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Interstitial Disease

MedGen UID:
361547
•Concept ID:
C1881236
•
Disease or Syndrome

Definition

A disease occurring chiefly in the connective-tissue framework of an organ. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVInterstitial Disease

Professional guidelines

PubMed

Diagnosis and Management of Fibrotic Interstitial Lung Diseases.
Collins BF, Luppi F
Clin Chest Med 2021 Jun;42(2):321-335. doi: 10.1016/j.ccm.2021.03.008. PMID: 34024407
Consensus Guidelines for Evaluation and Management of Pulmonary Disease in Sjögren's.
Lee AS, Scofield RH, Hammitt KM, Gupta N, Thomas DE, Moua T, Ussavarungsi K, St Clair EW, Meehan R, Dunleavy K, Makara M, Carsons SE, Carteron NL; Consensus Expert Panel (CEP) Members
Chest 2021 Feb;159(2):683-698. Epub 2020 Oct 16 doi: 10.1016/j.chest.2020.10.011. PMID: 33075377Free PMC Article
The lung in systemic vasculitis: radiological patterns and differential diagnosis.
Feragalli B, Mantini C, Sperandeo M, Galluzzo M, Belcaro G, Tartaro A, Cotroneo AR
Br J Radiol 2016;89(1061):20150992. Epub 2016 Feb 15 doi: 10.1259/bjr.20150992. PMID: 26876879Free PMC Article

Recent clinical studies

Therapy

Vocal cord lesions in representative autoimmune diseases.
Meng X, Xu HJ, Li RL, Zhao LD
Clin Rheumatol 2023 Mar;42(3):929-939. Epub 2022 Oct 21 doi: 10.1007/s10067-022-06411-9. PMID: 36269532
T(1) mapping in cardiac MRI.
Radenkovic D, Weingärtner S, Ricketts L, Moon JC, Captur G
Heart Fail Rev 2017 Jul;22(4):415-430. doi: 10.1007/s10741-017-9627-2. PMID: 28623475Free PMC Article
Antisynthetase syndrome: Analysis of 11 cases.
Zamarrón-de Lucas E, Gómez Carrera L, Bonilla G, Petit D, Mangas A, Álvarez-Sala R
Med Clin (Barc) 2017 Feb 23;148(4):166-169. Epub 2017 Jan 7 doi: 10.1016/j.medcli.2016.11.021. PMID: 28073522
Intravenous immunoglobulins (IVIG) in systemic sclerosis: a challenging yet promising future.
Cantarini L, Rigante D, Vitale A, Napodano S, Sakkas LI, Bogdanos DP, Shoenfeld Y
Immunol Res 2015 Mar;61(3):326-37. doi: 10.1007/s12026-014-8615-z. PMID: 25550086
Diagnostics and therapeutic interventions in myocardial interstitial disease, a previously neglected pathology.
Collier P, Ledwidge M, McDonald K
QJM 2012 Aug;105(8):721-4. Epub 2012 May 29 doi: 10.1093/qjmed/hcs072. PMID: 22647762

Prognosis

Interstitial disease associated with connective tissue disease and vasculitis.
Hernández Muñiz S, Olivera Serrano MJ, Jiménez Heffernan JA, Valenzuela C, Caballero Sánchez-Robles P
Radiologia (Engl Ed) 2022 Dec;64 Suppl 3:250-264. doi: 10.1016/j.rxeng.2022.07.004. PMID: 36737164
Myocardial Amyloidosis: The Exemplar Interstitial Disease.
Fontana M, Ćorović A, Scully P, Moon JC
JACC Cardiovasc Imaging 2019 Nov;12(11 Pt 2):2345-2356. Epub 2019 Aug 14 doi: 10.1016/j.jcmg.2019.06.023. PMID: 31422120
Myositis-specific autoantibodies, a cornerstone in immune-mediated necrotizing myopathy.
Anquetil C, Boyer O, Wesner N, Benveniste O, Allenbach Y
Autoimmun Rev 2019 Mar;18(3):223-230. Epub 2019 Jan 11 doi: 10.1016/j.autrev.2018.09.008. PMID: 30639649
Pulmonary manifestations in systemic lupus erythematosus: pleural involvement, acute pneumonitis, chronic interstitial lung disease and diffuse alveolar hemorrhage.
Aguilera-Pickens G, Abud-Mendoza C
Reumatol Clin (Engl Ed) 2018 Sep-Oct;14(5):294-300. doi: 10.1016/j.reuma.2018.03.012. PMID: 29773465
T(1) mapping in cardiac MRI.
Radenkovic D, Weingärtner S, Ricketts L, Moon JC, Captur G
Heart Fail Rev 2017 Jul;22(4):415-430. doi: 10.1007/s10741-017-9627-2. PMID: 28623475Free PMC Article

