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Left aortic arch with isolated subclavian artery

MedGen UID:
868869
•Concept ID:
C4023280
•
Anatomical Abnormality
HPO: HP:0011592

Definition

The subclavian artery arises from ductus arteriosus. While the ductus arteriosus is patent its blood supply comes from the ductus, hence from the pulmonary artery. After it closes, the blood supply is retrogradely from the vertebral artery via the circle of Willis. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVLeft aortic arch with isolated subclavian artery

Professional guidelines

PubMed

Prenatal diagnosis of isolation of aortic brachiocephalic artery.
Hao XY, Zhang Y, Zhao Y, Liu X, Gu X, Han JC, He YH
Acta Radiol 2022 Dec;63(12):1712-1720. Epub 2021 Dec 3 doi: 10.1177/02841851211058278. PMID: 34859686
Prenatal Diagnosis of Vascular Ring: Evaluation of Fetal Diagnosis and Postnatal Outcomes.
Aly S, Papneja K, Mawad W, Seed M, Jaeggi E, Yoo SJ
J Am Soc Echocardiogr 2022 Mar;35(3):312-321. Epub 2021 Sep 29 doi: 10.1016/j.echo.2021.09.010. PMID: 34600045
Prenatal diagnosis and clinical implications of an apparently isolated right aortic arch.
Vigneswaran TV, Allan L, Charakida M, Durward A, Simpson JM, Nicolaides KH, Zidere V
Prenat Diagn 2018 Dec;38(13):1055-1061. doi: 10.1002/pd.5388. PMID: 30421794

Recent clinical studies

Etiology

Prenatal diagnosis of isolation of aortic brachiocephalic artery.
Hao XY, Zhang Y, Zhao Y, Liu X, Gu X, Han JC, He YH
Acta Radiol 2022 Dec;63(12):1712-1720. Epub 2021 Dec 3 doi: 10.1177/02841851211058278. PMID: 34859686
Kommerell Diverticulum: Distinctions Between Arch Side and Evaluation of Morphology, Size, And Risk.
Hale BW, Lu JC, Romano JC, Lowery R, Yu S, Norris MD
Ann Thorac Surg 2022 Sep;114(3):848-856. Epub 2021 Jul 18 doi: 10.1016/j.athoracsur.2021.06.035. PMID: 34283954
Management of Interrupted Aortic Arch With Associated Anomalies: A Single-Center Experience.
Onalan MA, Temur B, Aydın S, Suzan D, Demir IH, Odemis E, Erek E
World J Pediatr Congenit Heart Surg 2021 Nov;12(6):706-714. doi: 10.1177/21501351211038508. PMID: 34846967
Isolated Coarctation Repair in Neonates and Infants Through Left Thoracotomy: Short-Term Outcomes.
Murakami AN, Croti UA, Cajueiro FCM, Arteaga G, Pike RB, Moscardini AC, Marchi CH, Cardoso MRR, Santos FCGB, Borim BC
Braz J Cardiovasc Surg 2021 Aug 6;36(4):461-467. doi: 10.21470/1678-9741-2020-0554. PMID: 34617427Free PMC Article
Congenital abnormalities of the aortic arch: revisiting the 1964 Stewart classification.
Li S, Wen H, Liang M, Luo D, Qin Y, Liao Y, Ouyang S, Bi J, Tian X, Norwitz ER, Luo G
Cardiovasc Pathol 2019 Mar-Apr;39:38-50. Epub 2018 Dec 6 doi: 10.1016/j.carpath.2018.11.004. PMID: 30623879

