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Choreas, Chronic Progressive

MedGen UID:
152114
Concept ID:
C0699728
Disease or Syndrome
Synonyms: Chorea, Chronic Progressive; Chronic Progressive Chorea; Chronic Progressive Choreas; Progressive Chorea, Chronic; Progressive Choreas, Chronic

Professional guidelines

PubMed

Stoker TB, Mason SL, Greenland JC, Holden ST, Santini H, Barker RA
Pract Neurol 2022 Feb;22(1):32-41. Epub 2021 Aug 19 doi: 10.1136/practneurol-2021-003074. PMID: 34413240
Kim A, Lalonde K, Truesdell A, Gomes Welter P, Brocardo PS, Rosenstock TR, Gil-Mohapel J
Int J Mol Sci 2021 Aug 4;22(16) doi: 10.3390/ijms22168363. PMID: 34445070Free PMC Article
Tater P, Pandey S
Neurol India 2021 Mar-Apr;69(2):272-283. doi: 10.4103/0028-3886.314574. PMID: 33904435

Recent clinical studies

Etiology

Ghosh R, Roy D, Dubey S, Das S, Benito-León J
Tremor Other Hyperkinet Mov (N Y) 2022;12:14. Epub 2022 May 4 doi: 10.5334/tohm.671. PMID: 35601204Free PMC Article
Teixeira AL, Vasconcelos LP, Nunes MDCP, Singer H
Expert Rev Neurother 2021 Aug;21(8):913-922. Epub 2021 Aug 18 doi: 10.1080/14737175.2021.1965883. PMID: 34353207
Cao L, Huang X, Wang N, Wu Z, Zhang C, Gu W, Cong S, Ma J, Wei L, Deng Y, Fang Q, Niu Q, Wang J, Wang Z, Yin Y, Tian J, Tian S, Bi H, Jiang H, Liu X, Lü Y, Sun M, Wu J, Xu E, Chen T, Chen T, Chen X, Li W, Li S, Li Q, Song X, Tang Y, Yang P, Yang Y, Zhang M, Zhang X, Zhang Y, Zhang R, Ouyang Y, Yu J, Hu Q, Ke Q, Yao Y, Zhao Z, Zhao X, Zhao G, Liang F, Cheng N, Han J, Peng R, Chen S, Tang B
Transl Neurodegener 2021 Feb 16;10(1):7. doi: 10.1186/s40035-021-00231-8. PMID: 33588936Free PMC Article
Brandsma R, van Egmond ME, Tijssen MAJ; Groningen Movement Disorder Expertise Centre
Dev Med Child Neurol 2021 Mar;63(3):252-258. Epub 2020 Nov 5 doi: 10.1111/dmcn.14721. PMID: 33150968Free PMC Article
Roos RA
Orphanet J Rare Dis 2010 Dec 20;5:40. doi: 10.1186/1750-1172-5-40. PMID: 21171977Free PMC Article

Diagnosis

Stoker TB, Mason SL, Greenland JC, Holden ST, Santini H, Barker RA
Pract Neurol 2022 Feb;22(1):32-41. Epub 2021 Aug 19 doi: 10.1136/practneurol-2021-003074. PMID: 34413240
Baizabal-Carvallo JF, Cardoso F
J Neural Transm (Vienna) 2020 Oct;127(10):1323-1342. Epub 2020 Aug 9 doi: 10.1007/s00702-020-02238-3. PMID: 32776155
Termsarasab P
Continuum (Minneap Minn) 2019 Aug;25(4):1001-1035. doi: 10.1212/CON.0000000000000763. PMID: 31356291
Wyant KJ, Ridder AJ, Dayalu P
Curr Neurol Neurosci Rep 2017 Apr;17(4):33. doi: 10.1007/s11910-017-0739-9. PMID: 28324302
Roos RA
Orphanet J Rare Dis 2010 Dec 20;5:40. doi: 10.1186/1750-1172-5-40. PMID: 21171977Free PMC Article

