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Syringomyelia and Hydromyelia

MedGen UID:: 888087
•Concept ID:: C4053961
•: Disease or Syndrome

Definition

Syringomyelia associated with accumulation of cerebrospinal fluid in the spinal cord. [from NCI]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVSyringomyelia and Hydromyelia

Morphological central nervous system abnormality
- Abnormal neural tube morphology
  - Neural tube defect
    - Closed neural tube defect
      - Myelopathy
        Syringomyelia
        Syringomyelia and Hydromyelia

Professional guidelines

PubMed

Treatment of posttraumatic syringomyelia: evidence from a systematic review.

Kleindienst A, Laut FM, Roeckelein V, Buchfelder M, Dodoo-Schittko F
Acta Neurochir (Wien) 2020 Oct;162(10):2541-2556. Epub 2020 Aug 20 doi: 10.1007/s00701-020-04529-w. PMID: 32820376 Free PMC Article

Hydromyelia: clinical presentation and comparison of modalities of treatment.

Schlesinger EB, Antunes JL, Michelsen WJ, Louis KM
Neurosurgery 1981 Oct;9(4):356-65. doi: 10.1227/00006123-198110000-00002. PMID: 7301079

See all (2)

Recent clinical studies

Etiology

Chiari Malformations.

Mancarella C, Delfini R, Landi A
Acta Neurochir Suppl 2019;125:89-95. doi: 10.1007/978-3-319-62515-7_13. PMID: 30610307

Surgical treatment of late neurological deterioration in children with myelodysplasia.

Caldarelli M, Di Rocco C, Colosimo C Jr, Fariello G, Di Gennaro M
Acta Neurochir (Wien) 1995;137(3-4):199-206. doi: 10.1007/BF02187194. PMID: 8789662

Surgical treatment of "hindbrain related" syringomyelia: new data for pathogenesis.

Blagodatsky MD, Larionov SN, Manohin PA, Shanturov VA, Gladyshev YuV
Acta Neurochir (Wien) 1993;124(2-4):82-5. doi: 10.1007/BF01401127. PMID: 8304075

Malformations of the spinal cord in 53 patients with spina bifida studied by magnetic resonance imaging.

Azimullah PC, Smit LM, Rietveld-Knol E, Valk J
Childs Nerv Syst 1991 Apr;7(2):63-6. doi: 10.1007/BF00247858. PMID: 1863931

Chiari I malformations and hydromyelia--complications.

Menezes AH
Pediatr Neurosurg 1991-1992;17(3):146-54. doi: 10.1159/000120586. PMID: 1819330

See all (21)

Diagnosis

Syringomyelia and hydromyelia: Current understanding and neurosurgical management.

Leclerc A, Matveeff L, Emery E
Rev Neurol (Paris) 2021 May;177(5):498-507. Epub 2020 Aug 18 doi: 10.1016/j.neurol.2020.07.004. PMID: 32826067

Chiari Malformations.

Mancarella C, Delfini R, Landi A
Acta Neurochir Suppl 2019;125:89-95. doi: 10.1007/978-3-319-62515-7_13. PMID: 30610307

An Exceptional Neurosurgical Presentation of a Patient with Osteopetrosis.

Isler C, Kayhan A, Ugurlar D, Hanimoglu H, Ulu MO, Uzan M, Erdincler P, Ozlen F
World Neurosurg 2018 Nov;119:25-29. Epub 2018 Jun 20 doi: 10.1016/j.wneu.2018.06.081. PMID: 29935324

MR imaging of the spinal cord: current status and future advances.

Sze G
AJR Am J Roentgenol 1992 Jul;159(1):149-59. doi: 10.2214/ajr.159.1.1609689. PMID: 1609689

Hydromyelia: a critical review.

Wisoff JH
Childs Nerv Syst 1988 Feb;4(1):1-8. doi: 10.1007/BF00274073. PMID: 3042131

See all (40)

Therapy

The Management of Idiopathic and Refractory Syringomyelia.

