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Chronic pneumonitis of infancy

MedGen UID:
846677
•Concept ID:
C3872848
•
Disease or Syndrome
Synonyms: chronic pneumonitis of infancy; CPI; CPI - chronic pneumonitis of infancy
SNOMED CT: Chronic pneumonitis of infancy (708026002); CPI - chronic pneumonitis of infancy (708026002)
Modes of inheritance:
Not genetically inherited
MedGen UID:
988794
•Concept ID:
CN307044
•
Finding
Source: Orphanet
clinical entity without genetic inheritance.
See: This record
Not genetically inherited (Orphanet)
 
Monarch Initiative: MONDO:0019621
Orphanet: ORPHA91359

Definition

Chronic pneumonitis of infancy is a rare pediatric form of interstitial lung disease (ILD, see this term). [from ORDO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVChronic pneumonitis of infancy

Professional guidelines

PubMed

Indian Academy of Pediatrics Revised (2021) Guidelines on Prevention and Treatment of Vitamin D Deficiency and Rickets.
Gupta P, Dabas A, Seth A, Bhatia VL, Khadgawat R, Kumar P, Balasubramanian S, Khadilkar V, Mallikarjuna HB, Godbole T, Krishnamurthy S, Goyal JP, Bhakhri BK, Ahmad A, Angadi K, Basavaraj GV, Parekh BJ, Kurpad A, Marwaha RK, Shah D, Munns C, Sachdev HPS
Indian Pediatr 2022 Feb 15;59(2):142-158. Epub 2021 Dec 29 PMID: 34969941
Management of inflammatory bowel disease during the COVID-19 pandemic.
Hisamatsu T
Immunol Med 2022 Sep;45(3):128-135. Epub 2021 Sep 16 doi: 10.1080/25785826.2021.1978205. PMID: 34530694
Consensus statement of the Italian society of pediatric allergy and immunology for the pragmatic management of children and adolescents with allergic or immunological diseases during the COVID-19 pandemic.
Cardinale F, Ciprandi G, Barberi S, Bernardini R, Caffarelli C, Calvani M, Cavagni G, Galli E, Minasi D, Del Giudice MM, Moschese V, Novembre E, Paravati F, Peroni DG, Tosca MA, Traina G, Tripodi S, Marseglia GL; and the SIAIP Task Force
Ital J Pediatr 2020 Jun 16;46(1):84. doi: 10.1186/s13052-020-00843-2. PMID: 32546234Free PMC Article

Recent clinical studies

Etiology

ABCA3-related interstitial lung disease beyond infancy.
Li Y, Seidl E, Knoflach K, Gothe F, Forstner ME, Michel K, Pawlita I, Gesenhues F, Sattler F, Yang X, Kroener C, Reu-Hofer S, Ley-Zaporozhan J, Kammer B, Krüger-Stollfuß I, Dinkel J, Carlens J, Wetzke M, Moreno-Galdó A, Torrent-Vernetta A, Lange J, Krenke K, Rumman N, Mayell S, Sismanlar T, Aslan A, Regamey N, Proesmans M, Stehling F, Naehrlich L, Ayse K, Becker S, Koerner-Rettberg C, Plattner E, Manali ED, Papiris SA, Campo I, Kappler M, Schwerk N, Griese M
Thorax 2023 Jun;78(6):587-595. Epub 2023 Feb 20 doi: 10.1136/thorax-2022-219434. PMID: 36808083Free PMC Article
Lung transplantation in young infants with interstitial pneumonia.
Moreno A, Maestre J, Balcells J, Marhuenda C, Cobos N, Roman A, Soler J, Montferrer N, Liñan S, Gartner S, Roqueta J, Majo J
Transplant Proc 2003 Aug;35(5):1951-3. doi: 10.1016/s0041-1345(03)00665-1. PMID: 12962860
Chronic pneumonitis of infancy. An autopsy study of 12 cases.
Kavantzas N, Theocharis S, Agapitos E, Davaris P
Clin Exp Pathol 1999;47(2):96-100. PMID: 10398582
The value of classifying interstitial pneumonitis in childhood according to defined histological patterns.
Nicholson AG, Kim H, Corrin B, Bush A, du Bois RM, Rosenthal M, Sheppard MN
Histopathology 1998 Sep;33(3):203-11. doi: 10.1046/j.1365-2559.1998.00488.x. PMID: 9777385