Therapy

Stoker TB, Mason SL, Greenland JC, Holden ST, Santini H, Barker RA
Pract Neurol 2022 Feb;22(1):32-41. Epub 2021 Aug 19 doi: 10.1136/practneurol-2021-003074. PMID: 34413240
Kim A, Lalonde K, Truesdell A, Gomes Welter P, Brocardo PS, Rosenstock TR, Gil-Mohapel J
Int J Mol Sci 2021 Aug 4;22(16) doi: 10.3390/ijms22168363. PMID: 34445070Free PMC Article
Tabrizi SJ, Flower MD, Ross CA, Wild EJ
Nat Rev Neurol 2020 Oct;16(10):529-546. Epub 2020 Aug 14 doi: 10.1038/s41582-020-0389-4. PMID: 32796930
Baizabal-Carvallo JF, Cardoso F
J Neural Transm (Vienna) 2020 Oct;127(10):1323-1342. Epub 2020 Aug 9 doi: 10.1007/s00702-020-02238-3. PMID: 32776155
Termsarasab P
Continuum (Minneap Minn) 2019 Aug;25(4):1001-1035. doi: 10.1212/CON.0000000000000763. PMID: 31356291

Prognosis

Stimming EF, Bega D
Continuum (Minneap Minn) 2022 Oct 1;28(5):1379-1408. doi: 10.1212/CON.0000000000001169. PMID: 36222771
Medina A, Mahjoub Y, Shaver L, Pringsheim T
Mov Disord 2022 Dec;37(12):2327-2335. Epub 2022 Sep 26 doi: 10.1002/mds.29228. PMID: 36161673Free PMC Article
Defebvre L, Krystkowiak P
Rev Neurol (Paris) 2016 Aug-Sep;172(8-9):483-487. Epub 2016 Jul 28 doi: 10.1016/j.neurol.2016.07.006. PMID: 27476417
Pringsheim T, Wiltshire K, Day L, Dykeman J, Steeves T, Jette N
Mov Disord 2012 Aug;27(9):1083-91. Epub 2012 Jun 12 doi: 10.1002/mds.25075. PMID: 22692795
Mov Disord 1996 Mar;11(2):136-42. doi: 10.1002/mds.870110204. PMID: 8684382

Clinical prediction guides

Furr Stimming E, Claassen DO, Kayson E, Goldstein J, Mehanna R, Zhang H, Liang GS, Haubenberger D; Huntington Study Group KINECT-HD Collaborators
Lancet Neurol 2023 Jun;22(6):494-504. doi: 10.1016/S1474-4422(23)00127-8. PMID: 37210099
Pérez-Dueñas B, Gorman K, Marcé-Grau A, Ortigoza-Escobar JD, Macaya A, Danti FR, Barwick K, Papandreou A, Ng J, Meyer E, Mohammad SS, Smith M, Muntoni F, Munot P, Uusimaa J, Vieira P, Sheridan E, Guerrini R, Cobben J, Yilmaz S, De Grandis E, Dale RC, Pons R, Peall KJ, Leuzzi V, Kurian MA
Mov Disord 2022 Nov;37(11):2197-2209. Epub 2022 Aug 25 doi: 10.1002/mds.29182. PMID: 36054588Free PMC Article
Bologna M, Valls-Solè J, Kamble N, Pal PK, Conte A, Guerra A, Belvisi D, Berardelli A
Clin Neurophysiol 2022 Aug;140:110-125. Epub 2022 Jun 8 doi: 10.1016/j.clinph.2022.05.014. PMID: 35785630
Roos RA
Orphanet J Rare Dis 2010 Dec 20;5:40. doi: 10.1186/1750-1172-5-40. PMID: 21171977Free PMC Article
Mov Disord 1996 Mar;11(2):136-42. doi: 10.1002/mds.870110204. PMID: 8684382

Recent systematic reviews

Medina A, Mahjoub Y, Shaver L, Pringsheim T
Mov Disord 2022 Dec;37(12):2327-2335. Epub 2022 Sep 26 doi: 10.1002/mds.29228. PMID: 36161673Free PMC Article
Bilbao A, Spanagel R
BMC Med 2022 Aug 19;20(1):259. doi: 10.1186/s12916-022-02459-1. PMID: 35982439Free PMC Article
Quinn L, Kegelmeyer D, Kloos A, Rao AK, Busse M, Fritz NE
Neurology 2020 Feb 4;94(5):217-228. Epub 2020 Jan 6 doi: 10.1212/WNL.0000000000008887. PMID: 31907286Free PMC Article
Fritz NE, Rao AK, Kegelmeyer D, Kloos A, Busse M, Hartel L, Carrier J, Quinn L
J Huntingtons Dis 2017;6(3):217-235. doi: 10.3233/JHD-170260. PMID: 28968244Free PMC Article
Pringsheim T, Wiltshire K, Day L, Dykeman J, Steeves T, Jette N
Mov Disord 2012 Aug;27(9):1083-91. Epub 2012 Jun 12 doi: 10.1002/mds.25075. PMID: 22692795

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