Clinical prediction guides

Vocal cord lesions in representative autoimmune diseases.
Meng X, Xu HJ, Li RL, Zhao LD
Clin Rheumatol 2023 Mar;42(3):929-939. Epub 2022 Oct 21 doi: 10.1007/s10067-022-06411-9. PMID: 36269532
Thoracic involvement and imaging patterns in IgG4-related disease.
Muller R, Habert P, Ebbo M, Graveleau J, Groh M, Launay D, Audia S, Pugnet G, Cohen F, Perlat A, Benyamine A, Bienvenu B, Gaigne L, Chanez P, Gaubert JY, Schleinitz N
Eur Respir Rev 2021 Dec 31;30(162) Epub 2021 Oct 5 doi: 10.1183/16000617.0078-2021. PMID: 34615698Free PMC Article
Myocardial Amyloidosis: The Exemplar Interstitial Disease.
Fontana M, Ćorović A, Scully P, Moon JC
JACC Cardiovasc Imaging 2019 Nov;12(11 Pt 2):2345-2356. Epub 2019 Aug 14 doi: 10.1016/j.jcmg.2019.06.023. PMID: 31422120
A more tubulocentric view of diabetic kidney disease.
Zeni L, Norden AGW, Cancarini G, Unwin RJ
J Nephrol 2017 Dec;30(6):701-717. Epub 2017 Aug 24 doi: 10.1007/s40620-017-0423-9. PMID: 28840540Free PMC Article
Pulmonary involvement in rheumatoid arthritis.
Anaya JM, Diethelm L, Ortiz LA, Gutierrez M, Citera G, Welsh RA, Espinoza LR
Semin Arthritis Rheum 1995 Feb;24(4):242-54. doi: 10.1016/s0049-0172(95)80034-4. PMID: 7740304

Recent systematic reviews

Pulmonary fibrosis insights and therapy targets from disease models and administration of the lipophilic diterpene, sodium tanshinone IIA sulfonate: Review and meta-analysis.
Peng LY, Shi JJ, Liang Y, Li Y, Tang Y, Kai T, Yang A, Xiong ZY
Int J Clin Pharmacol Ther 2024 Oct;62(10):460-478. doi: 10.5414/CP204622. PMID: 39120081
Effectivity of mesenchymal stem cells for bleomycin-induced pulmonary fibrosis: a systematic review and implication for clinical application.
Zhao Y, Yan Z, Liu Y, Zhang Y, Shi J, Li J, Ji F
Stem Cell Res Ther 2021 Aug 23;12(1):470. doi: 10.1186/s13287-021-02551-y. PMID: 34420515Free PMC Article
Prognostic role of Krebs von den Lungen-6 (KL-6) measurement in idiopathic pulmonary fibrosis: a systematic review and meta-analysis.
Aloisio E, Braga F, Puricelli C, Panteghini M
Clin Chem Lab Med 2021 Jul 27;59(8):1400-1408. Epub 2021 Apr 9 doi: 10.1515/cclm-2021-0199. PMID: 33831978
The impact of cardiopulmonary manifestations on the mortality of SSc: a systematic review and meta-analysis of observational studies.
Komócsi A, Vorobcsuk A, Faludi R, Pintér T, Lenkey Z, Költo G, Czirják L
Rheumatology (Oxford) 2012 Jun;51(6):1027-36. Epub 2012 Jan 5 doi: 10.1093/rheumatology/ker357. PMID: 22223705

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