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Congenital coronary artery anomaly

MedGen UID:
510602
•Concept ID:
C0158623
•
Congenital Abnormality
Synonym: Coronary artery anomalies
SNOMED CT: Congenital anomaly of coronary artery (28574005); Coronary artery anomaly (28574005)
 
Monarch Initiative: MONDO:0001389

Professional guidelines

PubMed

Diagnosis and Management of Congenital Coronary Artery Fistulas in Infants and Children.
Wu S, Fares M, Zellers TM, Jyothinagaram M, Reddy SRV
Curr Cardiol Rep 2023 Dec;25(12):1921-1932. Epub 2023 Dec 5 doi: 10.1007/s11886-023-02007-0. PMID: 38051412
Myocardial Bridging: Diagnosis, Functional Assessment, and Management: JACC State-of-the-Art Review.
Sternheim D, Power DA, Samtani R, Kini A, Fuster V, Sharma S
J Am Coll Cardiol 2021 Nov 30;78(22):2196-2212. doi: 10.1016/j.jacc.2021.09.859. PMID: 34823663
Spontaneous Coronary Artery Dissection: Current State of the Science: A Scientific Statement From the American Heart Association.
Hayes SN, Kim ESH, Saw J, Adlam D, Arslanian-Engoren C, Economy KE, Ganesh SK, Gulati R, Lindsay ME, Mieres JH, Naderi S, Shah S, Thaler DE, Tweet MS, Wood MJ; American Heart Association Council on Peripheral Vascular Disease; Council on Clinical Cardiology; Council on Cardiovascular and Stroke Nursing; Council on Genomic and Precision Medicine; and Stroke Council
Circulation 2018 May 8;137(19):e523-e557. Epub 2018 Feb 22 doi: 10.1161/CIR.0000000000000564. PMID: 29472380Free PMC Article

Recent clinical studies

Etiology

Coronary Artery Anomalies and Their Impact on the Feasibility of Percutaneous Pulmonary Valve Implantation.
Hanser A, Michel J, Hornung A, Sieverding L, Hofbeck M
Pediatr Cardiol 2022 Jan;43(1):8-16. Epub 2021 Aug 7 doi: 10.1007/s00246-021-02684-0. PMID: 34363499Free PMC Article
Congenital Coronary Artery Anomalies and Sudden Cardiac Death.
Schiavone M, Gobbi C, Gasperetti A, Zuffi A, Forleo GB
Pediatr Cardiol 2021 Dec;42(8):1676-1687. Epub 2021 Aug 30 doi: 10.1007/s00246-021-02713-y. PMID: 34459947
Unusual Association of Three Types of Congenital Coronary Artery Diseases.
Isorni MA, Amato A, Guihaire J
Can J Cardiol 2018 Sep;34(9):1233.e5-1233.e8. Epub 2018 Jun 8 doi: 10.1016/j.cjca.2018.05.026. PMID: 30170682
Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA), a forgotten congenital cause of sudden death in the adult.
Krexi L, Sheppard MN
Cardiovasc Pathol 2013 Jul-Aug;22(4):294-7. Epub 2013 Jan 8 doi: 10.1016/j.carpath.2012.11.006. PMID: 23305712
Importance of coronary artery anomalies in operations for congenital heart disease.
Landolt CC, Anderson JE, Zorn-Chelton S, Guyton RA, Hatcher CR Jr, Williams WH
Ann Thorac Surg 1986 Apr;41(4):351-5. doi: 10.1016/s0003-4975(10)62684-7. PMID: 3963912

Diagnosis

Congenital Coronary Artery Anomalies and Sudden Cardiac Death.
Schiavone M, Gobbi C, Gasperetti A, Zuffi A, Forleo GB
Pediatr Cardiol 2021 Dec;42(8):1676-1687. Epub 2021 Aug 30 doi: 10.1007/s00246-021-02713-y. PMID: 34459947
Unusual congenital coronary artery anomaly in a young adult presenting as sudden cardiac arrest.
Cortes M, Roldan CA, Clegg S
BMJ Case Rep 2018 Apr 24;2018 doi: 10.1136/bcr-2017-221995. PMID: 29691271Free PMC Article
Congenital coronary artery anomaly simulating a ventricular septal defect.
Azari A, Moravvej Z, Fazlinezhad A, Bigdelu L
Asian Cardiovasc Thorac Ann 2015 Nov;23(9):1062-4. Epub 2014 Apr 9 doi: 10.1177/0218492314531422. PMID: 24719168
ALCAPA syndrome: not just a pediatric disease.
Peña E, Nguyen ET, Merchant N, Dennie C
Radiographics 2009 Mar-Apr;29(2):553-65. doi: 10.1148/rg.292085059. PMID: 19325065
Coronary artery anomalies: classification and electrocardiogram-gated multidetector computed tomographic findings.
Kang JW, Seo JB, Chae EJ, Jang YM, Do KH, Lee JS, Song JW, Lim TH
Semin Ultrasound CT MR 2008 Jun;29(3):182-94. doi: 10.1053/j.sult.2008.02.004. PMID: 18564542

