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Infantile sensorineural hearing impairment

MedGen UID:
867177
Concept ID:
C4021535
Finding
Synonym: Infantile sensorineural hearing loss
 
HPO: HP:0008610

Definition

A form of sensorineural hearing impairment with infantile onset. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVInfantile sensorineural hearing impairment

Professional guidelines

PubMed

Drovandi S, Lipska-Ziętkiewicz BS, Ozaltin F, Emma F, Gulhan B, Boyer O, Trautmann A, Ziętkiewicz S, Xu H, Shen Q, Rao J, Riedhammer KM, Heemann U, Hoefele J, Stenton SL, Tsygin AN, Ng KH, Fomina S, Benetti E, Aurelle M, Prikhodina L, Schijvens AM, Tabatabaeifar M, Jankowski M, Baiko S, Mao J, Feng C, Deng F, Rousset-Rouviere C, Stańczyk M, Bałasz-Chmielewska I, Fila M, Durkan AM, Levart TK, Dursun I, Esfandiar N, Haas D, Bjerre A, Anarat A, Benz MR, Talebi S, Hooman N, Ariceta G; PodoNet Consortium; mitoNET Consortium; CCGKDD Consortium, Schaefer F
Kidney Int 2022 Sep;102(3):592-603. Epub 2022 Apr 26 doi: 10.1016/j.kint.2022.02.040. PMID: 35483523
Mehr S, Allen R, Boros C, Adib N, Kakakios A, Turner PJ, Rogers M, Zurynski Y, Singh-Grewal D
J Paediatr Child Health 2016 Sep;52(9):889-95. doi: 10.1111/jpc.13270. PMID: 27650144
Rösen-Wolff A, Quietzsch J, Schröder H, Lehmann R, Gahr M, Roesler J
Eur J Haematol 2003 Sep;71(3):215-9. doi: 10.1034/j.1600-0609.2003.00109.x. PMID: 12930324

Recent clinical studies

Etiology

Bryant D, Pauzuolyte V, Ingham NJ, Patel A, Pagarkar W, Anderson LA, Smith KE, Moulding DA, Leong YC, Jafree DJ, Long DA, Al-Yassin A, Steel KP, Jagger DJ, Forge A, Berger W, Sowden JC, Bitner-Glindzicz M
JCI Insight 2022 Feb 8;7(3) doi: 10.1172/jci.insight.148586. PMID: 35132964Free PMC Article
Hsueh CY, Huang CY, Yang CF, Chang CC, Lin WS, Cheng HL, Wu SL, Cheng YF, Niu DM
Orphanet J Rare Dis 2021 Aug 5;16(1):348. doi: 10.1186/s13023-021-01817-1. PMID: 34353347Free PMC Article
Srivastava S, D'Amore A, Cohen JS, Swanson LC, Ricca I, Pini A, Fatemi A, Ebrahimi-Fakhari D, Santorelli FM
Ann Clin Transl Neurol 2020 Apr;7(4):573-578. Epub 2020 Mar 8 doi: 10.1002/acn3.51007. PMID: 32147972Free PMC Article
Finetti M, Omenetti A, Federici S, Caorsi R, Gattorno M
Orphanet J Rare Dis 2016 Dec 7;11(1):167. doi: 10.1186/s13023-016-0542-8. PMID: 27927236Free PMC Article
Paparella MM, Shea D, Meyerhoff WL, Goycoolea MV
Laryngoscope 1980 Jul;90(7 Pt 1):1089-98. doi: 10.1288/00005537-198007000-00003. PMID: 7392745

