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Complete Atrioventricular Canal Defect Unbalanced

MedGen UID:
768594
•Concept ID:
C3639954
•
Congenital Abnormality
Synonym: Complete unbalanced atrioventricular canal defect

Definition

Atrioventricular septal defect in which there is usually a single dominant ventricle and a hypoplastic ventricle. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVComplete Atrioventricular Canal Defect Unbalanced

Recent clinical studies

Etiology

Common arterial trunk in functionally univentricular hearts: a case series.
Elhedai H, Yong S, Chaudhari M, Botha P, Miller P, Stumper O
Cardiol Young 2023 Jul;33(7):1097-1101. Epub 2022 Jul 11 doi: 10.1017/S1047951122002128. PMID: 35815558
Modified Single Repair Technique for Complete Atrioventricular Septal Defect: A Propensity Score Matching Analysis.
Wang G, Ma K, Pang K, Hua Z, Zhang S, Qi L, Yang Y, Feng Z, Mao F, Zhang H, Li S
Pediatr Cardiol 2020 Mar;41(3):615-623. Epub 2020 Jan 23 doi: 10.1007/s00246-020-02292-4. PMID: 31974717
Twelve Years of Complete Atrioventricular Septal Defect Repair.
Sena A, Sheytanov V, Liebrich M, Narr A, Schweigmann U, Uhlemann F, Doll N, Tzanavaros I
Rev Port Cir Cardiotorac Vasc 2019 Jul-Sep;26(3):187-193. PMID: 31734969
Mid-term outcomes in unbalanced complete atrioventricular septal defect: role of biventricular conversion from single-ventricle palliation.
Nathan M, Emani S, IJsselhof R, Liu H, Gauvreau K, Del Nido P
Eur J Cardiothorac Surg 2017 Sep 1;52(3):565-572. doi: 10.1093/ejcts/ezx129. PMID: 28521020
Surgical management of complete atrioventricular septal defect with tetralogy of fallot.
Hu R, Zhang H, Xu Z, Liu J, Su Z, Ding W
Ann Thorac Cardiovasc Surg 2014;20(5):341-6. Epub 2013 Oct 3 doi: 10.5761/atcs.oa.12-02198. PMID: 24088923

Diagnosis

Common arterial trunk in functionally univentricular hearts: a case series.
Elhedai H, Yong S, Chaudhari M, Botha P, Miller P, Stumper O
Cardiol Young 2023 Jul;33(7):1097-1101. Epub 2022 Jul 11 doi: 10.1017/S1047951122002128. PMID: 35815558
Modified Single Repair Technique for Complete Atrioventricular Septal Defect: A Propensity Score Matching Analysis.
Wang G, Ma K, Pang K, Hua Z, Zhang S, Qi L, Yang Y, Feng Z, Mao F, Zhang H, Li S
Pediatr Cardiol 2020 Mar;41(3):615-623. Epub 2020 Jan 23 doi: 10.1007/s00246-020-02292-4. PMID: 31974717
The Congenital Heart Surgeon's Society Complete Atrioventricular Septal Defect Cohort: Baseline, Preintervention Echocardiographic Characteristics.
Meza JM, Devlin PJ, Overman DM, Gremmels D, Baffa G, Cohen MS, Quartermain MD, Caldarone CA, Pourmoghadam K, DeCampli WM, Fackoury CT, Mertens L
Semin Thorac Cardiovasc Surg 2019 Spring;31(1):80-86. Epub 2018 Feb 8 doi: 10.1053/j.semtcvs.2018.02.004. PMID: 29428621
Mid-term outcomes in unbalanced complete atrioventricular septal defect: role of biventricular conversion from single-ventricle palliation.
Nathan M, Emani S, IJsselhof R, Liu H, Gauvreau K, Del Nido P
Eur J Cardiothorac Surg 2017 Sep 1;52(3):565-572. doi: 10.1093/ejcts/ezx129. PMID: 28521020
Surgical management of complete atrioventricular septal defect with tetralogy of fallot.
Hu R, Zhang H, Xu Z, Liu J, Su Z, Ding W
Ann Thorac Cardiovasc Surg 2014;20(5):341-6. Epub 2013 Oct 3 doi: 10.5761/atcs.oa.12-02198. PMID: 24088923

Therapy

Surgical management of complete atrioventricular septal defect with tetralogy of fallot.
Hu R, Zhang H, Xu Z, Liu J, Su Z, Ding W
Ann Thorac Cardiovasc Surg 2014;20(5):341-6. Epub 2013 Oct 3 doi: 10.5761/atcs.oa.12-02198. PMID: 24088923
Impact of pharmacotherapy on interstage outcomes in single ventricle infants.
Moffett BS, Mattamal R, Ocampo EC, Petit CJ
Congenit Heart Dis 2011 Jul-Aug;6(4):286-93. Epub 2011 Jun 22 doi: 10.1111/j.1747-0803.2011.00536.x. PMID: 21696551
Complete atrioventricular septal defect: outcome of pulmonary artery banding improved by adjustable device.
Dhannapuneni RR, Gladman G, Kerr S, Venugopal P, Alphonso N, Corno AF
J Thorac Cardiovasc Surg 2011 Jan;141(1):179-82. Epub 2010 Jul 2 doi: 10.1016/j.jtcvs.2010.03.047. PMID: 20598323
Remote control of pulmonary blood flow: a dream comes true.
Corno AF, Sekarski N, von Segesser LK
Swiss Med Wkly 2002 Jul 27;132(29-30):423-4. doi: 10.4414/smw.2002.10088. PMID: 12428188

