javadifar A
Hum Antibodies 2022;30(4):183-194. doi: 10.3233/HAB-220016. PMID: 37005883
Mullen CJR, Volesky KD, Greenwald ZR, El-Zein M, Franco EL
Cancer Epidemiol Biomarkers Prev 2021 Dec;30(12):2167-2175. Epub 2021 Sep 20 doi: 10.1158/1055-9965.EPI-21-0548. PMID: 34548328
Muller M, Broséus J, Feugier P, Thieblemont C, Beaugerie L, Danese S, Arnone D, Ndiaye NC, Kokten T, Houlgatte R, Peyrin-Biroulet L
J Crohns Colitis 2021 May 4;15(5):827-839. doi: 10.1093/ecco-jcc/jjaa193. PMID: 32949235
Bakkalci D, Jia Y, Winter JR, Lewis JE, Taylor GS, Stagg HR
J Glob Health 2020 Jun;10(1):010405. doi: 10.7189/jogh.10.010405. PMID: 32257153Free PMC Article
Masson P, Henderson L, Chapman JR, Craig JC, Webster AC
Cochrane Database Syst Rev 2014 Nov 24;2014(11):CD010699. doi: 10.1002/14651858.CD010699.pub2. PMID: 25416857Free PMC Article

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