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Syringobulbia

MedGen UID:
124368
•Concept ID:
C0270771
•
Congenital Abnormality
SNOMED CT: Syringobulbia (26594006)

Professional guidelines

PubMed

Anesthetic and Obstetric Management of Syringomyelia During Labor and Delivery: A Case Series and Systematic Review.
Garvey GP, Wasade VS, Murphy KE, Balki M
Anesth Analg 2017 Sep;125(3):913-924. doi: 10.1213/ANE.0000000000001987. PMID: 28598915
Diagnosis and treatment of intramedullary hemangioblastoma of cervical spinal cord.
Xu Q, Bao W, Pang L
Chin Med J (Engl) 2002 Jul;115(7):1010-3. PMID: 12150732
Basilar invagination in osteogenesis imperfecta and related osteochondrodysplasias: medical and surgical management.
Sawin PD, Menezes AH
J Neurosurg 1997 Jun;86(6):950-60. doi: 10.3171/jns.1997.86.6.0950. PMID: 9171173

Recent clinical studies

Etiology

Trapped fourth ventricle phenomenon following aneurysm rupture of the posterior circulation: case reports.
Ferreira M, Nahed BV, Babu MA, Walcott BP, Ellenbogen RG, Sekhar LN
Neurosurgery 2012 Jan;70(1):E253-8; discussion E258. doi: 10.1227/NEU.0b013e31822abf95. PMID: 21795864
Respiratory sinus arrhythmia of brainstem lesions.
DiMario FJ, Bauer L, Baxter D
J Child Neurol 1999 Apr;14(4):229-32. doi: 10.1177/088307389901400403. PMID: 10334396
The surgical treatment of Chiari I malformation.
Klekamp J, Batzdorf U, Samii M, Bothe HW
Acta Neurochir (Wien) 1996;138(7):788-801. doi: 10.1007/BF01411256. PMID: 8869706
Syringobulbia: a surgical appraisal.
Morgan D, Williams B
J Neurol Neurosurg Psychiatry 1992 Dec;55(12):1132-41. doi: 10.1136/jnnp.55.12.1132. PMID: 1479391Free PMC Article
Cardiovascular reflexes in syringomyelia.
Nogués MA, Newman PK, Male VJ, Foster JB
Brain 1982 Dec;105 (Pt 4):835-49. doi: 10.1093/brain/105.4.835. PMID: 7139257

Diagnosis

Central pain in the face and head.
Boivie J
Handb Clin Neurol 2010;97:693-701. doi: 10.1016/S0072-9752(10)97058-9. PMID: 20816464
Periodic limb movements in syringomyelia and syringobulbia.
Nogués M, Cammarota A, Leiguarda R, Rivero A, Pardal A, Encabo H
Mov Disord 2000 Jan;15(1):113-9. doi: 10.1002/1531-8257(200001)15:1<113::aid-mds1017>3.0.co;2-y. PMID: 10634249
Surgical treatment of syringobulbia.
Williams B
Neurosurg Clin N Am 1993 Jul;4(3):553-71. PMID: 8353453
Facial myokymia in syringobulbia.
Riaz G, Campbell WW, Carr J, Ghatak N
Arch Neurol 1990 Apr;47(4):472-4. doi: 10.1001/archneur.1990.00530040130030. PMID: 2181981
Familial syringomyelia.
Busis NA, Hochberg FH
J Neurol Neurosurg Psychiatry 1985 Sep;48(9):936-8. doi: 10.1136/jnnp.48.9.936. PMID: 4045487Free PMC Article

