Periosteal osteogenic sarcoma

MedGen UID:: 234607
•Concept ID:: C1377843
•: Neoplastic Process

Synonyms:	Juxtacortical Chondroblastic Osteosarcoma; juxtacortical chondroblastic osteosarcoma; PEOS; periosteal osteogenic sarcoma; Periosteal osteosarcoma; Periosteal Osteosarcoma; periosteal osteosarcoma; periosteal osteosarcoma (morphologic abnormality)
SNOMED CT:	Periosteal osteosarcoma (128772005); Periosteal osteosarcoma (1290870008)

Monarch Initiative:	MONDO:0003895

Definition

An intermediate grade malignant bone-forming mesenchymal neoplasm with chondroblastic differentiation. It arises from the surface of the bone and affects the diaphysis or diaphyseal- metaphyseal portion of the long bones. A painless mass or swelling is the most common clinical sign. It is associated with a better prognosis than conventional osteosarcoma. [from NCI]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVPeriosteal osteogenic sarcoma

Bone Neoplasm
- Bone cancer
  - Bone sarcoma
    - Bone osteosarcoma
      - Primary Bone Osteosarcoma
        Peripheral osteosarcoma
        Periosteal osteogenic sarcoma
        Childhood Periosteal Osteosarcoma

Professional guidelines

PubMed

Biology and Management of High-Grade Chondrosarcoma: An Update on Targets and Treatment Options.

Tlemsani C, Larousserie F, De Percin S, Audard V, Hadjadj D, Chen J, Biau D, Anract P, Terris B, Goldwasser F, Pasmant E, Boudou-Rouquette P
Int J Mol Sci 2023 Jan 10;24(2) doi: 10.3390/ijms24021361. PMID: 36674874 Free PMC Article

Osteosarcoma of the jaw: Challenges in the diagnosis and treatment.

ElKordy MA, ElBaradie TS, ElSebai HI, KhairAlla SM, Amin AAE
J Egypt Natl Canc Inst 2018 Mar;30(1):7-11. Epub 2018 Feb 26 doi: 10.1016/j.jnci.2018.02.001. PMID: 29490886

Ewing's sarcoma family of tumors: current management.

Bernstein M, Kovar H, Paulussen M, Randall RL, Schuck A, Teot LA, Juergens H
Oncologist 2006 May;11(5):503-19. doi: 10.1634/theoncologist.11-5-503. PMID: 16720851

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Recent clinical studies

Etiology

Limb-salvage operations in primary malignant tumors of the bone--interim report.

Lee SY, Baek GH
J Korean Med Sci 1990 Dec;5(4):205-12. doi: 10.3346/jkms.1990.5.4.205. PMID: 1966035 Free PMC Article

Periosteal osteogenic sarcoma.

Unni KK, Dahlin DC, Beabout JW
Cancer 1976 May;37(5):2476-85. doi: 10.1002/1097-0142(197605)37:5<2476::aid-cncr2820370541>3.0.co;2-c. PMID: 1063059

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Diagnosis

Cortical lesions of the tibia: characteristic appearances at conventional radiography.

Levine SM, Lambiase RE, Petchprapa CN
Radiographics 2003 Jan-Feb;23(1):157-77. doi: 10.1148/rg.231015088. PMID: 12533651

Limb-salvage operations in primary malignant tumors of the bone--interim report.

Lee SY, Baek GH
J Korean Med Sci 1990 Dec;5(4):205-12. doi: 10.3346/jkms.1990.5.4.205. PMID: 1966035 Free PMC Article

Test and teach. Number fifty-nine. Diagnosis: Periosteal osteogenic sarcoma.

Chan MK, McGuire LJ
Pathology 1989 Jan;21(1):17-8, 65-6. doi: 10.3109/00313028909059523. PMID: 2668864

Periosteal osteogenic sarcoma of the mandible.

Zarbo RJ, Regezi JA, Baker SR
Oral Surg Oral Med Oral Pathol 1984 Jun;57(6):643-7. doi: 10.1016/0030-4220(84)90287-1. PMID: 6588346

Metastatic periosteal osteosarcoma causing cardiac and renal failure.

Dash H, Little JR, Zaino R, Colao DJ, Chaurushiya P, Schoolwerth AC, O'Neill MJ, Hart JC, Martin GB
Am J Med 1983 Jul;75(1):145-9. doi: 10.1016/0002-9343(83)91178-6. PMID: 6574700

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