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Juvenile pilocytic astrocytoma

MedGen UID:
128890
Concept ID:
C0280783
Neoplastic Process
Synonyms: Astrocytoma, Juvenile Pilocytic; Juvenile Pilocytic Astrocytoma; Juvenile Pilocytic Astrocytomas; Pilocytic Astrocytoma, Juvenile
 
Monarch Initiative: MONDO:0003999

Definition

A pilocytic astrocytoma that occurs during adolescence. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVJuvenile pilocytic astrocytoma

Professional guidelines

PubMed

Shams I, Manoranjan B, Voth R, Ragulojan M, Ajani O, Yarascavitch B, Singh SK, Fleming AJ
J Neurosurg Sci 2023 Jun;67(3):311-316. Epub 2021 Apr 16 doi: 10.23736/S0390-5616.21.05169-9. PMID: 33870664
Allen JC
Pediatr Neurosurg 2000 Mar;32(3):154-62. doi: 10.1159/000028922. PMID: 10867564
Mamelak AN, Prados MD, Obana WG, Cogen PH, Edwards MS
J Neurosurg 1994 Jul;81(1):24-30. doi: 10.3171/jns.1994.81.1.0024. PMID: 8207524

Recent clinical studies

Etiology

Shams I, Manoranjan B, Voth R, Ragulojan M, Ajani O, Yarascavitch B, Singh SK, Fleming AJ
J Neurosurg Sci 2023 Jun;67(3):311-316. Epub 2021 Apr 16 doi: 10.23736/S0390-5616.21.05169-9. PMID: 33870664
Maharaj A, Manoranjan B, Verhey LH, Fleming AJ, Farrokhyar F, Almenawer S, Singh SK, Yarascavitch B
J Clin Neurosci 2019 Dec;70:79-84. Epub 2019 Aug 26 doi: 10.1016/j.jocn.2019.08.066. PMID: 31466905
Bookland M, Tang-Schomer M, Gillan E, Kolmakova A
Acta Neurochir (Wien) 2018 Aug;160(8):1571-1581. Epub 2018 Jun 18 doi: 10.1007/s00701-018-3589-6. PMID: 29911246
Mazloom A, Hodges JC, Teh BS, Chintagumpala M, Paulino AC
Int J Radiat Oncol Biol Phys 2012 Oct 1;84(2):350-4. Epub 2012 Mar 6 doi: 10.1016/j.ijrobp.2011.12.044. PMID: 22401918
Mamelak AN, Prados MD, Obana WG, Cogen PH, Edwards MS
J Neurosurg 1994 Jul;81(1):24-30. doi: 10.3171/jns.1994.81.1.0024. PMID: 8207524

Diagnosis

Lu VM, Niazi TN
Pediatr Rev 2021 Sep;42(9):486-499. doi: 10.1542/pir.2020-000661. PMID: 34470868
Bookland M, Tang-Schomer M, Gillan E, Kolmakova A
Acta Neurochir (Wien) 2018 Aug;160(8):1571-1581. Epub 2018 Jun 18 doi: 10.1007/s00701-018-3589-6. PMID: 29911246
Mazloom A, Hodges JC, Teh BS, Chintagumpala M, Paulino AC
Int J Radiat Oncol Biol Phys 2012 Oct 1;84(2):350-4. Epub 2012 Mar 6 doi: 10.1016/j.ijrobp.2011.12.044. PMID: 22401918
Bernaerts A, Vanhoenacker F, Debois V, Parizel PM
JBR-BTR 2003 May-Jun;86(3):142-3. PMID: 12880155
Mamelak AN, Prados MD, Obana WG, Cogen PH, Edwards MS
J Neurosurg 1994 Jul;81(1):24-30. doi: 10.3171/jns.1994.81.1.0024. PMID: 8207524