Therapy

Chronological Progression and Management of Syringobulbia Caused by Spinal Hemangioblastoma: A Case Series and Review of the Literature.
Tsuchiya T, Takami H, Yoshimoto S, Nambu S, Takayanagi S, Tanaka S, Saito N
World Neurosurg 2022 Nov;167:e127-e136. Epub 2022 Aug 6 doi: 10.1016/j.wneu.2022.07.118. PMID: 35944861
Trapped fourth ventricle phenomenon following aneurysm rupture of the posterior circulation: case reports.
Ferreira M, Nahed BV, Babu MA, Walcott BP, Ellenbogen RG, Sekhar LN
Neurosurgery 2012 Jan;70(1):E253-8; discussion E258. doi: 10.1227/NEU.0b013e31822abf95. PMID: 21795864
Central pain in the face and head.
Boivie J
Handb Clin Neurol 2010;97:693-701. doi: 10.1016/S0072-9752(10)97058-9. PMID: 20816464
Postural tachycardia syndrome in syringomyelia: response to fludrocortisone and beta-blockers.
Nogués M, Delorme R, Saadia D, Heidel K, Benarroch E
Clin Auton Res 2001 Aug;11(4):265-7. doi: 10.1007/BF02298959. PMID: 11710800
Respiratory sinus arrhythmia of brainstem lesions.
DiMario FJ, Bauer L, Baxter D
J Child Neurol 1999 Apr;14(4):229-32. doi: 10.1177/088307389901400403. PMID: 10334396

Prognosis

Syringobulbia: a surgical appraisal.
Morgan D, Williams B
J Neurol Neurosurg Psychiatry 1992 Dec;55(12):1132-41. doi: 10.1136/jnnp.55.12.1132. PMID: 1479391Free PMC Article
Surgical management of torticollis.
Maxwell RE
Postgrad Med 1984 May 15;75(7):147-52, 154-5. doi: 10.1080/00325481.1984.11698625. PMID: 6718289
Terminal ventriculostomy for syringomyelia.
Gardner WJ, Bell HS, Poolos PN, Dohn DF, Steinberg M
J Neurosurg 1977 May;46(5):609-17. doi: 10.3171/jns.1977.46.5.0609. PMID: 845650
Syringobulbia--prolonged survival.
Ratcheson RA, Wirth FP Jr, Li CL, Van Buren JM
Acta Neurochir (Wien) 1971;24(3):169-77. doi: 10.1007/BF01400553. PMID: 5123103
SYRINGOBULBIA. CASE REPORT WITH 19-YEAR FOLLOW-UP.
MORELLI RJ, KEMPE L
J Neurosurg 1964 Mar;21:230-2. doi: 10.3171/jns.1964.21.3.0230. PMID: 14127627

Clinical prediction guides

Louis Duménil (1823-1890), surgeon and pioneer in neurology.
Walusinski O
Rev Neurol (Paris) 2022 Apr;178(4):298-305. Epub 2021 Sep 23 doi: 10.1016/j.neurol.2021.06.011. PMID: 34565621
Neuro-ophthalmologic complications of syringobulbia.
Nogués M, López L, Meli F
Curr Neurol Neurosci Rep 2010 Nov;10(6):459-66. doi: 10.1007/s11910-010-0139-x. PMID: 20711820
Acute spinal cord swelling in a child with Chiari II malformation.
Galarza M, Gravori T, Lazareff JA
Pediatr Neurosurg 2001 Sep;35(3):145-8. doi: 10.1159/000050409. PMID: 11641624
Cardiovascular reflexes in syringomyelia.
Nogués MA, Newman PK, Male VJ, Foster JB
Brain 1982 Dec;105 (Pt 4):835-49. doi: 10.1093/brain/105.4.835. PMID: 7139257
Infantile hypoventilation syndrome, neurenteric cyst, and syringobulbia.
Chung HD, DeMello DE, D'Souza N, Estrada J
Neurology 1982 Apr;32(4):441-4. doi: 10.1212/wnl.32.4.441. PMID: 7038532

Recent systematic reviews

Syringobulbia in Patients with Chiari Malformation Type I: A Systematic Review.
Shen J, Shen J, Huang K, Wu Y, Pan J, Zhan R
Biomed Res Int 2019;2019:4829102. Epub 2019 Mar 19 doi: 10.1155/2019/4829102. PMID: 31016190Free PMC Article
Anesthetic and Obstetric Management of Syringomyelia During Labor and Delivery: A Case Series and Systematic Review.
Garvey GP, Wasade VS, Murphy KE, Balki M
Anesth Analg 2017 Sep;125(3):913-924. doi: 10.1213/ANE.0000000000001987. PMID: 28598915

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