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Phacoanaphylactic uveitis

MedGen UID:
731803
Concept ID:
C1444621
Disease or Syndrome
Synonyms: Endophthalmitis phacoanaphylactica; endophthalmitis phacoanaphylactica; Lens-associated uveitis; Lens-induced endophthalmitis; lens-induced endophthalmitis; Lens-induced iridocyclitis; lens-induced iridocyclitis; Lens-induced uveitis; lens-induced uveitis; Phacoallergic endophthalmitis; phacoanaphylactic uveitis; Phacoantigenic endophthalmitis; Phacoantigenic uveitis; Phacogenic uveitis; Phacotoxic uveitis; Phako-anaphylactic endophthalmitis
SNOMED CT: Lens-induced uveitis (410494003); Phacogenic uveitis (410494003); Lens-associated uveitis (410494003); Phacoantigenic uveitis (410494003); Phacotoxic uveitis (410494003)
Modes of inheritance:
Not genetically inherited
MedGen UID:
988794
Concept ID:
CN307044
Finding
Source: Orphanet
clinical entity without genetic inheritance.
 
Monarch Initiative: MONDO:0016207
Orphanet: ORPHA209959

Definition

A rare ophthalmic disorder characterized by a zonal granulomatous inflammatory reaction centered around the lens secondary to its traumatic rupture. Signs and symptoms include photophobia, ocular irritation or pain, blurred vision, redness, mutton-fat keratic precipitates, posterior synechiae, and sometimes hypopyon. Intraocular pressure may be elevated due to blockage of the trabecular meshwork by inflammatory cells or lens material. [from ORDO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPhacoanaphylactic uveitis

Recent clinical studies

Etiology

Zagórski Z
Lens Eye Toxic Res 1991;8(2-3):311-8. PMID: 1911642

Diagnosis

Abrahams IW
J Am Intraocul Implant Soc 1985 Sep;11(5):444-7. doi: 10.1016/s0146-2776(85)80080-x. PMID: 4044382

Therapy

Abrahams IW
J Am Intraocul Implant Soc 1985 Sep;11(5):444-7. doi: 10.1016/s0146-2776(85)80080-x. PMID: 4044382
Wolter JR
Graefes Arch Clin Exp Ophthalmol 1983;220(4):160-6. doi: 10.1007/BF02186661. PMID: 6604000

Clinical prediction guides

Zagórski Z
Lens Eye Toxic Res 1991;8(2-3):311-8. PMID: 1911642
Jain IS, Gupta A, Gangwar DN, Dhir SP
Ann Ophthalmol 1983 Jul;15(7):640-2. PMID: 6571349

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