Diagnosis

Prenatal diagnosis of isolation of aortic brachiocephalic artery.
Hao XY, Zhang Y, Zhao Y, Liu X, Gu X, Han JC, He YH
Acta Radiol 2022 Dec;63(12):1712-1720. Epub 2021 Dec 3 doi: 10.1177/02841851211058278. PMID: 34859686
Prenatal Diagnosis of Vascular Ring: Evaluation of Fetal Diagnosis and Postnatal Outcomes.
Aly S, Papneja K, Mawad W, Seed M, Jaeggi E, Yoo SJ
J Am Soc Echocardiogr 2022 Mar;35(3):312-321. Epub 2021 Sep 29 doi: 10.1016/j.echo.2021.09.010. PMID: 34600045
Isolated left subclavian artery in a right aortic arch: a rare association with distal arch hypoplasia, coarctation and ventricular septal defect.
Verma M, Pandey NN, Ojha V, Taxak A, Kumar S
Acta Cardiol 2021 Sep;76(7):803-804. Epub 2020 Jun 15 doi: 10.1080/00015385.2020.1778891. PMID: 32539563
Congenital abnormalities of the aortic arch: revisiting the 1964 Stewart classification.
Li S, Wen H, Liang M, Luo D, Qin Y, Liao Y, Ouyang S, Bi J, Tian X, Norwitz ER, Luo G
Cardiovasc Pathol 2019 Mar-Apr;39:38-50. Epub 2018 Dec 6 doi: 10.1016/j.carpath.2018.11.004. PMID: 30623879
Distal Aortic Arch Hypoplasia and Coarctation Repair: A Tailored Enlargement Technique.
Poncelet AJ, Henkens A, Sluysmans T, Moniotte S, de Beco G, Momeni M, Detaille T, Rubay JE
World J Pediatr Congenit Heart Surg 2018 Sep;9(5):496-503. doi: 10.1177/2150135118780611. PMID: 30157733

Therapy

Ultrasound Evaluation of Subclavian Artery and Internal Thoracic Artery Before Coronary Artery Bypass Grafting as Part of Preoperative Vascular Assessment.
Gao J, Li W, Zhu J, Liu Y, Tian H
Acad Radiol 2023 May;30(5):911-918. Epub 2022 Jul 9 doi: 10.1016/j.acra.2022.06.008. PMID: 35820976
Transposition of the left vertebral artery during endovascular stent-graft repair of the aortic arch.
Piffaretti G, Gelpi G, Tadiello M, Ferrarese S, Socrate AM, Tozzi M, Bellosta R
J Thorac Cardiovasc Surg 2020 Jun;159(6):2189-2198.e1. Epub 2019 Jun 15 doi: 10.1016/j.jtcvs.2019.06.011. PMID: 31301891
Management of type B aortic dissection with an isolated left vertebral artery.
Ding H, Zhu Y, Wang H, Luo S, Liu Y, Huang W, Dong H, Xue L, Fan R, Luo J
J Vasc Surg 2019 Oct;70(4):1065-1071. Epub 2019 Mar 2 doi: 10.1016/j.jvs.2018.11.052. PMID: 30837179
Advanced Techniques in Thoracic Endovascular Aortic Repair: Chimneys/Periscopes, Fenestrated Endografts, and Branched Devices.
Al-Hakim R, Schenning R
Tech Vasc Interv Radiol 2018 Sep;21(3):146-155. Epub 2018 Jun 14 doi: 10.1053/j.tvir.2018.06.004. PMID: 30497549
Early outcomes after left subclavian artery revascularisation in association with thoracic endovascular aortic repair.
Oladokun D, Patterson BO, Brownrigg JR, deBruin JL, Holt PJ, Loftus I, Thompson MM
Vascular 2017 Feb;25(1):74-79. Epub 2016 Jul 10 doi: 10.1177/1708538116647631. PMID: 27136950

