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Hemihypsarrhythmia

MedGen UID:
869042
•Concept ID:
C4023460
•
Finding
HPO: HP:0011215

Definition

Hypsarrhythmia occurring in one hemisphere. [from HPO]

Professional guidelines

PubMed

Hemimegalencephaly: clinical implications and surgical treatment.
Di Rocco C, Battaglia D, Pietrini D, Piastra M, Massimi L
Childs Nerv Syst 2006 Aug;22(8):852-66. Epub 2006 Jul 5 doi: 10.1007/s00381-006-0149-9. PMID: 16821075

Recent clinical studies

Etiology

Epileptic spasms in clusters with focal EEG paroxysms: A study of 12 patients.
Caraballo RH, Reyes G, Falsaperla R, Ramos B, Ruiz AC, Fernandez CA, Peretti G, Beltran L
Seizure 2016 Feb;35:88-92. Epub 2016 Jan 15 doi: 10.1016/j.seizure.2016.01.012. PMID: 26803282
Hemimegalencephaly: clinical implications and surgical treatment.
Di Rocco C, Battaglia D, Pietrini D, Piastra M, Massimi L
Childs Nerv Syst 2006 Aug;22(8):852-66. Epub 2006 Jul 5 doi: 10.1007/s00381-006-0149-9. PMID: 16821075
Heterogeneity of ictal SPECT findings in nine cases of West syndrome.
Haginoya K, Kon K, Takayanagi M, Yoshihara Y, Kato R, Tanaka S, Yokoyama H, Munakata M, Nagai M, Maruoka S, Yamazaki T, Abe Y, Iinuma K
Epilepsia 1998;39 Suppl 5:26-9. doi: 10.1111/j.1528-1157.1998.tb05146.x. PMID: 9737441
Focal features in West syndrome indicating candidacy for surgery.
Kramer U, Sue WC, Mikati MA
Pediatr Neurol 1997 Apr;16(3):213-7. doi: 10.1016/s0887-8994(97)00013-1. PMID: 9165511
Hypsarrhythmia: frequency of variant patterns and correlation with etiology and outcome.
Kramer U, Sue WC, Mikati MA
Neurology 1997 Jan;48(1):197-203. doi: 10.1212/wnl.48.1.197. PMID: 9008518

Diagnosis

Epileptic spasms in clusters with focal EEG paroxysms: A study of 12 patients.
Caraballo RH, Reyes G, Falsaperla R, Ramos B, Ruiz AC, Fernandez CA, Peretti G, Beltran L
Seizure 2016 Feb;35:88-92. Epub 2016 Jan 15 doi: 10.1016/j.seizure.2016.01.012. PMID: 26803282
A female case of West syndrome with remission of spasms following multiple cerebral hemorrhages.
Hino-Fukuyo N, Haginoya K, Uematsu M, Tsuchiya S
Brain Dev 2011 Sep;33(8):678-82. Epub 2010 Nov 3 doi: 10.1016/j.braindev.2010.10.010. PMID: 21051162
The role of epilepsy in early language development in a child with a congenital lesion in the right hemisphere.
Mayor-Dubois C, Maeder-Ingvar M, Deonna T, Roulet-Perez E
Dev Med Child Neurol 2008 Nov;50(11):870-5. doi: 10.1111/j.1469-8749.2008.03162.x. PMID: 19046180
Heterogeneity of ictal SPECT findings in nine cases of West syndrome.
Haginoya K, Kon K, Takayanagi M, Yoshihara Y, Kato R, Tanaka S, Yokoyama H, Munakata M, Nagai M, Maruoka S, Yamazaki T, Abe Y, Iinuma K
Epilepsia 1998;39 Suppl 5:26-9. doi: 10.1111/j.1528-1157.1998.tb05146.x. PMID: 9737441
Focal features in West syndrome indicating candidacy for surgery.
Kramer U, Sue WC, Mikati MA
Pediatr Neurol 1997 Apr;16(3):213-7. doi: 10.1016/s0887-8994(97)00013-1. PMID: 9165511

Therapy

Epileptic spasms in clusters with focal EEG paroxysms: A study of 12 patients.
Caraballo RH, Reyes G, Falsaperla R, Ramos B, Ruiz AC, Fernandez CA, Peretti G, Beltran L
Seizure 2016 Feb;35:88-92. Epub 2016 Jan 15 doi: 10.1016/j.seizure.2016.01.012. PMID: 26803282
The role of epilepsy in early language development in a child with a congenital lesion in the right hemisphere.
Mayor-Dubois C, Maeder-Ingvar M, Deonna T, Roulet-Perez E
Dev Med Child Neurol 2008 Nov;50(11):870-5. doi: 10.1111/j.1469-8749.2008.03162.x. PMID: 19046180
Hypsarrhythmia: frequency of variant patterns and correlation with etiology and outcome.
Kramer U, Sue WC, Mikati MA
Neurology 1997 Jan;48(1):197-203. doi: 10.1212/wnl.48.1.197. PMID: 9008518

Prognosis

The role of epilepsy in early language development in a child with a congenital lesion in the right hemisphere.
Mayor-Dubois C, Maeder-Ingvar M, Deonna T, Roulet-Perez E
Dev Med Child Neurol 2008 Nov;50(11):870-5. doi: 10.1111/j.1469-8749.2008.03162.x. PMID: 19046180
Heterogeneity of ictal SPECT findings in nine cases of West syndrome.
Haginoya K, Kon K, Takayanagi M, Yoshihara Y, Kato R, Tanaka S, Yokoyama H, Munakata M, Nagai M, Maruoka S, Yamazaki T, Abe Y, Iinuma K
Epilepsia 1998;39 Suppl 5:26-9. doi: 10.1111/j.1528-1157.1998.tb05146.x. PMID: 9737441
Hypsarrhythmia: frequency of variant patterns and correlation with etiology and outcome.
Kramer U, Sue WC, Mikati MA
Neurology 1997 Jan;48(1):197-203. doi: 10.1212/wnl.48.1.197. PMID: 9008518

Clinical prediction guides

Hypsarrhythmia in epileptic spasms: Synchrony in chaos.
Nenadovic V, Whitney R, Boulet J, Cortez MA
Seizure 2018 May;58:55-61. Epub 2018 Mar 30 doi: 10.1016/j.seizure.2018.03.026. PMID: 29656099
Hypsarrhythmia: frequency of variant patterns and correlation with etiology and outcome.
Kramer U, Sue WC, Mikati MA
Neurology 1997 Jan;48(1):197-203. doi: 10.1212/wnl.48.1.197. PMID: 9008518
Hemimegalencephaly and intractable epilepsy: benefits of hemispherectomy.
Vigevano F, Bertini E, Boldrini R, Bosman C, Claps D, di Capua M, di Rocco C, Rossi GF
Epilepsia 1989 Nov-Dec;30(6):833-43. doi: 10.1111/j.1528-1157.1989.tb05347.x. PMID: 2591346

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