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Renal sarcoma

MedGen UID:
87548
•Concept ID:
C0346251
•
Neoplastic Process
Synonyms: Kidney Sarcoma; kidney sarcoma; Renal Sarcoma; renal sarcoma; Sarcoma of kidney; Sarcoma of Kidney; sarcoma of kidney; Sarcoma of the Kidney; sarcoma of the kidney
SNOMED CT: Sarcoma of kidney (254918001)
 
HPO: HP:0008663
Monarch Initiative: MONDO:0002930

Definition

A sarcoma of the kidney. [from HPO]

Professional guidelines

PubMed

Epidemiology, treatment and outcomes of primary renal sarcomas in adult patients.
Uhlig J, Uhlig A, Deshpande H, Ströbel P, Trojan L, Lotz J, Hurwitz M, Hafez O, Humphrey P, Grünwald V, Kim HS
Sci Rep 2024 May 2;14(1):10038. doi: 10.1038/s41598-024-60174-8. PMID: 38693188Free PMC Article
Diagnosis and treatment of primary adult renal sarcoma.
Huang ZM, Li HZ, Ji ZG, Shi BB
Chin Med Sci J 2011 Sep;26(3):172-4. doi: 10.1016/s1001-9294(11)60044-8. PMID: 22207927
Thalidomide in the treatment of cancer.
Adlard JW
Anticancer Drugs 2000 Nov;11(10):787-91. doi: 10.1097/00001813-200011000-00002. PMID: 11142686

Recent clinical studies

Etiology

Renal Sarcoma: A Population-Based Study.
Alevizakos M, Gaitanidis A, Korentzelos D, Basourakos SP, Burgess M
Clin Genitourin Cancer 2023 Feb;21(1):155-161. Epub 2022 Jul 30 doi: 10.1016/j.clgc.2022.07.012. PMID: 36045013Free PMC Article
Primary Renal Synovial Sarcoma and Clinical and Pathological Findings: a Systematic Review.
Blas L, Roberti J
Curr Urol Rep 2021 Mar 11;22(4):25. doi: 10.1007/s11934-021-01038-w. PMID: 33704587
DICER1 and Associated Conditions: Identification of At-risk Individuals and Recommended Surveillance Strategies.
Schultz KAP, Williams GM, Kamihara J, Stewart DR, Harris AK, Bauer AJ, Turner J, Shah R, Schneider K, Schneider KW, Carr AG, Harney LA, Baldinger S, Frazier AL, Orbach D, Schneider DT, Malkin D, Dehner LP, Messinger YH, Hill DA
Clin Cancer Res 2018 May 15;24(10):2251-2261. Epub 2018 Jan 17 doi: 10.1158/1078-0432.CCR-17-3089. PMID: 29343557Free PMC Article
Pediatric imaging in DICER1 syndrome.
Bueno MT, Martínez-Ríos C, la Puente Gregorio A, Ahyad RA, Villani A, Druker H, van Engelen K, Gallinger B, Aronoff L, Grant R, Malkin D, Greer MC
Pediatr Radiol 2017 Sep;47(10):1292-1301. Epub 2017 May 4 doi: 10.1007/s00247-017-3875-0. PMID: 28474256
Clinicopathologic characteristics and survival for adult renal sarcoma: A population-based study.
Moreira DM, Gershman B, Thompson RH, Okuno SH, Robinson SI, Leibovich BC, Boorjian SA
Urol Oncol 2015 Dec;33(12):505.e15-20. Epub 2015 Aug 28 doi: 10.1016/j.urolonc.2015.07.022. PMID: 26321056

