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Disorder of pulmonary circulation

MedGen UID:
511735
•Concept ID:
C0178272
•
Disease or Syndrome
SNOMED CT: Disorder of pulmonary circulation (39785005)

Professional guidelines

PubMed

2023 ACC/AHA/ACCP/HRS Guideline for the Diagnosis and Management of Atrial Fibrillation: A Report of the American College of Cardiology/American Heart Association Joint Committee on Clinical Practice Guidelines.
Joglar JA, Chung MK, Armbruster AL, Benjamin EJ, Chyou JY, Cronin EM, Deswal A, Eckhardt LL, Goldberger ZD, Gopinathannair R, Gorenek B, Hess PL, Hlatky M, Hogan G, Ibeh C, Indik JH, Kido K, Kusumoto F, Link MS, Linta KT, Marcus GM, McCarthy PM, Patel N, Patton KK, Perez MV, Piccini JP, Russo AM, Sanders P, Streur MM, Thomas KL, Times S, Tisdale JE, Valente AM, Van Wagoner DR; Peer Review Committee Members
Circulation 2024 Jan 2;149(1):e1-e156. Epub 2023 Nov 30 doi: 10.1161/CIR.0000000000001193. PMID: 38033089Free PMC Article
Pathophysiology and Management of Persistent Pulmonary Hypertension of the Newborn.
Singh Y, Lakshminrusimha S
Clin Perinatol 2021 Aug;48(3):595-618. doi: 10.1016/j.clp.2021.05.009. PMID: 34353582Free PMC Article
Prevalence, risk factors, and management of asthma in China: a national cross-sectional study.
Huang K, Yang T, Xu J, Yang L, Zhao J, Zhang X, Bai C, Kang J, Ran P, Shen H, Wen F, Chen Y, Sun T, Shan G, Lin Y, Xu G, Wu S, Wang C, Wang R, Shi Z, Xu Y, Ye X, Song Y, Wang Q, Zhou Y, Li W, Ding L, Wan C, Yao W, Guo Y, Xiao F, Lu Y, Peng X, Zhang B, Xiao D, Wang Z, Chen Z, Bu X, Zhang H, Zhang X, An L, Zhang S, Zhu J, Cao Z, Zhan Q, Yang Y, Liang L, Tong X, Dai H, Cao B, Wu T, Chung KF, He J, Wang C; China Pulmonary Health (CPH) Study Group
Lancet 2019 Aug 3;394(10196):407-418. Epub 2019 Jun 20 doi: 10.1016/S0140-6736(19)31147-X. PMID: 31230828

Recent clinical studies

Etiology

Exercise Stress Echocardiography of the Right Ventricle and Pulmonary Circulation.
Gargani L, Pugliese NR, De Biase N, Mazzola M, Agoston G, Arcopinto M, Argiento P, Armstrong WF, Bandera F, Cademartiri F, Carbone A, Castaldo R, Citro R, Cocchia R, Codullo V, D'Alto M, D'Andrea A, Douschan P, Fabiani I, Ferrara F, Franzese M, Frumento P, Ghio S, Grünig E, Guazzi M, Kasprzak JD, Kolias T, Kovacs G, La Gerche A, Limogelli G, Marra AM, Matucci-Cerinic M, Mauro C, Moreo A, Pratali L, Ranieri B, Rega S, Rudski L, Saggar R, Salzano A, Serra W, Stanziola AA, Vannan MA, Voilliot D, Vriz O, Wierzbowska-Drabik K, Cittadini A, Naeije R, Bossone E; RIGHT Heart International NETwork (RIGHT-NET) Investigators
J Am Coll Cardiol 2023 Nov 21;82(21):1973-1985. doi: 10.1016/j.jacc.2023.09.807. PMID: 37968015
Balloon pulmonary angioplasty for chronic thromboembolic pulmonary hypertension: a clinical consensus statement of the ESC working group on pulmonary circulation and right ventricular function.
Lang IM, Andreassen AK, Andersen A, Bouvaist H, Coghlan G, Escribano-Subias P, Jansa P, Kopec G, Kurzyna M, Matsubara H, Meyer BC, Palazzini M, Post MC, Pruszczyk P, Räber L, Roik M, Rosenkranz S, Wiedenroth CB, Redlin-Werle C, Brenot P
Eur Heart J 2023 Aug 1;44(29):2659-2671. doi: 10.1093/eurheartj/ehad413. PMID: 37470202Free PMC Article
Percutaneous treatment options for acute pulmonary embolism: a clinical consensus statement by the ESC Working Group on Pulmonary Circulation and Right Ventricular Function and the European Association of Percutaneous Cardiovascular Interventions.
Pruszczyk P, Klok FA, Kucher N, Roik M, Meneveau N, Sharp ASP, Nielsen-Kudsk JE, Obradović S, Barco S, Giannini F, Stefanini G, Tarantini G, Konstantinides S, Dudek D
EuroIntervention 2022 Oct 7;18(8):e623-e638. doi: 10.4244/EIJ-D-22-00246. PMID: 36112184Free PMC Article
The Relationship Between the Right Ventricle and its Load in Pulmonary Hypertension.
Vonk Noordegraaf A, Westerhof BE, Westerhof N
J Am Coll Cardiol 2017 Jan 17;69(2):236-243. doi: 10.1016/j.jacc.2016.10.047. PMID: 28081831
Contemporary management of acute right ventricular failure: a statement from the Heart Failure Association and the Working Group on Pulmonary Circulation and Right Ventricular Function of the European Society of Cardiology.
Harjola VP, Mebazaa A, Čelutkienė J, Bettex D, Bueno H, Chioncel O, Crespo-Leiro MG, Falk V, Filippatos G, Gibbs S, Leite-Moreira A, Lassus J, Masip J, Mueller C, Mullens W, Naeije R, Nordegraaf AV, Parissis J, Riley JP, Ristic A, Rosano G, Rudiger A, Ruschitzka F, Seferovic P, Sztrymf B, Vieillard-Baron A, Yilmaz MB, Konstantinides S
Eur J Heart Fail 2016 Mar;18(3):226-41. doi: 10.1002/ejhf.478. PMID: 26995592