Gallo P, Kaliaperumal C
Adv Tech Stand Neurosurg 2022;45:317-338. doi: 10.1007/978-3-030-99166-1_10. PMID: 35976455

Treatment of posttraumatic syringomyelia: evidence from a systematic review.

Acute central canal dilatation after minimally invasive lateral cervical decompression through the Frykholm approach.

Foelsch C, Peterlein CD, Fuchs-Winkelmann S, Lakemeier S
J Spinal Disord Tech 2011 May;24(3):208-11. doi: 10.1097/BSD.0b013e3181e16217. PMID: 21519303

Hydromyelia in a child with chiari II.

McLone DG
Pediatr Neurosurg 2000 Jun;32(6):328. doi: 10.1159/000028963. PMID: 10971196

US of the spinal cord in newborns: spectrum of normal findings, variants, congenital anomalies, and acquired diseases.

Unsinn KM, Geley T, Freund MC, Gassner I
Radiographics 2000 Jul-Aug;20(4):923-38. doi: 10.1148/radiographics.20.4.g00jl06923. PMID: 10903684

See all (6)

Prognosis

Spinal sonography and magnetic resonance imaging in patients with repaired myelomeningocele: comparison of modalities.

Gerscovich EO, Maslen L, Cronan MS, Poirier V, Anderson MW, McDonald C, Boggan JE, Ivanovic M
J Ultrasound Med 1999 Sep;18(9):655-64. doi: 10.7863/jum.1999.18.9.655. PMID: 10478975

Surgical treatment of late neurological deterioration in children with myelodysplasia.

Caldarelli M, Di Rocco C, Colosimo C Jr, Fariello G, Di Gennaro M
Acta Neurochir (Wien) 1995;137(3-4):199-206. doi: 10.1007/BF02187194. PMID: 8789662

Surgical treatment of "hindbrain related" syringomyelia: new data for pathogenesis.

Blagodatsky MD, Larionov SN, Manohin PA, Shanturov VA, Gladyshev YuV
Acta Neurochir (Wien) 1993;124(2-4):82-5. doi: 10.1007/BF01401127. PMID: 8304075

Chiari I malformations and hydromyelia--complications.

Menezes AH
Pediatr Neurosurg 1991-1992;17(3):146-54. doi: 10.1159/000120586. PMID: 1819330

Hydromyelia: a critical review.

Wisoff JH
Childs Nerv Syst 1988 Feb;4(1):1-8. doi: 10.1007/BF00274073. PMID: 3042131

See all (18)

Clinical prediction guides

Treatment of posttraumatic syringomyelia: evidence from a systematic review.

Clinical Relevance of Preoperative MRI in Adolescent Idiopathic Scoliosis: Is Hydromyelia a Predictive Factor of Intraoperative Electrophysiological Monitoring Alterations?

Scaramuzzo L, Giudici F, Archetti M, Minoia L, Zagra A, Bongetta D
Clin Spine Surg 2019 May;32(4):E183-E187. doi: 10.1097/BSD.0000000000000820. PMID: 30913042

Delayed resolution of Chiari I-associated hydromyelia after posterior fossa decompression: case report and review of the literature.

Doughty KE, Tubbs RS, Webb D, Oakes WJ
Neurosurgery 2004 Sep;55(3):711. doi: 10.1227/01.neu.0000134548.16165.9. PMID: 16933383

Treatment of hydromyelia in spina bifida.

Caldarelli M, Di Rocco C, La Marca F
Surg Neurol 1998 Nov;50(5):411-20. doi: 10.1016/s0090-3019(97)00457-6. PMID: 9842864

Magnetic resonance imaging of the spinal cord in spinal dysraphisms.

Szalay EA, Roach JW, Smith H, Maravilla K, Partain CL
J Pediatr Orthop 1987 Sep-Oct;7(5):541-5. doi: 10.1097/01241398-198709000-00008. PMID: 3624464

See all (9)