Diagnosis

Renal Sarcoma: A Population-Based Study.
Alevizakos M, Gaitanidis A, Korentzelos D, Basourakos SP, Burgess M
Clin Genitourin Cancer 2023 Feb;21(1):155-161. Epub 2022 Jul 30 doi: 10.1016/j.clgc.2022.07.012. PMID: 36045013Free PMC Article
Primary renal sarcomas: imaging features and discrimination from non-sarcoma renal tumors.
Uhlig J, Uhlig A, Bachanek S, Onur MR, Kinner S, Geisel D, Köhler M, Preibsch H, Puesken M, Schramm D, May M, De Visschere P, Weber MA, Surov A
Eur Radiol 2022 Feb;32(2):981-989. Epub 2021 Jul 31 doi: 10.1007/s00330-021-08201-4. PMID: 34331576Free PMC Article
Primary Renal Synovial Sarcoma and Clinical and Pathological Findings: a Systematic Review.
Blas L, Roberti J
Curr Urol Rep 2021 Mar 11;22(4):25. doi: 10.1007/s11934-021-01038-w. PMID: 33704587
DICER1 and Associated Conditions: Identification of At-risk Individuals and Recommended Surveillance Strategies.
Schultz KAP, Williams GM, Kamihara J, Stewart DR, Harris AK, Bauer AJ, Turner J, Shah R, Schneider K, Schneider KW, Carr AG, Harney LA, Baldinger S, Frazier AL, Orbach D, Schneider DT, Malkin D, Dehner LP, Messinger YH, Hill DA
Clin Cancer Res 2018 May 15;24(10):2251-2261. Epub 2018 Jan 17 doi: 10.1158/1078-0432.CCR-17-3089. PMID: 29343557Free PMC Article
Renal sarcoma.
Jenkins JD, Anderson CK, Williams RE
Br J Urol 1971 Jun;43(3):263-7. doi: 10.1111/j.1464-410x.1971.tb12037.x. PMID: 4326673

Therapy

Development and validation of a prognostic nomogram for adult patients with renal sarcoma: A retrospective study based on the SEER database.
Zhu Y, Mao W, Zhang G, Sun S, Tao S, Jiang T, Wang Q, Meng Y, Wu J, Chen M
Front Public Health 2022;10:942608. Epub 2022 Sep 12 doi: 10.3389/fpubh.2022.942608. PMID: 36187680Free PMC Article
Primary renal sarcomas: imaging features and discrimination from non-sarcoma renal tumors.
Uhlig J, Uhlig A, Bachanek S, Onur MR, Kinner S, Geisel D, Köhler M, Preibsch H, Puesken M, Schramm D, May M, De Visschere P, Weber MA, Surov A
Eur Radiol 2022 Feb;32(2):981-989. Epub 2021 Jul 31 doi: 10.1007/s00330-021-08201-4. PMID: 34331576Free PMC Article
A phase I study of sorafenib and vorinostat in patients with advanced solid tumors with expanded cohorts in renal cell carcinoma and non-small cell lung cancer.
Dasari A, Gore L, Messersmith WA, Diab S, Jimeno A, Weekes CD, Lewis KD, Drabkin HA, Flaig TW, Camidge DR
Invest New Drugs 2013 Feb;31(1):115-25. Epub 2012 Mar 14 doi: 10.1007/s10637-012-9812-z. PMID: 22415798
Primary renal angiosarcoma: case report and review of world literature.
Zenico T, Saccomanni M, Salomone U, Bercovich E
Tumori 2011 Jul-Aug;97(4):e6-9. doi: 10.1177/030089161109700422. PMID: 21989448
Laparoscopic nephrectomy: initial experience in Israel with 110 cases.
Nadu A, Mor Y, Chen J, Sofer M, Golomb J, Ramon J
Isr Med Assoc J 2005 Jul;7(7):431-4. PMID: 16011057

