U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Heterotopia, Periventricular, Ehlers-Danlos Variant

MedGen UID:
375610
Concept ID:
C1845235
Congenital Abnormality
Synonym: Periventricular Nodular Heterotopia 4
 
OMIM®: 300049

Recent clinical studies

Etiology

Billon C, Adham S, Hernandez Poblete N, Legrand A, Frank M, Chiche L, Zuily S, Benistan K, Savale L, Zaafrane-Khachnaoui K, Brehin AC, Bal L, Busa T, Fradin M, Quelin C, Chesneau B, Wahl D, Fergelot P, Goizet C, Mirault T, Jeunemaitre X, Albuisson J; Bordeaux-cohort collaborators
Orphanet J Rare Dis 2021 Dec 4;16(1):504. doi: 10.1186/s13023-021-02128-1. PMID: 34863227Free PMC Article
Reinstein E, Frentz S, Morgan T, García-Miñaúr S, Leventer RJ, McGillivray G, Pariani M, van der Steen A, Pope M, Holder-Espinasse M, Scott R, Thompson EM, Robertson T, Coppin B, Siegel R, Bret Zurita M, Rodríguez JI, Morales C, Rodrigues Y, Arcas J, Saggar A, Horton M, Zackai E, Graham JM, Rimoin DL, Robertson SP
Eur J Hum Genet 2013 May;21(5):494-502. Epub 2012 Oct 3 doi: 10.1038/ejhg.2012.209. PMID: 23032111Free PMC Article
Parrini E, Ramazzotti A, Dobyns WB, Mei D, Moro F, Veggiotti P, Marini C, Brilstra EH, Dalla Bernardina B, Goodwin L, Bodell A, Jones MC, Nangeroni M, Palmeri S, Said E, Sander JW, Striano P, Takahashi Y, Van Maldergem L, Leonardi G, Wright M, Walsh CA, Guerrini R
Brain 2006 Jul;129(Pt 7):1892-906. Epub 2006 May 9 doi: 10.1093/brain/awl125. PMID: 16684786
Gómez-Garre P, Seijo M, Gutiérrez-Delicado E, Castro del Río M, de la Torre C, Gómez-Abad C, Morales-Corraliza J, Puig M, Serratosa JM
J Med Genet 2006 Mar;43(3):232-7. Epub 2005 Jul 1 doi: 10.1136/jmg.2004.029173. PMID: 15994863Free PMC Article

Diagnosis

Billon C, Adham S, Hernandez Poblete N, Legrand A, Frank M, Chiche L, Zuily S, Benistan K, Savale L, Zaafrane-Khachnaoui K, Brehin AC, Bal L, Busa T, Fradin M, Quelin C, Chesneau B, Wahl D, Fergelot P, Goizet C, Mirault T, Jeunemaitre X, Albuisson J; Bordeaux-cohort collaborators
Orphanet J Rare Dis 2021 Dec 4;16(1):504. doi: 10.1186/s13023-021-02128-1. PMID: 34863227Free PMC Article

Clinical prediction guides

Reinstein E, Frentz S, Morgan T, García-Miñaúr S, Leventer RJ, McGillivray G, Pariani M, van der Steen A, Pope M, Holder-Espinasse M, Scott R, Thompson EM, Robertson T, Coppin B, Siegel R, Bret Zurita M, Rodríguez JI, Morales C, Rodrigues Y, Arcas J, Saggar A, Horton M, Zackai E, Graham JM, Rimoin DL, Robertson SP
Eur J Hum Genet 2013 May;21(5):494-502. Epub 2012 Oct 3 doi: 10.1038/ejhg.2012.209. PMID: 23032111Free PMC Article

Supplemental Content

Table of contents

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...