Diagnosis

Dual-energy CT in pulmonary vascular disease.
Vlahos I, Jacobsen MC, Godoy MC, Stefanidis K, Layman RR
Br J Radiol 2022 Jan 1;95(1129):20210699. Epub 2021 Sep 24 doi: 10.1259/bjr.20210699. PMID: 34538091Free PMC Article
Pathophysiology of the right ventricle and of the pulmonary circulation in pulmonary hypertension: an update.
Vonk Noordegraaf A, Chin KM, Haddad F, Hassoun PM, Hemnes AR, Hopkins SR, Kawut SM, Langleben D, Lumens J, Naeije R
Eur Respir J 2019 Jan;53(1) Epub 2019 Jan 24 doi: 10.1183/13993003.01900-2018. PMID: 30545976Free PMC Article
Hypoxic Pulmonary Vasoconstriction: From Molecular Mechanisms to Medicine.
Dunham-Snary KJ, Wu D, Sykes EA, Thakrar A, Parlow LRG, Mewburn JD, Parlow JL, Archer SL
Chest 2017 Jan;151(1):181-192. Epub 2016 Sep 16 doi: 10.1016/j.chest.2016.09.001. PMID: 27645688Free PMC Article
Contemporary management of acute right ventricular failure: a statement from the Heart Failure Association and the Working Group on Pulmonary Circulation and Right Ventricular Function of the European Society of Cardiology.
Harjola VP, Mebazaa A, Čelutkienė J, Bettex D, Bueno H, Chioncel O, Crespo-Leiro MG, Falk V, Filippatos G, Gibbs S, Leite-Moreira A, Lassus J, Masip J, Mueller C, Mullens W, Naeije R, Nordegraaf AV, Parissis J, Riley JP, Ristic A, Rosano G, Rudiger A, Ruschitzka F, Seferovic P, Sztrymf B, Vieillard-Baron A, Yilmaz MB, Konstantinides S
Eur J Heart Fail 2016 Mar;18(3):226-41. doi: 10.1002/ejhf.478. PMID: 26995592
Left ventricular heart failure and pulmonary hypertension.
Rosenkranz S, Gibbs JS, Wachter R, De Marco T, Vonk-Noordegraaf A, Vachiéry JL
Eur Heart J 2016 Mar 21;37(12):942-54. Epub 2015 Oct 27 doi: 10.1093/eurheartj/ehv512. PMID: 26508169Free PMC Article