Therapy

Rubio RR, Chae R, Khare A, Dubnicoff T, Winkler E, Sloan E, Bollen AW, Berger MS, Abla AA
World Neurosurg 2019 Dec;132:57. Epub 2019 Aug 31 doi: 10.1016/j.wneu.2019.08.172. PMID: 31479784
Maharaj A, Manoranjan B, Verhey LH, Fleming AJ, Farrokhyar F, Almenawer S, Singh SK, Yarascavitch B
J Clin Neurosci 2019 Dec;70:79-84. Epub 2019 Aug 26 doi: 10.1016/j.jocn.2019.08.066. PMID: 31466905
Naftel RP, Pollack IF, Zuccoli G, Deutsch M, Jakacki RI
Pediatr Blood Cancer 2015 Jan;62(1):35-9. Epub 2014 Sep 11 doi: 10.1002/pbc.25179. PMID: 25213668
Aryan HE, Meltzer HS, Lu DC, Ozgur BM, Levy ML, Bruce DA
Childs Nerv Syst 2005 Jun;21(6):477-81. Epub 2004 Sep 15 doi: 10.1007/s00381-004-1002-7. PMID: 15378329
Mamelak AN, Prados MD, Obana WG, Cogen PH, Edwards MS
J Neurosurg 1994 Jul;81(1):24-30. doi: 10.3171/jns.1994.81.1.0024. PMID: 8207524

Prognosis

Shams I, Manoranjan B, Voth R, Ragulojan M, Ajani O, Yarascavitch B, Singh SK, Fleming AJ
J Neurosurg Sci 2023 Jun;67(3):311-316. Epub 2021 Apr 16 doi: 10.23736/S0390-5616.21.05169-9. PMID: 33870664
Lu VM, Niazi TN
Pediatr Rev 2021 Sep;42(9):486-499. doi: 10.1542/pir.2020-000661. PMID: 34470868
Maharaj A, Manoranjan B, Verhey LH, Fleming AJ, Farrokhyar F, Almenawer S, Singh SK, Yarascavitch B
J Clin Neurosci 2019 Dec;70:79-84. Epub 2019 Aug 26 doi: 10.1016/j.jocn.2019.08.066. PMID: 31466905
Bookland M, Tang-Schomer M, Gillan E, Kolmakova A
Acta Neurochir (Wien) 2018 Aug;160(8):1571-1581. Epub 2018 Jun 18 doi: 10.1007/s00701-018-3589-6. PMID: 29911246
Garcia DM, Fulling KH
J Neurosurg 1985 Sep;63(3):382-6. doi: 10.3171/jns.1985.63.3.0382. PMID: 4020465

Clinical prediction guides

Maharaj A, Manoranjan B, Verhey LH, Fleming AJ, Farrokhyar F, Almenawer S, Singh SK, Yarascavitch B
J Clin Neurosci 2019 Dec;70:79-84. Epub 2019 Aug 26 doi: 10.1016/j.jocn.2019.08.066. PMID: 31466905
Bookland M, Tang-Schomer M, Gillan E, Kolmakova A
Acta Neurochir (Wien) 2018 Aug;160(8):1571-1581. Epub 2018 Jun 18 doi: 10.1007/s00701-018-3589-6. PMID: 29911246
Pricola Fehnel K, Duggins-Warf M, Zurakowski D, McKee-Proctor M, Majumder R, Raber M, Han X, Smith ER
J Neurosurg Pediatr 2016 Oct;18(4):396-407. Epub 2016 Jun 17 doi: 10.3171/2015.12.PEDS15448. PMID: 27314542
Kestle J, Townsend JJ, Brockmeyer DL, Walker ML
J Neurosurg 2004 Aug;101(1 Suppl):1-6. doi: 10.3171/ped.2004.101.2.0001. PMID: 16206964
Lee YY, Van Tassel P, Bruner JM, Moser RP, Share JC
AJR Am J Roentgenol 1989 Jun;152(6):1263-70. doi: 10.2214/ajr.152.6.1263. PMID: 2718863

Recent systematic reviews

Vazquez S, Zuckerman DA, Gandhi C, Al-Mufti F, Muh C, Santarelli J, Pisapia JM
Pediatr Neurosurg 2024;59(1):44-53. Epub 2023 Oct 30 doi: 10.1159/000534895. PMID: 37903471

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