Prognosis

Modified Single Repair Technique for Complete Atrioventricular Septal Defect: A Propensity Score Matching Analysis.
Wang G, Ma K, Pang K, Hua Z, Zhang S, Qi L, Yang Y, Feng Z, Mao F, Zhang H, Li S
Pediatr Cardiol 2020 Mar;41(3):615-623. Epub 2020 Jan 23 doi: 10.1007/s00246-020-02292-4. PMID: 31974717
The Congenital Heart Surgeon's Society Complete Atrioventricular Septal Defect Cohort: Baseline, Preintervention Echocardiographic Characteristics.
Meza JM, Devlin PJ, Overman DM, Gremmels D, Baffa G, Cohen MS, Quartermain MD, Caldarone CA, Pourmoghadam K, DeCampli WM, Fackoury CT, Mertens L
Semin Thorac Cardiovasc Surg 2019 Spring;31(1):80-86. Epub 2018 Feb 8 doi: 10.1053/j.semtcvs.2018.02.004. PMID: 29428621
Mid-term outcomes in unbalanced complete atrioventricular septal defect: role of biventricular conversion from single-ventricle palliation.
Nathan M, Emani S, IJsselhof R, Liu H, Gauvreau K, Del Nido P
Eur J Cardiothorac Surg 2017 Sep 1;52(3):565-572. doi: 10.1093/ejcts/ezx129. PMID: 28521020
Surgical management of complete atrioventricular septal defect with tetralogy of fallot.
Hu R, Zhang H, Xu Z, Liu J, Su Z, Ding W
Ann Thorac Cardiovasc Surg 2014;20(5):341-6. Epub 2013 Oct 3 doi: 10.5761/atcs.oa.12-02198. PMID: 24088923
Complete atrioventricular septal defect: outcome of pulmonary artery banding improved by adjustable device.
Dhannapuneni RR, Gladman G, Kerr S, Venugopal P, Alphonso N, Corno AF
J Thorac Cardiovasc Surg 2011 Jan;141(1):179-82. Epub 2010 Jul 2 doi: 10.1016/j.jtcvs.2010.03.047. PMID: 20598323

Clinical prediction guides

Cardiac magnetic resonance predictors for successful primary biventricular repair of unbalanced complete common atrioventricular canal.
Jones AL, White BR, Ghosh RM, Mondal A, Ampah S, Ho DY, Whitehead K, Harris MA, Biko DM, Partington S, Fuller S, Cohen MS, Fogel MA
Cardiol Young 2024 Feb;34(2):387-394. Epub 2023 Jul 18 doi: 10.1017/S1047951123001786. PMID: 37462049Free PMC Article
Common arterial trunk in functionally univentricular hearts: a case series.
Elhedai H, Yong S, Chaudhari M, Botha P, Miller P, Stumper O
Cardiol Young 2023 Jul;33(7):1097-1101. Epub 2022 Jul 11 doi: 10.1017/S1047951122002128. PMID: 35815558
Modified Single Repair Technique for Complete Atrioventricular Septal Defect: A Propensity Score Matching Analysis.
Wang G, Ma K, Pang K, Hua Z, Zhang S, Qi L, Yang Y, Feng Z, Mao F, Zhang H, Li S
Pediatr Cardiol 2020 Mar;41(3):615-623. Epub 2020 Jan 23 doi: 10.1007/s00246-020-02292-4. PMID: 31974717
The Congenital Heart Surgeon's Society Complete Atrioventricular Septal Defect Cohort: Baseline, Preintervention Echocardiographic Characteristics.
Meza JM, Devlin PJ, Overman DM, Gremmels D, Baffa G, Cohen MS, Quartermain MD, Caldarone CA, Pourmoghadam K, DeCampli WM, Fackoury CT, Mertens L
Semin Thorac Cardiovasc Surg 2019 Spring;31(1):80-86. Epub 2018 Feb 8 doi: 10.1053/j.semtcvs.2018.02.004. PMID: 29428621
Impact of pharmacotherapy on interstage outcomes in single ventricle infants.
Moffett BS, Mattamal R, Ocampo EC, Petit CJ
Congenit Heart Dis 2011 Jul-Aug;6(4):286-93. Epub 2011 Jun 22 doi: 10.1111/j.1747-0803.2011.00536.x. PMID: 21696551

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