Therapy

Exercise Stress Echocardiography of the Right Ventricle and Pulmonary Circulation.
Gargani L, Pugliese NR, De Biase N, Mazzola M, Agoston G, Arcopinto M, Argiento P, Armstrong WF, Bandera F, Cademartiri F, Carbone A, Castaldo R, Citro R, Cocchia R, Codullo V, D'Alto M, D'Andrea A, Douschan P, Fabiani I, Ferrara F, Franzese M, Frumento P, Ghio S, Grünig E, Guazzi M, Kasprzak JD, Kolias T, Kovacs G, La Gerche A, Limogelli G, Marra AM, Matucci-Cerinic M, Mauro C, Moreo A, Pratali L, Ranieri B, Rega S, Rudski L, Saggar R, Salzano A, Serra W, Stanziola AA, Vannan MA, Voilliot D, Vriz O, Wierzbowska-Drabik K, Cittadini A, Naeije R, Bossone E; RIGHT Heart International NETwork (RIGHT-NET) Investigators
J Am Coll Cardiol 2023 Nov 21;82(21):1973-1985. doi: 10.1016/j.jacc.2023.09.807. PMID: 37968015
Percutaneous treatment options for acute pulmonary embolism: a clinical consensus statement by the ESC Working Group on Pulmonary Circulation and Right Ventricular Function and the European Association of Percutaneous Cardiovascular Interventions.
Pruszczyk P, Klok FA, Kucher N, Roik M, Meneveau N, Sharp ASP, Nielsen-Kudsk JE, Obradović S, Barco S, Giannini F, Stefanini G, Tarantini G, Konstantinides S, Dudek D
EuroIntervention 2022 Oct 7;18(8):e623-e638. doi: 10.4244/EIJ-D-22-00246. PMID: 36112184Free PMC Article
Pulmonary Vasodilators and Anesthesia Considerations.
Green JB, Hart B, Cornett EM, Kaye AD, Salehi A, Fox CJ
Anesthesiol Clin 2017 Jun;35(2):221-232. Epub 2017 Apr 14 doi: 10.1016/j.anclin.2017.01.008. PMID: 28526144
Disorders of the pulmonary circulation.
Pineo GF, Hull RD
Curr Opin Pulm Med 2012 Sep;18(5):391-2. doi: 10.1097/MCP.0b013e3283560729. PMID: 22759769
Bronchopulmonary dysplasia.
Kinsella JP, Greenough A, Abman SH
Lancet 2006 Apr 29;367(9520):1421-31. doi: 10.1016/S0140-6736(06)68615-7. PMID: 16650652

Prognosis

Exercise Stress Echocardiography of the Right Ventricle and Pulmonary Circulation.
Gargani L, Pugliese NR, De Biase N, Mazzola M, Agoston G, Arcopinto M, Argiento P, Armstrong WF, Bandera F, Cademartiri F, Carbone A, Castaldo R, Citro R, Cocchia R, Codullo V, D'Alto M, D'Andrea A, Douschan P, Fabiani I, Ferrara F, Franzese M, Frumento P, Ghio S, Grünig E, Guazzi M, Kasprzak JD, Kolias T, Kovacs G, La Gerche A, Limogelli G, Marra AM, Matucci-Cerinic M, Mauro C, Moreo A, Pratali L, Ranieri B, Rega S, Rudski L, Saggar R, Salzano A, Serra W, Stanziola AA, Vannan MA, Voilliot D, Vriz O, Wierzbowska-Drabik K, Cittadini A, Naeije R, Bossone E; RIGHT Heart International NETwork (RIGHT-NET) Investigators
J Am Coll Cardiol 2023 Nov 21;82(21):1973-1985. doi: 10.1016/j.jacc.2023.09.807. PMID: 37968015
Acute high-altitude sickness.
Luks AM, Swenson ER, Bärtsch P
Eur Respir Rev 2017 Jan;26(143) Epub 2017 Jan 31 doi: 10.1183/16000617.0096-2016. PMID: 28143879Free PMC Article
The Relationship Between the Right Ventricle and its Load in Pulmonary Hypertension.
Vonk Noordegraaf A, Westerhof BE, Westerhof N
J Am Coll Cardiol 2017 Jan 17;69(2):236-243. doi: 10.1016/j.jacc.2016.10.047. PMID: 28081831
Left ventricular heart failure and pulmonary hypertension.
Rosenkranz S, Gibbs JS, Wachter R, De Marco T, Vonk-Noordegraaf A, Vachiéry JL
Eur Heart J 2016 Mar 21;37(12):942-54. Epub 2015 Oct 27 doi: 10.1093/eurheartj/ehv512. PMID: 26508169Free PMC Article
Bronchopulmonary dysplasia.
Kinsella JP, Greenough A, Abman SH
Lancet 2006 Apr 29;367(9520):1421-31. doi: 10.1016/S0140-6736(06)68615-7. PMID: 16650652