Diagnosis

Drovandi S, Lipska-Ziętkiewicz BS, Ozaltin F, Emma F, Gulhan B, Boyer O, Trautmann A, Ziętkiewicz S, Xu H, Shen Q, Rao J, Riedhammer KM, Heemann U, Hoefele J, Stenton SL, Tsygin AN, Ng KH, Fomina S, Benetti E, Aurelle M, Prikhodina L, Schijvens AM, Tabatabaeifar M, Jankowski M, Baiko S, Mao J, Feng C, Deng F, Rousset-Rouviere C, Stańczyk M, Bałasz-Chmielewska I, Fila M, Durkan AM, Levart TK, Dursun I, Esfandiar N, Haas D, Bjerre A, Anarat A, Benz MR, Talebi S, Hooman N, Ariceta G; PodoNet Consortium; mitoNET Consortium; CCGKDD Consortium, Schaefer F
Kidney Int 2022 Sep;102(3):592-603. Epub 2022 Apr 26 doi: 10.1016/j.kint.2022.02.040. PMID: 35483523
Bryant D, Pauzuolyte V, Ingham NJ, Patel A, Pagarkar W, Anderson LA, Smith KE, Moulding DA, Leong YC, Jafree DJ, Long DA, Al-Yassin A, Steel KP, Jagger DJ, Forge A, Berger W, Sowden JC, Bitner-Glindzicz M
JCI Insight 2022 Feb 8;7(3) doi: 10.1172/jci.insight.148586. PMID: 35132964Free PMC Article
Hsueh CY, Huang CY, Yang CF, Chang CC, Lin WS, Cheng HL, Wu SL, Cheng YF, Niu DM
Orphanet J Rare Dis 2021 Aug 5;16(1):348. doi: 10.1186/s13023-021-01817-1. PMID: 34353347Free PMC Article
Ralli M, Rolesi R, Anzivino R, Turchetta R, Fetoni AR
Acta Otorhinolaryngol Ital 2017 Dec;37(6):500-508. doi: 10.14639/0392-100X-1574. PMID: 29327735Free PMC Article
Finetti M, Omenetti A, Federici S, Caorsi R, Gattorno M
Orphanet J Rare Dis 2016 Dec 7;11(1):167. doi: 10.1186/s13023-016-0542-8. PMID: 27927236Free PMC Article

Therapy

Hsueh CY, Huang CY, Yang CF, Chang CC, Lin WS, Cheng HL, Wu SL, Cheng YF, Niu DM
Orphanet J Rare Dis 2021 Aug 5;16(1):348. doi: 10.1186/s13023-021-01817-1. PMID: 34353347Free PMC Article
Wubben TJ, Branham KH, Besirli CG, Bohnsack BL
Ophthalmic Genet 2018 Oct;39(5):615-618. Epub 2018 Aug 21 doi: 10.1080/13816810.2018.1509355. PMID: 30130436
Ralli M, Rolesi R, Anzivino R, Turchetta R, Fetoni AR
Acta Otorhinolaryngol Ital 2017 Dec;37(6):500-508. doi: 10.14639/0392-100X-1574. PMID: 29327735Free PMC Article
Prater SN, Banugaria SG, DeArmey SM, Botha EG, Stege EM, Case LE, Jones HN, Phornphutkul C, Wang RY, Young SP, Kishnani PS
Genet Med 2012 Sep;14(9):800-10. Epub 2012 Apr 26 doi: 10.1038/gim.2012.44. PMID: 22538254Free PMC Article
van Capelle CI, Goedegebure A, Homans NC, Hoeve HL, Reuser AJ, van der Ploeg AT
J Inherit Metab Dis 2010 Oct;33(5):597-602. Epub 2010 Jul 2 doi: 10.1007/s10545-010-9144-0. PMID: 20596893Free PMC Article

