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Colobomas, Uveoretinal

MedGen UID:
1633435
Concept ID:
C4554007
Congenital Abnormality
Synonyms: Coloboma, Uveoretinal; Uveoretinal Coloboma; Uveoretinal Colobomas
 
OMIM®: 120200

Professional guidelines

PubMed

Mustillo PJ, Sullivan KE, Chinn IK, Notarangelo LD, Haddad E, Davies EG, de la Morena MT, Hartog N, Yu JE, Hernandez-Trujillo VP, Ip W, Franco J, Gambineri E, Hickey SE, Varga E, Markert ML
J Clin Immunol 2023 Feb;43(2):247-270. Epub 2023 Jan 17 doi: 10.1007/s10875-022-01418-y. PMID: 36648576Free PMC Article
Marszałek-Kruk BA, Wójcicki P, Dowgierd K, Śmigiel R
Genes (Basel) 2021 Sep 9;12(9) doi: 10.3390/genes12091392. PMID: 34573374Free PMC Article
Verma IC, Paliwal P, Singh K
Indian J Pediatr 2018 Mar;85(3):228-236. Epub 2017 Oct 2 doi: 10.1007/s12098-017-2453-7. PMID: 28971364

Recent clinical studies

Etiology

Ratra D, Mohan S, Nadig R, Kashyap H
Indian J Ophthalmol 2023 Jun;71(6):2632. doi: 10.4103/IJO.IJO_250_23. PMID: 37322728Free PMC Article
Mustillo PJ, Sullivan KE, Chinn IK, Notarangelo LD, Haddad E, Davies EG, de la Morena MT, Hartog N, Yu JE, Hernandez-Trujillo VP, Ip W, Franco J, Gambineri E, Hickey SE, Varga E, Markert ML
J Clin Immunol 2023 Feb;43(2):247-270. Epub 2023 Jan 17 doi: 10.1007/s10875-022-01418-y. PMID: 36648576Free PMC Article
Lingam G, Sen AC, Lingam V, Bhende M, Padhi TR, Xinyi S
Eye (Lond) 2021 Aug;35(8):2086-2109. Epub 2021 Mar 21 doi: 10.1038/s41433-021-01501-5. PMID: 33746210Free PMC Article
Wieczorek D
Clin Genet 2013 Jun;83(6):499-510. Epub 2013 Apr 8 doi: 10.1111/cge.12123. PMID: 23565775
Friede H
Acta Odontol Scand 1995 Jun;53(3):203-9. doi: 10.3109/00016359509005973. PMID: 7572098

Diagnosis

Ratra D, Mohan S, Nadig R, Kashyap H
Indian J Ophthalmol 2023 Jun;71(6):2632. doi: 10.4103/IJO.IJO_250_23. PMID: 37322728Free PMC Article
Marszałek-Kruk BA, Wójcicki P, Dowgierd K, Śmigiel R
Genes (Basel) 2021 Sep 9;12(9) doi: 10.3390/genes12091392. PMID: 34573374Free PMC Article
Schimmenti LA
Eur J Hum Genet 2011 Dec;19(12):1207-12. Epub 2011 Jun 8 doi: 10.1038/ejhg.2011.102. PMID: 21654726Free PMC Article
Bloch-Zupan A, Goodman JR
Orphanet J Rare Dis 2006 Mar 21;1:5. doi: 10.1186/1750-1172-1-5. PMID: 16722606Free PMC Article
Onwochei BC, Simon JW, Bateman JB, Couture KC, Mir E
Surv Ophthalmol 2000 Nov-Dec;45(3):175-94. doi: 10.1016/s0039-6257(00)00151-x. PMID: 11094243

Therapy

Choudhary S, Katoch D, Pandav SS, Kaushik S
J Postgrad Med 2023 Jan-Mar;69(1):41-42. doi: 10.4103/jpgm.jpgm_1145_21. PMID: 35708396Free PMC Article
Angmo D, Dewan L, Behera A, Gagrani M
Eur J Ophthalmol 2021 Mar;31(2):NP116-NP118. Epub 2019 Jul 25 doi: 10.1177/1120672119866106. PMID: 31342778
Blake KD, Prasad C
Orphanet J Rare Dis 2006 Sep 7;1:34. doi: 10.1186/1750-1172-1-34. PMID: 16959034Free PMC Article
Peyman GA, Schulman JA, Sullivan B
Surv Ophthalmol 1995 Mar-Apr;39(5):375-95. doi: 10.1016/s0039-6257(05)80093-1. PMID: 7604361
Poswillo DE
Proc R Soc Med 1974 May;67(5):343-9. PMID: 4835278Free PMC Article

