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Adult extraskeletal osteosarcoma

MedGen UID:
83016
Concept ID:
C0278985
Neoplastic Process
Synonyms: Adult Extraosseous Osteosarcoma; adult extraosseous osteosarcoma; Adult Extraskeletal Osteosarcoma; adult extraskeletal osteosarcoma; extraosseous osteosarcoma of adults
 
Monarch Initiative: MONDO:0004374

Definition

An osteosarcoma arising from the soft tissue, and occurring in adults. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAdult extraskeletal osteosarcoma

Professional guidelines

PubMed

Houdek MT, Heidenreich MJ, Ahmed SK, Allen-Rhoades W, Siontis BL, Robinson SI, Petersen IA, Rose PS
J Surg Oncol 2023 Jul;128(1):105-110. Epub 2023 Mar 31 doi: 10.1002/jso.27250. PMID: 36999583
Habeeb O, Weigelt MA, Goldblum JR, Ko JS, Habermehl G, Rubin BP, Billings SD
Pathology 2023 Apr;55(3):315-323. Epub 2022 Nov 30 doi: 10.1016/j.pathol.2022.10.002. PMID: 36567163
Nystrom LM, Reimer NB, Reith JD, Scarborough MT, Gibbs CP Jr
Iowa Orthop J 2016;36:98-103. PMID: 27528844Free PMC Article

Curated

NCCN Clinical Practice Guidelines in Oncology (NCCN Guidelines®), Soft Tissue Sarcoma, 2024

Recent clinical studies

Etiology

Wang XC, Zhang L, Lin JB, Huang XY, Liang JH, Zhong JP, Peng JD, Zhong JY
BMC Cancer 2024 Jan 2;24(1):11. doi: 10.1186/s12885-023-11731-3. PMID: 38166700Free PMC Article
Kunisada T, Nakata E, Fujiwara T, Hosono A, Takihira S, Kondo H, Ozaki T
Int J Clin Oncol 2023 Jan;28(1):1-11. Epub 2022 Jan 27 doi: 10.1007/s10147-022-02119-7. PMID: 35084598
Heng M, Gupta A, Chung PW, Healey JH, Vaynrub M, Rose PS, Houdek MT, Lin PP, Bishop AJ, Hornicek FJ, Chen YL, Lozano-Calderon S, Holt GE, Han I, Biau D, Niu X, Bernthal NM, Ferguson PC, Wunder JS; Japanese Musculoskeletal Oncology Group (JMOG); Soft Tissue Osteosarcoma International Collaborative (STOIC)
Eur J Cancer 2020 Jan;125:130-141. Epub 2019 Dec 2 doi: 10.1016/j.ejca.2019.07.029. PMID: 31806415Free PMC Article
Paludo J, Fritchie K, Haddox CL, Rose PS, Arndt CAS, Marks RS, Galanis E, Okuno SH, Robinson SI
Am J Clin Oncol 2018 Sep;41(9):832-837. doi: 10.1097/COC.0000000000000397. PMID: 28622153Free PMC Article
Chung EB, Enzinger FM
Cancer 1987 Sep 1;60(5):1132-42. doi: 10.1002/1097-0142(19870901)60:5<1132::aid-cncr2820600536>3.0.co;2-l. PMID: 3475157

Diagnosis

Wang XC, Zhang L, Lin JB, Huang XY, Liang JH, Zhong JP, Peng JD, Zhong JY
BMC Cancer 2024 Jan 2;24(1):11. doi: 10.1186/s12885-023-11731-3. PMID: 38166700Free PMC Article
Cammareri C, Beltzung F, Michal M, Vanhersecke L, Coindre JM, Velasco V, Le Loarer F, Vergier B, Perret R
Virchows Arch 2023 Aug;483(2):145-156. Epub 2023 Jul 21 doi: 10.1007/s00428-023-03606-6. PMID: 37477762
Habeeb O, Weigelt MA, Goldblum JR, Ko JS, Habermehl G, Rubin BP, Billings SD
Pathology 2023 Apr;55(3):315-323. Epub 2022 Nov 30 doi: 10.1016/j.pathol.2022.10.002. PMID: 36567163
Fiegen AP, Tjarks BJ, Jassim AD
S D Med 2018 Apr;71(4):164-166. PMID: 29996033
Paludo J, Fritchie K, Haddox CL, Rose PS, Arndt CAS, Marks RS, Galanis E, Okuno SH, Robinson SI
Am J Clin Oncol 2018 Sep;41(9):832-837. doi: 10.1097/COC.0000000000000397. PMID: 28622153Free PMC Article