Prognosis

Morphology of the left subclavian artery: implications for single-branched endovascular aortic arch repair.
Kondov S, Beyersdorf F, Braun N, Höhn R, Schlett C, Rylski B, Siepe M, Kreibich M, Gottardi R, Czerny M
Eur J Cardiothorac Surg 2022 Jan 24;61(2):348-354. doi: 10.1093/ejcts/ezab482. PMID: 34792129
Management of Interrupted Aortic Arch With Associated Anomalies: A Single-Center Experience.
Onalan MA, Temur B, Aydın S, Suzan D, Demir IH, Odemis E, Erek E
World J Pediatr Congenit Heart Surg 2021 Nov;12(6):706-714. doi: 10.1177/21501351211038508. PMID: 34846967
Fetal Echocardiographic Dimension Indices: Important Predictors of Postnatal Coarctation.
Fricke K, Liuba P, Weismann CG
Pediatr Cardiol 2021 Mar;42(3):517-525. Epub 2020 Dec 23 doi: 10.1007/s00246-020-02509-6. PMID: 33355680Free PMC Article
Congenital abnormalities of the aortic arch: revisiting the 1964 Stewart classification.
Li S, Wen H, Liang M, Luo D, Qin Y, Liao Y, Ouyang S, Bi J, Tian X, Norwitz ER, Luo G
Cardiovasc Pathol 2019 Mar-Apr;39:38-50. Epub 2018 Dec 6 doi: 10.1016/j.carpath.2018.11.004. PMID: 30623879
Distal Aortic Arch Hypoplasia and Coarctation Repair: A Tailored Enlargement Technique.
Poncelet AJ, Henkens A, Sluysmans T, Moniotte S, de Beco G, Momeni M, Detaille T, Rubay JE
World J Pediatr Congenit Heart Surg 2018 Sep;9(5):496-503. doi: 10.1177/2150135118780611. PMID: 30157733

Clinical prediction guides

Morphology of the left subclavian artery: implications for single-branched endovascular aortic arch repair.
Kondov S, Beyersdorf F, Braun N, Höhn R, Schlett C, Rylski B, Siepe M, Kreibich M, Gottardi R, Czerny M
Eur J Cardiothorac Surg 2022 Jan 24;61(2):348-354. doi: 10.1093/ejcts/ezab482. PMID: 34792129
Isolated Coarctation Repair in Neonates and Infants Through Left Thoracotomy: Short-Term Outcomes.
Murakami AN, Croti UA, Cajueiro FCM, Arteaga G, Pike RB, Moscardini AC, Marchi CH, Cardoso MRR, Santos FCGB, Borim BC
Braz J Cardiovasc Surg 2021 Aug 6;36(4):461-467. doi: 10.21470/1678-9741-2020-0554. PMID: 34617427Free PMC Article
Fetal Echocardiographic Dimension Indices: Important Predictors of Postnatal Coarctation.
Fricke K, Liuba P, Weismann CG
Pediatr Cardiol 2021 Mar;42(3):517-525. Epub 2020 Dec 23 doi: 10.1007/s00246-020-02509-6. PMID: 33355680Free PMC Article
Management of type B aortic dissection with an isolated left vertebral artery.
Ding H, Zhu Y, Wang H, Luo S, Liu Y, Huang W, Dong H, Xue L, Fan R, Luo J
J Vasc Surg 2019 Oct;70(4):1065-1071. Epub 2019 Mar 2 doi: 10.1016/j.jvs.2018.11.052. PMID: 30837179
Congenital abnormalities of the aortic arch: revisiting the 1964 Stewart classification.
Li S, Wen H, Liang M, Luo D, Qin Y, Liao Y, Ouyang S, Bi J, Tian X, Norwitz ER, Luo G
Cardiovasc Pathol 2019 Mar-Apr;39:38-50. Epub 2018 Dec 6 doi: 10.1016/j.carpath.2018.11.004. PMID: 30623879

Recent systematic reviews

Management of the left subclavian artery during endovascular stent grafting for traumatic aortic injury - a systematic review.
Sepehripour AH, Ahmed K, Vecht JA, Anagnostakou V, Suliman A, Ashrafian H, Darzi A, Athanasiou T
Eur J Vasc Endovasc Surg 2011 Jun;41(6):758-69. Epub 2011 Feb 22 doi: 10.1016/j.ejvs.2011.01.007. PMID: 21345700

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