Therapy

Symptomatic myocardial bridging: a frequently occurring coronary variation can cause severe myocardial ischaemia in affected children with underlying cardiac conditions.
Kiess A, Vollroth M, Bakhtiary F, Seki H, Kostelka M, Djukic M, Daehnert I, Wagner R
Cardiol Young 2018 Jun;28(6):826-831. Epub 2018 May 16 doi: 10.1017/S1047951118000409. PMID: 29764528
Isolated myocardial bridging and exercise-related cardiac events.
Gowd BM, Thompson PD
Int J Sports Med 2014 Dec;35(14):1145-50. Epub 2014 Aug 21 doi: 10.1055/s-0034-1370912. PMID: 25144435

Prognosis

Characterizing an absent right coronary artery through 3-dimensional coronary computed tomography angiography.
Lee HC, Lai HY, Hsieh KL, Lan GY
Rev Cardiovasc Med 2018 Sep 30;19(3):111-112. doi: 10.31083/j.rcm.2018.03.3184. PMID: 31054560
Unusual Association of Three Types of Congenital Coronary Artery Diseases.
Isorni MA, Amato A, Guihaire J
Can J Cardiol 2018 Sep;34(9):1233.e5-1233.e8. Epub 2018 Jun 8 doi: 10.1016/j.cjca.2018.05.026. PMID: 30170682
Adult-type ALCAPA syndrome: A rare coronary artery anomaly.
Patrianakos AP, Hatzidakis A, Marketou M, Parthenakis FI
Echocardiography 2018 Jul;35(7):1056-1059. Epub 2018 May 11 doi: 10.1111/echo.14013. PMID: 29749648
Congenital coronary artery anomaly simulating a ventricular septal defect.
Azari A, Moravvej Z, Fazlinezhad A, Bigdelu L
Asian Cardiovasc Thorac Ann 2015 Nov;23(9):1062-4. Epub 2014 Apr 9 doi: 10.1177/0218492314531422. PMID: 24719168
ALCAPA syndrome: not just a pediatric disease.
Peña E, Nguyen ET, Merchant N, Dennie C
Radiographics 2009 Mar-Apr;29(2):553-65. doi: 10.1148/rg.292085059. PMID: 19325065

Clinical prediction guides

Congenital Coronary Artery Anomalies and Sudden Cardiac Death.
Schiavone M, Gobbi C, Gasperetti A, Zuffi A, Forleo GB
Pediatr Cardiol 2021 Dec;42(8):1676-1687. Epub 2021 Aug 30 doi: 10.1007/s00246-021-02713-y. PMID: 34459947
Characterizing an absent right coronary artery through 3-dimensional coronary computed tomography angiography.
Lee HC, Lai HY, Hsieh KL, Lan GY
Rev Cardiovasc Med 2018 Sep 30;19(3):111-112. doi: 10.31083/j.rcm.2018.03.3184. PMID: 31054560
Unusual Association of Three Types of Congenital Coronary Artery Diseases.
Isorni MA, Amato A, Guihaire J
Can J Cardiol 2018 Sep;34(9):1233.e5-1233.e8. Epub 2018 Jun 8 doi: 10.1016/j.cjca.2018.05.026. PMID: 30170682
Congenital coronary artery anomaly simulating a ventricular septal defect.
Azari A, Moravvej Z, Fazlinezhad A, Bigdelu L
Asian Cardiovasc Thorac Ann 2015 Nov;23(9):1062-4. Epub 2014 Apr 9 doi: 10.1177/0218492314531422. PMID: 24719168
Single right coronary artery-R-I subtype: a report of an extremely rare case.
Serçelik A, Akbulut E, Mavi A, Batyraliev T, Gümüşburun E
Morphologie 2008 Aug;92(297):90-3. Epub 2008 Jul 23 doi: 10.1016/j.morpho.2008.06.001. PMID: 18653368

Recent systematic reviews

A Contemporary Review of the Genomic Associations of Coronary Artery Myocardial Bridging.
Moore P, Murdock P, Ramanathan A, Sathyamoorthy M
Genes (Basel) 2023 Dec 4;14(12) doi: 10.3390/genes14122175. PMID: 38136997Free PMC Article

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