Clinical prediction guides

Exercise Stress Echocardiography of the Right Ventricle and Pulmonary Circulation.
Gargani L, Pugliese NR, De Biase N, Mazzola M, Agoston G, Arcopinto M, Argiento P, Armstrong WF, Bandera F, Cademartiri F, Carbone A, Castaldo R, Citro R, Cocchia R, Codullo V, D'Alto M, D'Andrea A, Douschan P, Fabiani I, Ferrara F, Franzese M, Frumento P, Ghio S, Grünig E, Guazzi M, Kasprzak JD, Kolias T, Kovacs G, La Gerche A, Limogelli G, Marra AM, Matucci-Cerinic M, Mauro C, Moreo A, Pratali L, Ranieri B, Rega S, Rudski L, Saggar R, Salzano A, Serra W, Stanziola AA, Vannan MA, Voilliot D, Vriz O, Wierzbowska-Drabik K, Cittadini A, Naeije R, Bossone E; RIGHT Heart International NETwork (RIGHT-NET) Investigators
J Am Coll Cardiol 2023 Nov 21;82(21):1973-1985. doi: 10.1016/j.jacc.2023.09.807. PMID: 37968015
Pathophysiology of the right ventricle in health and disease: an update.
Tello K, Naeije R, de Man F, Guazzi M
Cardiovasc Res 2023 Aug 19;119(10):1891-1904. doi: 10.1093/cvr/cvad108. PMID: 37463510
Exercise Testing in the Risk Assessment of Pulmonary Hypertension.
Forbes LM, Bull TM, Lahm T, Make BJ, Cornwell WK 3rd
Chest 2023 Sep;164(3):736-746. Epub 2023 Apr 14 doi: 10.1016/j.chest.2023.04.013. PMID: 37061028Free PMC Article
Physiological mechanisms of pulmonary hypertension.
MacIver DH, Adeniran I, MacIver IR, Revell A, Zhang H
Am Heart J 2016 Oct;180:1-11. Epub 2016 Jul 15 doi: 10.1016/j.ahj.2016.07.003. PMID: 27659877
Clinical and research measurement techniques of the pulmonary circulation: the present and the future.
Naeije R, D'Alto M, Forfia PR
Prog Cardiovasc Dis 2015 Mar-Apr;57(5):463-72. Epub 2014 Dec 19 doi: 10.1016/j.pcad.2014.12.003. PMID: 25534670

Recent systematic reviews

Comparison of Different Treatments of Persistent Pulmonary Hypertension of the Newborn: A Systematic Review and Network Meta-Analysis.
Fei Q, Pan J, Zhang F, Lin Y, Yuan T
Crit Care Med 2024 Jun 1;52(6):e314-e322. Epub 2024 Feb 16 doi: 10.1097/CCM.0000000000006227. PMID: 38363176
Pulmonary vasodilators and exercise in Fontan circulation: a systematic review and meta-analysis.
Kosmidis D, Arvanitaki A, Farmakis IT, Liakos A, Giannopoulos A, Ziakas A, Giannakoulas G
Heart 2024 Mar 22;110(8):552-559. doi: 10.1136/heartjnl-2023-323166. PMID: 37918902
Oxygen Therapy in Pulmonary Vascular Disease: A Systematic Review, Meta-Analysis, and Comment.
Schuster M, Müller J, Schwarz EI, Saxer S, Schneider SR, Ulrich S, Lichtblau M
Heart Fail Clin 2023 Jan;19(1S):e1-e11. Epub 2023 Feb 26 doi: 10.1016/j.hfc.2022.11.001. PMID: 36922056Free PMC Article
Optical coherence tomography of the pulmonary arteries: A systematic review.
Jorge E, Baptista R, Calisto J, Faria H, Monteiro P, Pan M, Pêgo M
J Cardiol 2016 Jan;67(1):6-14. Epub 2015 Nov 10 doi: 10.1016/j.jjcc.2015.09.024. PMID: 26572955
Risk of cardiovascular comorbidity in patients with chronic obstructive pulmonary disease: a systematic review and meta-analysis.
Chen W, Thomas J, Sadatsafavi M, FitzGerald JM
Lancet Respir Med 2015 Aug;3(8):631-9. Epub 2015 Jul 22 doi: 10.1016/S2213-2600(15)00241-6. PMID: 26208998

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