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3-phosphoglycerate dehydrogenase deficiency

MedGen UID:
663158
Concept ID:
C0580190
Disease or Syndrome
Synonym: 3-Phosphoglycerate dehydrogenase deficiency
SNOMED CT: 3-Phosphoglycerate dehydrogenase deficiency (303098002)
 
Monarch Initiative: MONDO:0018491

Professional guidelines

PubMed

de Koning TJ
J Inherit Metab Dis 2006 Apr-Jun;29(2-3):347-51. doi: 10.1007/s10545-006-0269-0. PMID: 16763900

Recent clinical studies

Etiology

Coşkun T, Aydin HI, Kiliç M, Dursun A, Haliloğlu G, Topaloğlu H, Karli-Oğuz K, de Koning TJ
Turk J Pediatr 2009 Nov-Dec;51(6):587-92. PMID: 20196394
Tohyama J, Akasaka N, Osaka H, Maegaki Y, Kato M, Saito N, Yamashita S, Ohno K
Brain Dev 2008 May;30(5):349-55. Epub 2007 Dec 11 doi: 10.1016/j.braindev.2007.10.006. PMID: 18065176
de Koning TJ, Poll-The BT, Jaeken J
Neuropediatrics 1999 Feb;30(1):1-4. doi: 10.1055/s-2007-973447. PMID: 10222452

Diagnosis

Kraoua I, Wiame E, Kraoua L, Nasrallah F, Benrhouma H, Rouissi A, Turki I, Chaabouni H, Briand G, Kaabachi N, Van Schaftingen E, Gouider-Khouja N
Neuropediatrics 2013 Oct;44(5):281-5. Epub 2013 Apr 6 doi: 10.1055/s-0033-1338133. PMID: 23564319
Tabatabaie L, Klomp LW, Rubio-Gozalbo ME, Spaapen LJ, Haagen AA, Dorland L, de Koning TJ
J Inherit Metab Dis 2011 Feb;34(1):181-4. Epub 2010 Nov 27 doi: 10.1007/s10545-010-9249-5. PMID: 21113737Free PMC Article
Coşkun T, Aydin HI, Kiliç M, Dursun A, Haliloğlu G, Topaloğlu H, Karli-Oğuz K, de Koning TJ
Turk J Pediatr 2009 Nov-Dec;51(6):587-92. PMID: 20196394
Ramaekers VT, Blau N
Dev Med Child Neurol 2004 Dec;46(12):843-51. doi: 10.1017/s0012162204001471. PMID: 15581159
de Koning TJ, Poll-The BT, Jaeken J
Neuropediatrics 1999 Feb;30(1):1-4. doi: 10.1055/s-2007-973447. PMID: 10222452

Therapy

Coşkun T, Aydin HI, Kiliç M, Dursun A, Haliloğlu G, Topaloğlu H, Karli-Oğuz K, de Koning TJ
Turk J Pediatr 2009 Nov-Dec;51(6):587-92. PMID: 20196394
de Koning TJ
J Inherit Metab Dis 2006 Apr-Jun;29(2-3):347-51. doi: 10.1007/s10545-006-0269-0. PMID: 16763900
De Koning TJ, Duran M, Van Maldergem L, Pineda M, Dorland L, Gooskens R, Jaeken J, Poll-The BT
J Inherit Metab Dis 2002 May;25(2):119-25. doi: 10.1023/a:1015624726822. PMID: 12118526
Pineda M, Vilaseca MA, Artuch R, Santos S, García González MM, Aracil A, Van Schaftingen E, Jaeken J
Dev Med Child Neurol 2000 Sep;42(9):629-33. doi: 10.1017/s0012162200001171. PMID: 11034457
de Koning TJ, Poll-The BT, Jaeken J
Neuropediatrics 1999 Feb;30(1):1-4. doi: 10.1055/s-2007-973447. PMID: 10222452

Prognosis

Coşkun T, Aydin HI, Kiliç M, Dursun A, Haliloğlu G, Topaloğlu H, Karli-Oğuz K, de Koning TJ
Turk J Pediatr 2009 Nov-Dec;51(6):587-92. PMID: 20196394
Klomp LW, de Koning TJ, Malingré HE, van Beurden EA, Brink M, Opdam FL, Duran M, Jaeken J, Pineda M, Van Maldergem L, Poll-The BT, van den Berg IE, Berger R
Am J Hum Genet 2000 Dec;67(6):1389-99. Epub 2000 Oct 27 doi: 10.1086/316886. PMID: 11055895Free PMC Article

Clinical prediction guides

Tabatabaie L, Klomp LW, Rubio-Gozalbo ME, Spaapen LJ, Haagen AA, Dorland L, de Koning TJ
J Inherit Metab Dis 2011 Feb;34(1):181-4. Epub 2010 Nov 27 doi: 10.1007/s10545-010-9249-5. PMID: 21113737Free PMC Article
Fuchs SA, Dorland L, de Sain-van der Velden MG, Hendriks M, Klomp LW, Berger R, de Koning TJ
Ann Neurol 2006 Oct;60(4):476-80. doi: 10.1002/ana.20977. PMID: 17068790
Ramaekers VT, Blau N
Dev Med Child Neurol 2004 Dec;46(12):843-51. doi: 10.1017/s0012162204001471. PMID: 15581159
De Koning TJ, Duran M, Van Maldergem L, Pineda M, Dorland L, Gooskens R, Jaeken J, Poll-The BT
J Inherit Metab Dis 2002 May;25(2):119-25. doi: 10.1023/a:1015624726822. PMID: 12118526
Klomp LW, de Koning TJ, Malingré HE, van Beurden EA, Brink M, Opdam FL, Duran M, Jaeken J, Pineda M, Van Maldergem L, Poll-The BT, van den Berg IE, Berger R
Am J Hum Genet 2000 Dec;67(6):1389-99. Epub 2000 Oct 27 doi: 10.1086/316886. PMID: 11055895Free PMC Article

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