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Neurothekeoma

MedGen UID:
64641
•Concept ID:
C0206730
•
Neoplastic Process
Synonyms: Myxoma, Nerve Sheath; Myxomas, Nerve Sheath; Nerve Sheath Myxoma; Nerve Sheath Myxomas; Neurotheceoma; Neurotheceomas; Neurothecoma; Neurothecomas; Neurothekeomas
SNOMED CT: Neurothekeoma (51836001); Nerve sheath myxoma (51836001)
 
Monarch Initiative: MONDO:0006317

Definition

A benign neoplasm arising from nerve sheaths. It is characterized by the presence of a myxoid stroma. [from NCI]

Recent clinical studies

Therapy

Fibrous and fibrohistiocytic neoplasms: an update.
Clarke LE
Dermatol Clin 2012 Oct;30(4):643-56, vi. Epub 2012 Aug 11 doi: 10.1016/j.det.2012.06.005. PMID: 23021051
Atypical cellular neurothekeoma--a diagnosis to be aware of.
Wilson AD, Rigby H, Orlando A
J Plast Reconstr Aesthet Surg 2008;61(2):186-8. Epub 2007 Aug 20 doi: 10.1016/j.bjps.2007.01.078. PMID: 17709307
Right ventricular nerve sheath tumour and patent foramen ovale presenting with transient ischemic attack.
Sharif MN, Schwarz D, Cujec B, Radhi J, Thomson D
Can J Cardiol 1996 Sep;12(9):789-91. PMID: 8842130

Prognosis

Cellular neurothekeoma occurring at the site of radiation therapy in a child with medulloblastoma.
Zhao Z, Koh MJA
Pediatr Dermatol 2022 May;39(3):488-490. Epub 2022 Feb 17 doi: 10.1111/pde.14941. PMID: 35178793
Peripheral Nerve Sheath Tumors of Head and Neck: Imaging-Based Review of World Health Organization Classification.
Abdel Razek AAK, Gamaleldin OA, Elsebaie NA
J Comput Assist Tomogr 2020 Nov/Dec;44(6):928-940. doi: 10.1097/RCT.0000000000001109. PMID: 33196600
Neurothekeoma of the toe.
Wiemeyer S, Hafer G
Foot Ankle Spec 2013 Dec;6(6):479-81. Epub 2013 Oct 9 doi: 10.1177/1938640013507106. PMID: 24107319
Fibrous and fibrohistiocytic neoplasms: an update.
Clarke LE
Dermatol Clin 2012 Oct;30(4):643-56, vi. Epub 2012 Aug 11 doi: 10.1016/j.det.2012.06.005. PMID: 23021051
New entities in cutaneous soft tissue tumours.
Calonje E, Fletcher CD
Pathologica 1993 Jan-Feb;85(1095):1-15. PMID: 8390634

Clinical prediction guides

Multiple myxoid cellular neurothekeomas in a patient with systemic lupus erythematosus.
Lau SK, Cassarino DS, Koh SS
J Cutan Pathol 2021 Jul;48(7):980-985. Epub 2021 May 9 doi: 10.1111/cup.14025. PMID: 33844324
Peripheral Nerve Sheath Tumors of Head and Neck: Imaging-Based Review of World Health Organization Classification.
Abdel Razek AAK, Gamaleldin OA, Elsebaie NA
J Comput Assist Tomogr 2020 Nov/Dec;44(6):928-940. doi: 10.1097/RCT.0000000000001109. PMID: 33196600
Neurothekeoma of the toe.
Wiemeyer S, Hafer G
Foot Ankle Spec 2013 Dec;6(6):479-81. Epub 2013 Oct 9 doi: 10.1177/1938640013507106. PMID: 24107319
Cellular neurothekeoma with neuroendocrine differentiation.
D'Antonio A, Cuomo R, Angrisani B, Addesso M, Angrisani P
Dermatol Online J 2011 Apr 15;17(4):2. PMID: 21549077
Studies on the cellular origin of neurothekeoma: clinical, light microscopic, immunohistochemical, and ultrastructural observations.
Barnhill RL, Dickersin GR, Nickeleit V, Bhan AK, Muhlbauer JE, Phillips ME, Mihm MC Jr
J Am Acad Dermatol 1991 Jul;25(1 Pt 1):80-8. doi: 10.1016/0190-9622(91)70177-4. PMID: 1880258

Recent systematic reviews

Pediatric cellular neurothekeoma: Seven cases and systematic review of the literature.
Murphrey M, Huy Nguyen A, White KP, Krol A, Bernert R, Yarbrough K
Pediatr Dermatol 2020 Mar;37(2):320-325. Epub 2020 Jan 12 doi: 10.1111/pde.14043. PMID: 31930561
Intraoral nerve sheath myxoma: case report and systematic review of the literature.
Rozza-de-Menezes RE, Andrade RM, Israel MS, Gonçalves Cunha KS
Head Neck 2013 Dec;35(12):E397-404. Epub 2013 Jul 30 doi: 10.1002/hed.23361. PMID: 23616426

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