Diagnosis

ABCA3-related interstitial lung disease beyond infancy.
Li Y, Seidl E, Knoflach K, Gothe F, Forstner ME, Michel K, Pawlita I, Gesenhues F, Sattler F, Yang X, Kroener C, Reu-Hofer S, Ley-Zaporozhan J, Kammer B, Krüger-Stollfuß I, Dinkel J, Carlens J, Wetzke M, Moreno-Galdó A, Torrent-Vernetta A, Lange J, Krenke K, Rumman N, Mayell S, Sismanlar T, Aslan A, Regamey N, Proesmans M, Stehling F, Naehrlich L, Ayse K, Becker S, Koerner-Rettberg C, Plattner E, Manali ED, Papiris SA, Campo I, Kappler M, Schwerk N, Griese M
Thorax 2023 Jun;78(6):587-595. Epub 2023 Feb 20 doi: 10.1136/thorax-2022-219434. PMID: 36808083Free PMC Article
Infant pulmonary function testing in chronic pneumonitis of infancy due to surfactant protein C mutation.
Hevroni A, Goldman A, Springer C
Pediatr Pulmonol 2015 Jun;50(6):E17-23. Epub 2015 Mar 9 doi: 10.1002/ppul.23166. PMID: 25755194
Chronic pneumonitis of infancy: high-resolution CT findings.
Olsen E ØE, Sebire NJ, Jaffe A, Owens CM
Pediatr Radiol 2004 Jan;34(1):86-8. Epub 2003 Sep 18 doi: 10.1007/s00247-003-1059-6. PMID: 14504845
Chronic pneumonitis of infancy.
Abe K, Kamata N, Okazaki E, Moriyama S, Funata N, Takita J, Yamada H, Takayama N
Eur Radiol 2002 Dec;12 Suppl 3:S155-7. Epub 2002 Jun 26 doi: 10.1007/s00330-002-1496-x. PMID: 12522629
Chronic pneumonitis of infancy. A unique form of interstitial lung disease occurring in early childhood.
Katzenstein AL, Gordon LP, Oliphant M, Swender PT
Am J Surg Pathol 1995 Apr;19(4):439-47. PMID: 7694945

Prognosis

ABCA3-related interstitial lung disease beyond infancy.
Li Y, Seidl E, Knoflach K, Gothe F, Forstner ME, Michel K, Pawlita I, Gesenhues F, Sattler F, Yang X, Kroener C, Reu-Hofer S, Ley-Zaporozhan J, Kammer B, Krüger-Stollfuß I, Dinkel J, Carlens J, Wetzke M, Moreno-Galdó A, Torrent-Vernetta A, Lange J, Krenke K, Rumman N, Mayell S, Sismanlar T, Aslan A, Regamey N, Proesmans M, Stehling F, Naehrlich L, Ayse K, Becker S, Koerner-Rettberg C, Plattner E, Manali ED, Papiris SA, Campo I, Kappler M, Schwerk N, Griese M
Thorax 2023 Jun;78(6):587-595. Epub 2023 Feb 20 doi: 10.1136/thorax-2022-219434. PMID: 36808083Free PMC Article
Lung transplantation in young infants with interstitial pneumonia.
Moreno A, Maestre J, Balcells J, Marhuenda C, Cobos N, Roman A, Soler J, Montferrer N, Liñan S, Gartner S, Roqueta J, Majo J
Transplant Proc 2003 Aug;35(5):1951-3. doi: 10.1016/s0041-1345(03)00665-1. PMID: 12962860
Chronic pneumonitis of infancy. An autopsy study of 12 cases.
Kavantzas N, Theocharis S, Agapitos E, Davaris P
Clin Exp Pathol 1999;47(2):96-100. PMID: 10398582

Clinical prediction guides

ABCA3-related interstitial lung disease beyond infancy.
Li Y, Seidl E, Knoflach K, Gothe F, Forstner ME, Michel K, Pawlita I, Gesenhues F, Sattler F, Yang X, Kroener C, Reu-Hofer S, Ley-Zaporozhan J, Kammer B, Krüger-Stollfuß I, Dinkel J, Carlens J, Wetzke M, Moreno-Galdó A, Torrent-Vernetta A, Lange J, Krenke K, Rumman N, Mayell S, Sismanlar T, Aslan A, Regamey N, Proesmans M, Stehling F, Naehrlich L, Ayse K, Becker S, Koerner-Rettberg C, Plattner E, Manali ED, Papiris SA, Campo I, Kappler M, Schwerk N, Griese M
Thorax 2023 Jun;78(6):587-595. Epub 2023 Feb 20 doi: 10.1136/thorax-2022-219434. PMID: 36808083Free PMC Article

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