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Abnormal pulmonary lymphatics

MedGen UID:
870577
•Concept ID:
C4025026
•
Anatomical Abnormality
HPO: HP:0006529

Definition

An abnormality of the pulmonary lymphatic chain. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAbnormal pulmonary lymphatics

Professional guidelines

PubMed

Kaposiform lymphangiomatosis: Diagnosis, pathogenesis, and treatment.
McDaniel CG, Adams DM, Steele KE, Hammill AM, Merrow AC, Crane JL, Smith CL, Kozakewich HPW, Le Cras TD
Pediatr Blood Cancer 2023 Apr;70(4):e30219. Epub 2023 Jan 22 doi: 10.1002/pbc.30219. PMID: 36683202Free PMC Article
Congenital heart defects in Noonan syndrome: Diagnosis, management, and treatment.
Linglart L, Gelb BD
Am J Med Genet C Semin Med Genet 2020 Mar;184(1):73-80. Epub 2020 Feb 5 doi: 10.1002/ajmg.c.31765. PMID: 32022400Free PMC Article
Management of the adult Fontan patient.
Rodriguez FH, Book WM
Heart 2020 Jan;106(2):105-110. Epub 2019 Oct 29 doi: 10.1136/heartjnl-2019-314937. PMID: 31662332

Recent clinical studies

Therapy

Interventional Treatment of Pulmonary Lymphatic Anomalies.
Itkin M
Tech Vasc Interv Radiol 2016 Dec;19(4):299-304. Epub 2016 Oct 8 doi: 10.1053/j.tvir.2016.10.005. PMID: 27993326
Plastic Bronchitis.
Rubin BK
Clin Chest Med 2016 Sep;37(3):405-8. Epub 2016 Jun 15 doi: 10.1016/j.ccm.2016.04.003. PMID: 27514587
Lymphangioleiomyomatosis.
Johnson SR, Taveira-DaSilva AM, Moss J
Clin Chest Med 2016 Sep;37(3):389-403. doi: 10.1016/j.ccm.2016.04.002. PMID: 27514586
Yellow nail syndrome.
Maldonado F, Ryu JH
Curr Opin Pulm Med 2009 Jul;15(4):371-5. doi: 10.1097/MCP.0b013e32832ad45a. PMID: 19373089
Taxane-induced scleroderma.
Itoh M, Yanaba K, Kobayashi T, Nakagawa H
Br J Dermatol 2007 Feb;156(2):363-7. doi: 10.1111/j.1365-2133.2006.07597.x. PMID: 17223879

Prognosis

Congenital heart defects in Noonan syndrome: Diagnosis, management, and treatment.
Linglart L, Gelb BD
Am J Med Genet C Semin Med Genet 2020 Mar;184(1):73-80. Epub 2020 Feb 5 doi: 10.1002/ajmg.c.31765. PMID: 32022400Free PMC Article
Lymphangioleiomyomatosis.
Doubková M, Štefániková M, Čan V, Merta Z, Svoboda M
Klin Onkol 2019 Fall;32(5):367-374. doi: 10.14735/amko2019367. PMID: 31610670
Yellow nail syndrome.
Maldonado F, Ryu JH
Curr Opin Pulm Med 2009 Jul;15(4):371-5. doi: 10.1097/MCP.0b013e32832ad45a. PMID: 19373089
Taxane-induced scleroderma.
Itoh M, Yanaba K, Kobayashi T, Nakagawa H
Br J Dermatol 2007 Feb;156(2):363-7. doi: 10.1111/j.1365-2133.2006.07597.x. PMID: 17223879
Noonan syndrome.
van der Burgt I
Orphanet J Rare Dis 2007 Jan 14;2:4. doi: 10.1186/1750-1172-2-4. PMID: 17222357Free PMC Article

Clinical prediction guides

Lung disease manifestations in Down syndrome.
Danopoulos S, Deutsch GH, Dumortier C, Mariani TJ, Al Alam D
Am J Physiol Lung Cell Mol Physiol 2021 Nov 1;321(5):L892-L899. Epub 2021 Sep 1 doi: 10.1152/ajplung.00434.2020. PMID: 34469245Free PMC Article
Lymphangioleiomyomatosis.
Doubková M, Štefániková M, Čan V, Merta Z, Svoboda M
Klin Onkol 2019 Fall;32(5):367-374. doi: 10.14735/amko2019367. PMID: 31610670
Bone Morphogenetic Proteins in Vascular Homeostasis and Disease.
Goumans MJ, Zwijsen A, Ten Dijke P, Bailly S
Cold Spring Harb Perspect Biol 2018 Feb 1;10(2) doi: 10.1101/cshperspect.a031989. PMID: 28348038Free PMC Article
Interventional Treatment of Pulmonary Lymphatic Anomalies.
Itkin M
Tech Vasc Interv Radiol 2016 Dec;19(4):299-304. Epub 2016 Oct 8 doi: 10.1053/j.tvir.2016.10.005. PMID: 27993326
Proteus syndrome review: molecular, clinical, and pathologic features.
Cohen MM Jr
Clin Genet 2014 Feb;85(2):111-9. Epub 2013 Oct 23 doi: 10.1111/cge.12266. PMID: 23992099

Recent systematic reviews

Bleomycin for orbital and peri-orbital veno-lymphatic malformations - A systematic review.
Faiz K, Finitsis S, Linton J, Shankar JJS
Interv Neuroradiol 2021 Apr;27(2):291-297. Epub 2020 Nov 11 doi: 10.1177/1591019920972514. PMID: 33175616Free PMC Article
Primary angiosarcoma of the femoral artery in patient with kidney and liver polycystosis and multiple arterial aneurysms: report of the case and review of the literature.
Fabian O, Mokra D, Masopust J, Skorepa J, Kodetova DN, Zamecnik J
Cardiovasc Pathol 2019 Mar-Apr;39:8-11. Epub 2018 Nov 30 doi: 10.1016/j.carpath.2018.11.001. PMID: 30579128
Intralesional Bleomycin Injections for Vascular Malformations: A Systematic Review and Meta-Analysis.
Horbach SER, Rigter IM, Smitt JHS, Reekers JA, Spuls PI, van der Horst CMAM
Plast Reconstr Surg 2016 Jan;137(1):244-256. doi: 10.1097/PRS.0000000000001924. PMID: 26710030

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