Prognosis

Salvago P, Immordino A, Vaccaro D, Plescia F, Dispenza F, Sireci F, Martines F
Eur Arch Otorhinolaryngol 2024 Jan;281(1):163-170. Epub 2023 Jul 12 doi: 10.1007/s00405-023-08119-1. PMID: 37436499
Bryant D, Pauzuolyte V, Ingham NJ, Patel A, Pagarkar W, Anderson LA, Smith KE, Moulding DA, Leong YC, Jafree DJ, Long DA, Al-Yassin A, Steel KP, Jagger DJ, Forge A, Berger W, Sowden JC, Bitner-Glindzicz M
JCI Insight 2022 Feb 8;7(3) doi: 10.1172/jci.insight.148586. PMID: 35132964Free PMC Article
Keshavan N, Abdenur J, Anderson G, Assouline Z, Barcia G, Bouhikbar L, Chakrapani A, Cleary M, Cohen MC, Feillet F, Fratter C, Hauser N, Jacques T, Lam A, McCullagh H, Phadke R, Rötig A, Sharrard M, Simon M, Smith C, Sommerville EW, Taylor RW, Yue WW, Rahman S
Genet Med 2020 Jan;22(1):199-209. Epub 2019 Aug 29 doi: 10.1038/s41436-019-0613-z. PMID: 31462754
Wubben TJ, Branham KH, Besirli CG, Bohnsack BL
Ophthalmic Genet 2018 Oct;39(5):615-618. Epub 2018 Aug 21 doi: 10.1080/13816810.2018.1509355. PMID: 30130436
Finetti M, Omenetti A, Federici S, Caorsi R, Gattorno M
Orphanet J Rare Dis 2016 Dec 7;11(1):167. doi: 10.1186/s13023-016-0542-8. PMID: 27927236Free PMC Article

Clinical prediction guides

Drovandi S, Lipska-Ziętkiewicz BS, Ozaltin F, Emma F, Gulhan B, Boyer O, Trautmann A, Ziętkiewicz S, Xu H, Shen Q, Rao J, Riedhammer KM, Heemann U, Hoefele J, Stenton SL, Tsygin AN, Ng KH, Fomina S, Benetti E, Aurelle M, Prikhodina L, Schijvens AM, Tabatabaeifar M, Jankowski M, Baiko S, Mao J, Feng C, Deng F, Rousset-Rouviere C, Stańczyk M, Bałasz-Chmielewska I, Fila M, Durkan AM, Levart TK, Dursun I, Esfandiar N, Haas D, Bjerre A, Anarat A, Benz MR, Talebi S, Hooman N, Ariceta G; PodoNet Consortium; mitoNET Consortium; CCGKDD Consortium, Schaefer F
Kidney Int 2022 Sep;102(3):592-603. Epub 2022 Apr 26 doi: 10.1016/j.kint.2022.02.040. PMID: 35483523
Hsueh CY, Huang CY, Yang CF, Chang CC, Lin WS, Cheng HL, Wu SL, Cheng YF, Niu DM
Orphanet J Rare Dis 2021 Aug 5;16(1):348. doi: 10.1186/s13023-021-01817-1. PMID: 34353347Free PMC Article
Sakaguchi Y, Yoshihashi H, Uehara T, Miyama S, Kosaki K, Takenouchi T
Am J Med Genet A 2021 Mar;185(3):884-888. Epub 2020 Dec 27 doi: 10.1002/ajmg.a.62020. PMID: 33369122
Yaramis A
Med Hypotheses 2020 Sep;142:109796. Epub 2020 Apr 30 doi: 10.1016/j.mehy.2020.109796. PMID: 32388477
Finetti M, Omenetti A, Federici S, Caorsi R, Gattorno M
Orphanet J Rare Dis 2016 Dec 7;11(1):167. doi: 10.1186/s13023-016-0542-8. PMID: 27927236Free PMC Article

Recent systematic reviews

Drovandi S, Lipska-Ziętkiewicz BS, Ozaltin F, Emma F, Gulhan B, Boyer O, Trautmann A, Ziętkiewicz S, Xu H, Shen Q, Rao J, Riedhammer KM, Heemann U, Hoefele J, Stenton SL, Tsygin AN, Ng KH, Fomina S, Benetti E, Aurelle M, Prikhodina L, Schijvens AM, Tabatabaeifar M, Jankowski M, Baiko S, Mao J, Feng C, Deng F, Rousset-Rouviere C, Stańczyk M, Bałasz-Chmielewska I, Fila M, Durkan AM, Levart TK, Dursun I, Esfandiar N, Haas D, Bjerre A, Anarat A, Benz MR, Talebi S, Hooman N, Ariceta G; PodoNet Consortium; mitoNET Consortium; CCGKDD Consortium, Schaefer F
Kidney Int 2022 Sep;102(3):592-603. Epub 2022 Apr 26 doi: 10.1016/j.kint.2022.02.040. PMID: 35483523

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