Prognosis

Renal Sarcoma: A Population-Based Study.
Alevizakos M, Gaitanidis A, Korentzelos D, Basourakos SP, Burgess M
Clin Genitourin Cancer 2023 Feb;21(1):155-161. Epub 2022 Jul 30 doi: 10.1016/j.clgc.2022.07.012. PMID: 36045013Free PMC Article
Primary renal sarcomas: imaging features and discrimination from non-sarcoma renal tumors.
Uhlig J, Uhlig A, Bachanek S, Onur MR, Kinner S, Geisel D, Köhler M, Preibsch H, Puesken M, Schramm D, May M, De Visschere P, Weber MA, Surov A
Eur Radiol 2022 Feb;32(2):981-989. Epub 2021 Jul 31 doi: 10.1007/s00330-021-08201-4. PMID: 34331576Free PMC Article
Primary Renal Synovial Sarcoma and Clinical and Pathological Findings: a Systematic Review.
Blas L, Roberti J
Curr Urol Rep 2021 Mar 11;22(4):25. doi: 10.1007/s11934-021-01038-w. PMID: 33704587
Clinicopathologic characteristics and survival for adult renal sarcoma: A population-based study.
Moreira DM, Gershman B, Thompson RH, Okuno SH, Robinson SI, Leibovich BC, Boorjian SA
Urol Oncol 2015 Dec;33(12):505.e15-20. Epub 2015 Aug 28 doi: 10.1016/j.urolonc.2015.07.022. PMID: 26321056
Renal sarcoma.
Jenkins JD, Anderson CK, Williams RE
Br J Urol 1971 Jun;43(3):263-7. doi: 10.1111/j.1464-410x.1971.tb12037.x. PMID: 4326673

Clinical prediction guides

Development and validation of a prognostic nomogram for adult patients with renal sarcoma: A retrospective study based on the SEER database.
Zhu Y, Mao W, Zhang G, Sun S, Tao S, Jiang T, Wang Q, Meng Y, Wu J, Chen M
Front Public Health 2022;10:942608. Epub 2022 Sep 12 doi: 10.3389/fpubh.2022.942608. PMID: 36187680Free PMC Article
Primary renal sarcomas: imaging features and discrimination from non-sarcoma renal tumors.
Uhlig J, Uhlig A, Bachanek S, Onur MR, Kinner S, Geisel D, Köhler M, Preibsch H, Puesken M, Schramm D, May M, De Visschere P, Weber MA, Surov A
Eur Radiol 2022 Feb;32(2):981-989. Epub 2021 Jul 31 doi: 10.1007/s00330-021-08201-4. PMID: 34331576Free PMC Article
Metastatic pediatric sclerosing epithelioid fibrosarcoma.
Woods AD, Purohit R, Mitchell LC, Collier JR, Collier KA, Lathara M, Learned K, Vaske O, Geiger H, Wrzeszczynski KO, Jobanputra V, Srinivasa G, Rudzinski ER, Whelan K, Beierle E, Spunt SL, Keller C, Wadhwa A
Cold Spring Harb Mol Case Stud 2021 Oct;7(5) Epub 2021 Oct 19 doi: 10.1101/mcs.a006093. PMID: 34362827Free PMC Article
A risk-based approach to identifying oligometastatic disease on imaging.
deSouza NM, Tempany CM
Int J Cancer 2019 Feb 1;144(3):422-430. Epub 2018 Oct 9 doi: 10.1002/ijc.31793. PMID: 30098215Free PMC Article
Pediatric imaging in DICER1 syndrome.
Bueno MT, Martínez-Ríos C, la Puente Gregorio A, Ahyad RA, Villani A, Druker H, van Engelen K, Gallinger B, Aronoff L, Grant R, Malkin D, Greer MC
Pediatr Radiol 2017 Sep;47(10):1292-1301. Epub 2017 May 4 doi: 10.1007/s00247-017-3875-0. PMID: 28474256

Recent systematic reviews

Primary Renal Synovial Sarcoma and Clinical and Pathological Findings: a Systematic Review.
Blas L, Roberti J
Curr Urol Rep 2021 Mar 11;22(4):25. doi: 10.1007/s11934-021-01038-w. PMID: 33704587

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