Prognosis

Ernst J, Medsinge A, Scanga HL, Hiasat J, Moore W, Ali A, Levin AV, Stahl ED, Nischal KK
J AAPOS 2022 Feb;26(1):4.e1-4.e5. Epub 2022 Jan 17 doi: 10.1016/j.jaapos.2021.09.008. PMID: 35051625
Colombo L, Maltese PE, Castori M, El Shamieh S, Zeitz C, Audo I, Zulian A, Marinelli C, Benedetti S, Costantini A, Bressan S, Percio M, Ferri P, Abeshi A, Bertelli M, Rossetti L
Invest Ophthalmol Vis Sci 2021 Feb 1;62(2):13. doi: 10.1167/iovs.62.2.13. PMID: 33576794Free PMC Article
Verma IC, Paliwal P, Singh K
Indian J Pediatr 2018 Mar;85(3):228-236. Epub 2017 Oct 2 doi: 10.1007/s12098-017-2453-7. PMID: 28971364
Demetrio R, Ruiz-Sancho D, Rolón N, del Campo A, Blanco C
Arch Soc Esp Oftalmol 2015 Mar;90(3):142-3. Epub 2014 Nov 15 doi: 10.1016/j.oftal.2014.02.012. PMID: 25443185
Onwochei BC, Simon JW, Bateman JB, Couture KC, Mir E
Surv Ophthalmol 2000 Nov-Dec;45(3):175-94. doi: 10.1016/s0039-6257(00)00151-x. PMID: 11094243

Clinical prediction guides

Smallwood K, Watt KEN, Ide S, Baltrunaite K, Brunswick C, Inskeep K, Capannari C, Adam MP, Begtrup A, Bertola DR, Demmer L, Demo E, Devinsky O, Gallagher ER, Guillen Sacoto MJ, Jech R, Keren B, Kussmann J, Ladda R, Lansdon LA, Lunke S, Mardy A, McWalters K, Person R, Raiti L, Saitoh N, Saunders CJ, Schnur R, Skorvanek M, Sell SL, Slavotinek A, Sullivan BR, Stark Z, Symonds JD, Wenger T, Weber S, Whalen S, White SM, Winkelmann J, Zech M, Zeidler S, Maeshima K, Stottmann RW, Trainor PA, Weaver KN
Am J Hum Genet 2023 May 4;110(5):809-825. Epub 2023 Apr 18 doi: 10.1016/j.ajhg.2023.03.014. PMID: 37075751Free PMC Article
de Geus CM, Free RH, Verbist BM, Sival DA, Blake KD, Meiners LC, van Ravenswaaij-Arts CMA
Am J Med Genet C Semin Med Genet 2017 Dec;175(4):450-464. Epub 2017 Nov 23 doi: 10.1002/ajmg.c.31593. PMID: 29168326Free PMC Article
Venincasa VD, Modi YS, Aziz HA, Ayres B, Zehetner C, Shi W, Murray TG, Flynn HW Jr, Berrocal AM
Invest Ophthalmol Vis Sci 2015 Jun;56(6):3615-20. doi: 10.1167/iovs.15-16596. PMID: 26047048Free PMC Article
Demetrio R, Ruiz-Sancho D, Rolón N, del Campo A, Blanco C
Arch Soc Esp Oftalmol 2015 Mar;90(3):142-3. Epub 2014 Nov 15 doi: 10.1016/j.oftal.2014.02.012. PMID: 25443185
Pian D, Ferrucci S, Anderson SF, Wu C
Optom Vis Sci 2003 Aug;80(8):556-63. doi: 10.1097/00006324-200308000-00008. PMID: 12917574

Recent systematic reviews

Mahmoud A, Pomar L, Lambert V, Picone O, Hcini N
Ocul Immunol Inflamm 2024 Nov;32(9):2217-2227. Epub 2024 Feb 13 doi: 10.1080/09273948.2024.2314086. PMID: 38350011
Ulhaq ZS, Nurputra DK, Soraya GV, Kurniawati S, Istifiani LA, Pamungkas SA, Tse WKF
Clin Genet 2023 Feb;103(2):146-155. Epub 2022 Oct 17 doi: 10.1111/cge.14243. PMID: 36203321
Thomas AT, Waite J, Williams CA, Kirk J, Oliver C, Richards C
J Neurodev Disord 2022 Aug 31;14(1):49. doi: 10.1186/s11689-022-09459-5. PMID: 36045324Free PMC Article
Amirhassankhani S, Lloyd MS
J Craniofac Surg 2018 Mar;29(2):372-375. doi: 10.1097/SCS.0000000000004201. PMID: 29239919
Plomp RG, van Lieshout MJS, Joosten KFM, Wolvius EB, van der Schroeff MP, Versnel SL, Poublon RML, Mathijssen IMJ
Plast Reconstr Surg 2016 Jan;137(1):191-204. doi: 10.1097/PRS.0000000000001896. PMID: 26710023

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