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Progonoma

MedGen UID:
689801
•Concept ID:
C1265730
•
Anatomical Abnormality
SNOMED CT: Progonoma (125239005)

Recent clinical studies

Etiology

Melanotic neuroectodermal tumor of infancy (MNTI) of the head and neck: A French multicenter study.
Moreau A, Galmiche L, Minard-Colin V, Rachwalski M, Belhous K, Orbach D, Joly A, Picard A, Kadlub N
J Craniomaxillofac Surg 2018 Feb;46(2):201-206. Epub 2017 Dec 12 doi: 10.1016/j.jcms.2017.12.001. PMID: 29275074
Giant melanotic neuroectodermal tumor of infancy (melanotic progonoma) of the head and neck: report of a malignant case.
Nicosia G, Spennato P, Aliberti F, Cascone D, Quaglietta L, Errico ME, Muto M, Ionna F, Cinalli G
J Neurosurg Pediatr 2017 May;19(5):538-545. Epub 2017 Feb 24 doi: 10.3171/2016.11.PEDS16509. PMID: 28291424
Early outcome of three cases of melanotic neuroectodermal tumour of infancy.
Butt FM, Guthua SW, Chindia ML, Rana F, Osundwa TM
J Craniomaxillofac Surg 2009 Dec;37(8):434-7. doi: 10.1016/j.jcms.2009.03.016. PMID: 19836964
Orbital melanotic neuroectodermal tumor of infancy successfully treated with chemotherapy and subtotal excision.
Hered RW, Smithwick W 4th, Sandler E, Goldstein JD
J AAPOS 2007 Oct;11(5):504-5. Epub 2007 May 29 doi: 10.1016/j.jaapos.2007.03.010. PMID: 17532239
Melanotic progonoma (retinoblastoma) of maxilla. Case report.
De Cholnoky T
Plast Reconstr Surg 1970 Dec;46(6):600-3. doi: 10.1097/00006534-197012000-00015. PMID: 5493028

Diagnosis

Melanotic neuroectodermal tumor of infancy (MNTI) of the head and neck: A French multicenter study.
Moreau A, Galmiche L, Minard-Colin V, Rachwalski M, Belhous K, Orbach D, Joly A, Picard A, Kadlub N
J Craniomaxillofac Surg 2018 Feb;46(2):201-206. Epub 2017 Dec 12 doi: 10.1016/j.jcms.2017.12.001. PMID: 29275074
Melanotic Neuroectodermal Tumor of Infancy Presenting With Fast-Growing Scrotal Swelling: A Case Report and Literature Review.
Fabien-Dupuis C, Niver B, Shillingford N, Wang L, Kokorowski PJ, Zhou S
Pediatr Dev Pathol 2017 Sep-Oct;20(5):411-415. Epub 2017 Jan 25 doi: 10.1177/1093526616686437. PMID: 28812465
Giant melanotic neuroectodermal tumor of infancy (melanotic progonoma) of the head and neck: report of a malignant case.
Nicosia G, Spennato P, Aliberti F, Cascone D, Quaglietta L, Errico ME, Muto M, Ionna F, Cinalli G
J Neurosurg Pediatr 2017 May;19(5):538-545. Epub 2017 Feb 24 doi: 10.3171/2016.11.PEDS16509. PMID: 28291424
Melanotic progonoma of the skull in infancy.
Kantar M, Sezak M, Turhan T, Kitis O, Mutluer S, Demirag BK, Aksoylar S, Akalin T, Ersahin Y, Cetingul N
Childs Nerv Syst 2008 Nov;24(11):1371-5. Epub 2008 Jul 1 doi: 10.1007/s00381-008-0664-y. PMID: 18592253
Rare primary cranial vault and base of the skull tumors in children. Report of 30 cases with a short literature review.
Kozlowski K, Campbell J, McAlister W, Babyn P, Cama A, Masel J, Pelizza A, Taccone A
Radiol Med 1991 Mar;81(3):213-24. PMID: 2014322

Therapy

Orbital melanotic neuroectodermal tumor of infancy successfully treated with chemotherapy and subtotal excision.
Hered RW, Smithwick W 4th, Sandler E, Goldstein JD
J AAPOS 2007 Oct;11(5):504-5. Epub 2007 May 29 doi: 10.1016/j.jaapos.2007.03.010. PMID: 17532239

Prognosis

Giant melanotic neuroectodermal tumor of infancy (melanotic progonoma) of the head and neck: report of a malignant case.
Nicosia G, Spennato P, Aliberti F, Cascone D, Quaglietta L, Errico ME, Muto M, Ionna F, Cinalli G
J Neurosurg Pediatr 2017 May;19(5):538-545. Epub 2017 Feb 24 doi: 10.3171/2016.11.PEDS16509. PMID: 28291424
Early outcome of three cases of melanotic neuroectodermal tumour of infancy.
Butt FM, Guthua SW, Chindia ML, Rana F, Osundwa TM
J Craniomaxillofac Surg 2009 Dec;37(8):434-7. doi: 10.1016/j.jcms.2009.03.016. PMID: 19836964
Large cell medulloblastoma with myogenic and melanotic differentiation: a case report with molecular analysis.
Polydorides AD, Perry A, Edgar MA
J Neurooncol 2008 Jun;88(2):193-7. doi: 10.1007/s11060-008-9548-y. PMID: 18317693
Melanotic progonoma of the brain: a case report and review.
Rickert CH, Probst-Cousin S, Blasius S, Gullotta F
Childs Nerv Syst 1998 Aug;14(8):389-93. doi: 10.1007/s003810050251. PMID: 9753407
Melanotic progonoma (retinoblastoma) of maxilla. Case report.
De Cholnoky T
Plast Reconstr Surg 1970 Dec;46(6):600-3. doi: 10.1097/00006534-197012000-00015. PMID: 5493028

Clinical prediction guides

Diagnostic significance of coexpression of intermediate filaments in fine needle aspirates of human tumors.
Domagala W, Weber K, Osborn M
Acta Cytol 1988 Jan-Feb;32(1):49-59. PMID: 2447723
Studies on melanocytes. V. The presence of melanocytes in the human dental primordium: an explanation for pigmented lesions of the jaws.
Lawson W, Abaci IF, Zak FG
Oral Surg Oral Med Oral Pathol 1976 Sep;42(3):375-80. doi: 10.1016/0030-4220(76)90171-7. PMID: 1067535

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