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Streak gonad

MedGen UID:
452347
Concept ID:
C0266360
Congenital Abnormality
Synonym: Streak gonads
SNOMED CT: Streak gonad (84814009)

Professional guidelines

PubMed

de la Calle CM, Kim S, Baskin LS
J Pediatr Surg 2020 Nov;55(11):2480-2491. Epub 2020 Feb 19 doi: 10.1016/j.jpedsurg.2020.02.014. PMID: 32164982
Farrugia MK, Sebire NJ, Achermann JC, Eisawi A, Duffy PG, Mushtaq I
J Pediatr Urol 2013 Apr;9(2):139-44. Epub 2012 Jan 26 doi: 10.1016/j.jpurol.2011.12.012. PMID: 22281282Free PMC Article
Capito C, Leclair MD, Arnaud A, David A, Baron S, Corradini N, Héloury Y
J Pediatr Urol 2011 Feb;7(1):72-5. Epub 2010 Feb 11 doi: 10.1016/j.jpurol.2010.01.010. PMID: 20153258

Recent clinical studies

Etiology

Kilic C, Cakir C, Yuksel D, Kilic F, Kayikcioglu F, Koc S, Korkmaz V, Kimyon Comert G, Turkmen O, Boran N, Turan T
J Adolesc Young Adult Oncol 2021 Jun;10(3):303-308. Epub 2020 Aug 5 doi: 10.1089/jayao.2020.0087. PMID: 32762565
Matsumoto F, Matsuyama S, Matsui F, Yazawa K, Matsuoka K
Urology 2020 Mar;137:157-160. Epub 2019 Dec 27 doi: 10.1016/j.urology.2019.12.014. PMID: 31883875
Roth LM, Cheng L
Hum Pathol 2020 Jun;100:47-53. Epub 2019 Dec 2 doi: 10.1016/j.humpath.2019.11.005. PMID: 31805291
Lepais L, Morel Y, Mouriquand P, Gorduza D, Plotton I, Collardeau-Frachon S, Dijoud F
Mod Pathol 2016 Nov;29(11):1399-1414. Epub 2016 Jul 29 doi: 10.1038/modpathol.2016.123. PMID: 27469328
Bösze P, László J
Obstet Gynecol 1979 Nov;54(5):544-8. PMID: 503377

Diagnosis

Kilic C, Cakir C, Yuksel D, Kilic F, Kayikcioglu F, Koc S, Korkmaz V, Kimyon Comert G, Turkmen O, Boran N, Turan T
J Adolesc Young Adult Oncol 2021 Jun;10(3):303-308. Epub 2020 Aug 5 doi: 10.1089/jayao.2020.0087. PMID: 32762565
Chavhan GB, Parra DA, Oudjhane K, Miller SF, Babyn PS, Pippi Salle FL
Radiographics 2008 Nov-Dec;28(7):1891-904. doi: 10.1148/rg.287085034. PMID: 19001646
Brosman SA
J Urol 1979 Mar;121(3):344-7. doi: 10.1016/s0022-5347(17)56781-6. PMID: 430632
van Niekerk WA
Am J Obstet Gynecol 1978 Apr 15;130(8):862-75. doi: 10.1016/0002-9378(78)90263-6. PMID: 345819
Zäh W, Kalderon AE, Tucci JR
Acta Endocrinol Suppl (Copenh) 1975;197:1-39. PMID: 1094776

Therapy

Faure-Conter C, Orbach D, Fresneau B, Verité C, Bonneau J, Thebaud E, Poirée M, Thouvenin S, Pluchart C, Mure PY, Dijoud F, Morel Y
Pediatr Blood Cancer 2020 Apr;67(4):e28169. Epub 2020 Feb 4 doi: 10.1002/pbc.28169. PMID: 32020769
Matsumoto F, Matsuyama S, Matsui F, Yazawa K, Matsuoka K
Urology 2020 Mar;137:157-160. Epub 2019 Dec 27 doi: 10.1016/j.urology.2019.12.014. PMID: 31883875
Huang YC, Lee CT, Wu MZ, Liu SY, Tung YC, Ho HN, Tsai WY
J Formos Med Assoc 2019 Jan;118(1 Pt 3):450-456. Epub 2018 Jul 14 doi: 10.1016/j.jfma.2018.07.003. PMID: 30017534
Muroya K, Okuyama T, Goishi K, Ogiso Y, Fukuda S, Kameyama J, Sato H, Suzuki Y, Terasaki H, Gomyo H, Wakui K, Fukushima Y, Ogata T
J Clin Endocrinol Metab 2000 Sep;85(9):3094-100. doi: 10.1210/jcem.85.9.6771. PMID: 10999792
Bösze P, Bognár B, Szilvási I, Bohar, Tusnády G, Rejtö L, László J
Gynecol Obstet Invest 1988;26(1):44-51. doi: 10.1159/000293671. PMID: 3169629

Prognosis

Matsumoto F, Matsuyama S, Matsui F, Yazawa K, Matsuoka K
Urology 2020 Mar;137:157-160. Epub 2019 Dec 27 doi: 10.1016/j.urology.2019.12.014. PMID: 31883875
Şimşek E, Binay Ç, Demiral M, Tokar B, Kabukçuoğlu S, Üstün M
J Clin Res Pediatr Endocrinol 2016 Sep 1;8(3):351-5. Epub 2016 Apr 18 doi: 10.4274/jcrpe.2705. PMID: 27087521Free PMC Article
Chemes HE, Venara M, Del Rey G, Arcari AJ, Musse MP, Papazian R, Forclaz V, Gottlieb S
Andrology 2015 Jan;3(1):59-69. Epub 2015 Jan 19 doi: 10.1111/andr.301. PMID: 25598272
Andrade JG, Guerra-Júnior G, Maciel-Guerra AT
Arq Bras Endocrinol Metabol 2010 Mar;54(3):331-4. doi: 10.1590/s0004-27302010000300013. PMID: 20520965
Iliev DI, Ranke MB, Wollmann HA
Horm Res 2002;58(1):30-3. doi: 10.1159/000063213. PMID: 12169778

Clinical prediction guides

Matsumoto F, Matsuyama S, Matsui F, Yazawa K, Matsuoka K
Urology 2020 Mar;137:157-160. Epub 2019 Dec 27 doi: 10.1016/j.urology.2019.12.014. PMID: 31883875
Huang YC, Lee CT, Wu MZ, Liu SY, Tung YC, Ho HN, Tsai WY
J Formos Med Assoc 2019 Jan;118(1 Pt 3):450-456. Epub 2018 Jul 14 doi: 10.1016/j.jfma.2018.07.003. PMID: 30017534
Şimşek E, Binay Ç, Demiral M, Tokar B, Kabukçuoğlu S, Üstün M
J Clin Res Pediatr Endocrinol 2016 Sep 1;8(3):351-5. Epub 2016 Apr 18 doi: 10.4274/jcrpe.2705. PMID: 27087521Free PMC Article
Serra A, Denzer F, Hiort O, Barth TF, Henne-Bruns D, Barbi G, Rettenberger G, Wabitsch M, Just W, Leriche C
Sex Dev 2015;9(3):136-43. Epub 2015 Jun 3 doi: 10.1159/000430897. PMID: 26043854
Jirásek JE
Birth Defects Orig Artic Ser 1971 May;7(6):159-65. PMID: 5173158

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