Therapy

Houdek MT, Heidenreich MJ, Ahmed SK, Allen-Rhoades W, Siontis BL, Robinson SI, Petersen IA, Rose PS
J Surg Oncol 2023 Jul;128(1):105-110. Epub 2023 Mar 31 doi: 10.1002/jso.27250. PMID: 36999583
Mathew J, Arjunan R, Dasappa A, Namachivayam A
Ann Surg Oncol 2023 May;30(5):3084-3094. Epub 2022 Dec 23 doi: 10.1245/s10434-022-12992-1. PMID: 36564656
Paludo J, Fritchie K, Haddox CL, Rose PS, Arndt CAS, Marks RS, Galanis E, Okuno SH, Robinson SI
Am J Clin Oncol 2018 Sep;41(9):832-837. doi: 10.1097/COC.0000000000000397. PMID: 28622153Free PMC Article
Nystrom LM, Reimer NB, Reith JD, Scarborough MT, Gibbs CP Jr
Iowa Orthop J 2016;36:98-103. PMID: 27528844Free PMC Article
Xie CF, Liu MZ, Xi M
Chin J Cancer 2010 Apr;29(4):420-4. doi: 10.5732/cjc.009.10402. PMID: 20346219

Prognosis

Habeeb O, Weigelt MA, Goldblum JR, Ko JS, Habermehl G, Rubin BP, Billings SD
Pathology 2023 Apr;55(3):315-323. Epub 2022 Nov 30 doi: 10.1016/j.pathol.2022.10.002. PMID: 36567163
Kunisada T, Nakata E, Fujiwara T, Hosono A, Takihira S, Kondo H, Ozaki T
Int J Clin Oncol 2023 Jan;28(1):1-11. Epub 2022 Jan 27 doi: 10.1007/s10147-022-02119-7. PMID: 35084598
Heng M, Gupta A, Chung PW, Healey JH, Vaynrub M, Rose PS, Houdek MT, Lin PP, Bishop AJ, Hornicek FJ, Chen YL, Lozano-Calderon S, Holt GE, Han I, Biau D, Niu X, Bernthal NM, Ferguson PC, Wunder JS; Japanese Musculoskeletal Oncology Group (JMOG); Soft Tissue Osteosarcoma International Collaborative (STOIC)
Eur J Cancer 2020 Jan;125:130-141. Epub 2019 Dec 2 doi: 10.1016/j.ejca.2019.07.029. PMID: 31806415Free PMC Article
Paludo J, Fritchie K, Haddox CL, Rose PS, Arndt CAS, Marks RS, Galanis E, Okuno SH, Robinson SI
Am J Clin Oncol 2018 Sep;41(9):832-837. doi: 10.1097/COC.0000000000000397. PMID: 28622153Free PMC Article
Nystrom LM, Reimer NB, Reith JD, Scarborough MT, Gibbs CP Jr
Iowa Orthop J 2016;36:98-103. PMID: 27528844Free PMC Article

Clinical prediction guides

Crombé A, Spinnato P, Righi A, Leopardi MP, Carpenzano M, Izzo F, Parmeggiani A, Linck PA, Perret R, Cesari M, Longhi A, Miceli M, Kind M, Bianchi G
Diagn Interv Imaging 2023 Jun;104(6):297-306. Epub 2023 Feb 21 doi: 10.1016/j.diii.2023.01.009. PMID: 36813659
Sparreboom BD, Trautman J, Yaxley J
J Med Imaging Radiat Oncol 2022 Sep;66(6):812-818. Epub 2022 Jul 16 doi: 10.1111/1754-9485.13456. PMID: 35842789
Lozano Calderón SA, Garbutt C, Kim J, Lietz CE, Chen YL, Bernstein K, Chebib I, Nielsen GP, Deshpande V, Rubio R, Wang YE, Quackenbush J, Delaney T, Raskin K, Schwab J, Cote G, Spentzos D
Clin Orthop Relat Res 2019 Sep;477(9):2114-2126. doi: 10.1097/CORR.0000000000000867. PMID: 31389890Free PMC Article
Makise N, Sekimizu M, Kubo T, Wakai S, Watanabe SI, Kato T, Kinoshita T, Hiraoka N, Fukayama M, Kawai A, Ichikawa H, Yoshida A
Histopathology 2018 Jul;73(1):147-156. Epub 2018 Apr 19 doi: 10.1111/his.13506. PMID: 29489027
Berner K, Bjerkehagen B, Bruland ØS, Berner A
Anticancer Res 2015 Apr;35(4):2129-40. PMID: 25862869

Recent systematic reviews

Salama H, Abu-Hilal LH, Idkedek M, Kharousha A, Abulihya M, Nimer H
J Med Case Rep 2024 Mar 9;18(1):144. doi: 10.1186/s13256-024-04384-8. PMID: 38459600Free PMC Article

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    Clinical resources

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    • PubMed
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      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Curated

    • NCCN, 2024
      NCCN Clinical Practice Guidelines in Oncology (NCCN Guidelines®), Soft Tissue Sarcoma, 2024

    Consumer resources

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