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Kidney Synovial Sarcoma

MedGen UID:
1679617
•Concept ID:
C4763820
•
Neoplastic Process
Synonym: Renal Synovial Sarcoma

Definition

A synovial sarcoma arising from the kidney. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVKidney Synovial Sarcoma

Professional guidelines

PubMed

Primary Renal Synovial Sarcoma Presenting as Metastatic Right Atrial Obstruction.
Ulhaq O, Ali SA, Khalid U, Kayani WT
Tex Heart Inst J 2022 Sep 1;49(5) doi: 10.14503/THIJ-20-7386. PMID: 36228326Free PMC Article
Incidence, treatment, and outcomes of primary and recurrent Non-Wilms renal tumors in children: Report of 109 patients treated at a single institution.
Qureshi SS, Bhagat M, Verma K, Yadav S, Prasad M, Vora T, Chinnaswamy G, Amin N, Smriti V, Baheti A, Laskar S, Khanna N, Ramadwar M, Shah S
J Pediatr Urol 2020 Aug;16(4):475.e1-475.e9. Epub 2020 Jun 5 doi: 10.1016/j.jpurol.2020.05.168. PMID: 32620510
Immunophenotype-Genotype Correlations in Clear Cell Sarcoma of Kidney-An Evaluation of Diagnostic Ancillary Studies.
Kenny C, Grehan D, Ulas M, Banga GB, Coulomb A, Vokuhl C, O'Sullivan MJ
Pediatr Dev Pathol 2020 Sep-Oct;23(5):345-351. Epub 2020 May 4 doi: 10.1177/1093526620910658. PMID: 32364435

Recent clinical studies

Etiology

Primary Renal Synovial Sarcoma and Clinical and Pathological Findings: a Systematic Review.
Blas L, Roberti J
Curr Urol Rep 2021 Mar 11;22(4):25. doi: 10.1007/s11934-021-01038-w. PMID: 33704587
BCOR-CCNB3 Fusion Positive Sarcomas: A Clinicopathologic and Molecular Analysis of 36 Cases With Comparison to Morphologic Spectrum and Clinical Behavior of Other Round Cell Sarcomas.
Kao YC, Owosho AA, Sung YS, Zhang L, Fujisawa Y, Lee JC, Wexler L, Argani P, Swanson D, Dickson BC, Fletcher CDM, Antonescu CR
Am J Surg Pathol 2018 May;42(5):604-615. doi: 10.1097/PAS.0000000000000965. PMID: 29300189Free PMC Article
Primary renal synovial sarcoma: computed tomography imaging findings.
Lv XF, Qiu YW, Han LJ, Cao J, Zhang C, Liu ZY, Zhang XL, Cai PQ, Li L
Acta Radiol 2015 Apr;56(4):493-9. Epub 2014 Mar 28 doi: 10.1177/0284185114528836. PMID: 24682407
Cystic renal neoplasms and renal neoplasms associated with cystic renal diseases in adults: cross-sectional imaging findings.
Katabathina VS, Garg D, Prasad SR, Vikram R
J Comput Assist Tomogr 2012 Nov-Dec;36(6):659-68. doi: 10.1097/RCT.0b013e31826dba18. PMID: 23192202
Retroperitoneal sarcomas.
Eilber FC, Eilber KS, Eilber FR
Curr Treat Options Oncol 2000 Aug;1(3):274-8. doi: 10.1007/s11864-000-0040-y. PMID: 12057171

Diagnosis

Primary Renal Synovial Sarcoma and Clinical and Pathological Findings: a Systematic Review.
Blas L, Roberti J
Curr Urol Rep 2021 Mar 11;22(4):25. doi: 10.1007/s11934-021-01038-w. PMID: 33704587
BCOR-CCNB3 Fusion Positive Sarcomas: A Clinicopathologic and Molecular Analysis of 36 Cases With Comparison to Morphologic Spectrum and Clinical Behavior of Other Round Cell Sarcomas.
Kao YC, Owosho AA, Sung YS, Zhang L, Fujisawa Y, Lee JC, Wexler L, Argani P, Swanson D, Dickson BC, Fletcher CDM, Antonescu CR
Am J Surg Pathol 2018 May;42(5):604-615. doi: 10.1097/PAS.0000000000000965. PMID: 29300189Free PMC Article
Mesenchymal tumors of adult kidney.
Samaratunga H, Delahunt B
Semin Diagn Pathol 2015 Mar;32(2):160-71. Epub 2015 Feb 4 doi: 10.1053/j.semdp.2015.02.007. PMID: 25773128
Primary cardiac synovial sarcoma.
Varma T, Adegboyega P
Arch Pathol Lab Med 2012 Apr;136(4):454-8. doi: 10.5858/arpa.2011-0008-RS. PMID: 22458908
Retroperitoneal sarcomas.
Eilber FC, Eilber KS, Eilber FR
Curr Treat Options Oncol 2000 Aug;1(3):274-8. doi: 10.1007/s11864-000-0040-y. PMID: 12057171

