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Cruveilhier-Baumgarten syndrome

MedGen UID:
8187
•Concept ID:
C0010398
•
Disease or Syndrome
Synonyms: Cruveilhier Baumgarten Disease; Cruveilhier Baumgarten Syndrome; Cruveilhier-Baumgarten Disease; Cruveilhier-Baumgarten Syndrome; Disease, Cruveilhier-Baumgarten; Syndrome, Cruveilhier-Baumgarten
SNOMED CT: Cruveilhier-Baumgarten syndrome (45256007)

Definition

Liver cirrhosis with intrahepatic portal obstruction, HYPERTENSION, and patent UMBILICAL VEINS. [from MeSH]

Professional guidelines

PubMed

AASLD Practice Guidance on risk stratification and management of portal hypertension and varices in cirrhosis.
Kaplan DE, Ripoll C, Thiele M, Fortune BE, Simonetto DA, Garcia-Tsao G, Bosch J
Hepatology 2024 May 1;79(5):1180-1211. Epub 2023 Oct 23 doi: 10.1097/HEP.0000000000000647. PMID: 37870298
Evidence-based clinical practice guidelines for Liver Cirrhosis 2020.
Yoshiji H, Nagoshi S, Akahane T, Asaoka Y, Ueno Y, Ogawa K, Kawaguchi T, Kurosaki M, Sakaida I, Shimizu M, Taniai M, Terai S, Nishikawa H, Hiasa Y, Hidaka H, Miwa H, Chayama K, Enomoto N, Shimosegawa T, Takehara T, Koike K
J Gastroenterol 2021 Jul;56(7):593-619. Epub 2021 Jul 7 doi: 10.1007/s00535-021-01788-x. PMID: 34231046Free PMC Article
Diagnosis and Management of Hepatic Encephalopathy.
Rudler M, Weiss N, Bouzbib C, Thabut D
Clin Liver Dis 2021 May;25(2):393-417. Epub 2021 Mar 11 doi: 10.1016/j.cld.2021.01.008. PMID: 33838857

Recent clinical studies

Etiology

Cruveilhier-Baumgarten syndrome: an efficient spontaneous portosystemic collateral preventing oesophageal varices bleeding.
Caturelli E, Pompili M, Squillante MM, Sperandeo G, Carughi S, Sperandeo M, Perri F, Andriulli A, Cellerino C, Rapaccini GL
J Gastroenterol Hepatol 1994 May-Jun;9(3):236-41. doi: 10.1111/j.1440-1746.1994.tb01716.x. PMID: 8054522
The importance of variant insertions of the ligamentum teres hepatis in the Cruveilhier-Baumgarten syndrome.
Friedrich K, Vogel HM, Henning H
Endoscopy 1988 Sep;20(5):254-9. doi: 10.1055/s-2007-1018187. PMID: 2971527

Diagnosis

Giant paraumblical veins in Cruveilhier-Baumgarten syndrome.
Sodhi KS, Saxena AK, Khandelwal N, Dhiman RK
Gastrointest Endosc 2010 Aug;72(2):435-6; discussion 436. Epub 2010 Jun 11 doi: 10.1016/j.gie.2010.02.005. PMID: 20538272
Cruveilhier-Baumgarten syndrome in idiopathic portal hypertension.
Chawla YK, Bhushnurmath SR, Dilawari JB
Am J Gastroenterol 1987 Dec;82(12):1336-7. PMID: 3687914
Ultrasonic diagnosis of Cruveilhier-Baumgarten syndrome.
Capron JP, Clément J, Descombes P, Delamarre J, Dupas JL, Rémond A
JAMA 1982 Feb 5;247(5):681-2. PMID: 7054571
The Cruveilhier-Baumgarten syndrome.
Chelvam P, Ahmad Z, Weng Hwa N
Med J Malaysia 1979 Mar;33(3):266-8. PMID: 522733
CRUVEILHIER-BAUMGARTEN SYNDROME.
SINGH A, LAKHANPAL VP
J Indian Med Assoc 1963 Sep 1;41:259-61. PMID: 14063353

Therapy

Cruveilhier-Baumgarten syndrome in a cirrhotic patient taking alcohol with Boesenbergia pundurata.
Wilairatana P, Tangpukdee N, Jittaseree L
Southeast Asian J Trop Med Public Health 2010 Sep;41(5):1267-70. PMID: 21073049
Cruveilhier-Baumgarten syndrome in which venous hum disappeared following endoscopic variceal sclerotherapy.
Yamakawa O, Ohta H, Watanabe H, Motoo Y, Okai T, Kadoya M, Matsui O, Sawabu N
J Gastroenterol 1996 Aug;31(4):618-22. doi: 10.1007/BF02355069. PMID: 8844490
Development of the Cruveilhier-Baumgarten syndrome after endoscopic obliteration of oesophageal varices. Report of a case.
Dilawari JB, Chawla YK, Kaur U
Acta Radiol 1989 Jul-Aug;30(4):401-2. PMID: 2775603
The importance of variant insertions of the ligamentum teres hepatis in the Cruveilhier-Baumgarten syndrome.
Friedrich K, Vogel HM, Henning H
Endoscopy 1988 Sep;20(5):254-9. doi: 10.1055/s-2007-1018187. PMID: 2971527

Prognosis

The importance of variant insertions of the ligamentum teres hepatis in the Cruveilhier-Baumgarten syndrome.
Friedrich K, Vogel HM, Henning H
Endoscopy 1988 Sep;20(5):254-9. doi: 10.1055/s-2007-1018187. PMID: 2971527
Venous hum of the Cruveilhier-Baumgarten syndrome: response to the Valsalva maneuver.
Hardison JE
Arch Intern Med 1977 Nov;137(11):1623-4. PMID: 921454

Clinical prediction guides

Patent paraumbilical vein: anatomic and hemodynamic variants and their clinical importance.
Morin C, Lafortune M, Pomier G, Robin M, Breton G
Radiology 1992 Oct;185(1):253-6. doi: 10.1148/radiology.185.1.1523319. PMID: 1523319
Development of the Cruveilhier-Baumgarten syndrome after endoscopic obliteration of oesophageal varices. Report of a case.
Dilawari JB, Chawla YK, Kaur U
Acta Radiol 1989 Jul-Aug;30(4):401-2. PMID: 2775603
Venous hum of the Cruveilhier-Baumgarten syndrome: response to the Valsalva maneuver.
Hardison JE
Arch Intern Med 1977 Nov;137(11):1623-4. PMID: 921454

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