Therapy

Primary synovial sarcoma of the kidney: a case report of complete pathological response at a Lebanese tertiary care center.
El Chediak A, Mukherji D, Temraz S, Nassif S, Sinno S, Mahfouz R, Shamseddine A
BMC Urol 2018 May 11;18(1):40. doi: 10.1186/s12894-018-0358-z. PMID: 29751751Free PMC Article
Primary Synovial Sarcoma of the Kidney: A Rare Presentation.
Puj KS, Pandya SJ, Warikoo V, Chauhan T, Samanta ST
Urology 2018 Jun;116:e7-e8. Epub 2018 Mar 19 doi: 10.1016/j.urology.2017.12.017. PMID: 29567016
Immunotherapeutic approaches to sarcoma.
Burgess M, Tawbi H
Curr Treat Options Oncol 2015 Jun;16(6):26. doi: 10.1007/s11864-015-0345-5. PMID: 25975445
A case of renal synovial sarcoma treated with adjuvant ifosfamide and doxorubicin.
Ozkan EE, Mertsoylu H, Ozardali HI
Intern Med 2011;50(15):1575-80. Epub 2011 Aug 1 doi: 10.2169/internalmedicine.50.5224. PMID: 21804284
Retroperitoneal sarcomas.
Eilber FC, Eilber KS, Eilber FR
Curr Treat Options Oncol 2000 Aug;1(3):274-8. doi: 10.1007/s11864-000-0040-y. PMID: 12057171

Prognosis

Primary Renal Synovial Sarcoma and Clinical and Pathological Findings: a Systematic Review.
Blas L, Roberti J
Curr Urol Rep 2021 Mar 11;22(4):25. doi: 10.1007/s11934-021-01038-w. PMID: 33704587
BCOR-CCNB3 Fusion Positive Sarcomas: A Clinicopathologic and Molecular Analysis of 36 Cases With Comparison to Morphologic Spectrum and Clinical Behavior of Other Round Cell Sarcomas.
Kao YC, Owosho AA, Sung YS, Zhang L, Fujisawa Y, Lee JC, Wexler L, Argani P, Swanson D, Dickson BC, Fletcher CDM, Antonescu CR
Am J Surg Pathol 2018 May;42(5):604-615. doi: 10.1097/PAS.0000000000000965. PMID: 29300189Free PMC Article
SMARCB1-deficient Tumors of Childhood: A Practical Guide.
Pawel BR
Pediatr Dev Pathol 2018 Jan-Feb;21(1):6-28. Epub 2017 Dec 27 doi: 10.1177/1093526617749671. PMID: 29280680
Primary cardiac synovial sarcoma.
Varma T, Adegboyega P
Arch Pathol Lab Med 2012 Apr;136(4):454-8. doi: 10.5858/arpa.2011-0008-RS. PMID: 22458908
Retroperitoneal sarcomas.
Eilber FC, Eilber KS, Eilber FR
Curr Treat Options Oncol 2000 Aug;1(3):274-8. doi: 10.1007/s11864-000-0040-y. PMID: 12057171

Clinical prediction guides

BCOR-CCNB3 Fusion Positive Sarcomas: A Clinicopathologic and Molecular Analysis of 36 Cases With Comparison to Morphologic Spectrum and Clinical Behavior of Other Round Cell Sarcomas.
Kao YC, Owosho AA, Sung YS, Zhang L, Fujisawa Y, Lee JC, Wexler L, Argani P, Swanson D, Dickson BC, Fletcher CDM, Antonescu CR
Am J Surg Pathol 2018 May;42(5):604-615. doi: 10.1097/PAS.0000000000000965. PMID: 29300189Free PMC Article
Primary renal synovial sarcoma: computed tomography imaging findings.
Lv XF, Qiu YW, Han LJ, Cao J, Zhang C, Liu ZY, Zhang XL, Cai PQ, Li L
Acta Radiol 2015 Apr;56(4):493-9. Epub 2014 Mar 28 doi: 10.1177/0284185114528836. PMID: 24682407
Synovial sarcoma of the kidney: a clinicopathologic, immunohistochemical, and molecular genetic study of 16 cases.
Schoolmeester JK, Cheville JC, Folpe AL
Am J Surg Pathol 2014 Jan;38(1):60-5. doi: 10.1097/PAS.0b013e31829b2d0d. PMID: 24061517
Primary synovial sarcoma of the kidney.
Ozkanli SS, Yildirim A, Zemheri E, Gucer Fİ, Aydin A, Caskurlu T
Urol Int 2014;92(3):369-72. Epub 2013 Sep 17 doi: 10.1159/000353087. PMID: 24051997
Genetics of pediatric renal tumors.
Royer-Pokora B
Pediatr Nephrol 2013 Jan;28(1):13-23. Epub 2012 Mar 30 doi: 10.1007/s00467-012-2146-4. PMID: 22461142

Recent systematic reviews

Primary Renal Synovial Sarcoma and Clinical and Pathological Findings: a Systematic Review.
Blas L, Roberti J
Curr Urol Rep 2021 Mar 11;22(4):25. doi: 10.1007/s11934-021-01038-w. PMID: 33704587

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