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Anomalous origin of left pulmonary artery from ascending aorta

MedGen UID:
576708
•Concept ID:
C0345040
•
Congenital Abnormality
Synonyms: Hemitruncus to left; Left hemitruncus; Origin of left pulmonary artery from ascending aorta
SNOMED CT: Anomalous origin of left pulmonary artery from ascending aorta (253637002); Origin of left pulmonary artery from ascending aorta (253637002); Hemitruncus to left (253637002); Left hemitruncus (253637002)
 
HPO: HP:0011661

Definition

The left pulmonary artery originates from the ascending aorta in the presence of a pulmonary valve and main pulmonary artery. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAnomalous origin of left pulmonary artery from ascending aorta

Professional guidelines

PubMed

Prenatal diagnosis of anomalous origin of one pulmonary artery branch by two-dimensional echocardiography: summary of 12 cases.
Wenxiu L, Yuan Z, Chaoning H, Bin G, Jiang W, Shuang Y
Cardiol Young 2020 Jan;30(1):39-46. Epub 2019 Dec 17 doi: 10.1017/S1047951119002890. PMID: 31845638
Prenatal diagnosis of anomalous origin of pulmonary artery.
Li X, Mu Z, Li X, Weng Z
Prenat Diagn 2018 Apr;38(5):310-317. Epub 2018 Mar 23 doi: 10.1002/pd.5235. PMID: 29451683
Utility and importance of new echocardiographic screening methods in diagnosis of anomalous coronary origins in the pediatric population: assessment of quality improvement.
Thankavel PP, Lemler MS, Ramaciotti C
Pediatr Cardiol 2015 Jan;36(1):120-5. Epub 2014 Aug 2 doi: 10.1007/s00246-014-0973-8. PMID: 25085263

Recent clinical studies

Etiology

Coronary unroofing does not fits all anomalous aortic origin of coronary arteries.
Arcieri L, Colaneri M, Bianco F, Merlino E, Santoro G, Silvano R, Baldinelli A, Pozzi M
J Card Surg 2022 Nov;37(11):3536-3542. Epub 2022 Aug 21 doi: 10.1111/jocs.16876. PMID: 35989538
Anomalous origin of one pulmonary artery from aorta: Evaluation on computed tomography angiography.
Verma M, Pandey NN, Ramakrishnan S, Jagia P
J Card Surg 2022 Mar;37(3):483-491. Epub 2022 Jan 11 doi: 10.1111/jocs.16229. PMID: 35018673
Congenital abnormalities of the aortic arch: revisiting the 1964 Stewart classification.
Li S, Wen H, Liang M, Luo D, Qin Y, Liao Y, Ouyang S, Bi J, Tian X, Norwitz ER, Luo G
Cardiovasc Pathol 2019 Mar-Apr;39:38-50. Epub 2018 Dec 6 doi: 10.1016/j.carpath.2018.11.004. PMID: 30623879
Prenatal diagnosis of anomalous origin of pulmonary artery.
Li X, Mu Z, Li X, Weng Z
Prenat Diagn 2018 Apr;38(5):310-317. Epub 2018 Mar 23 doi: 10.1002/pd.5235. PMID: 29451683
Anomalous origin of the right pulmonary artery from the ascending aorta.
Prifti E, Bonacchi M, Murzi B, Crucean A, Leacche M, Bernabei M, Bartolozzi F, Nathan NS, Vanini V
J Card Surg 2004 Mar-Apr;19(2):103-12. doi: 10.1111/j.0886-0440.2004.04023.x. PMID: 15016045

Diagnosis

Anomalous origin of one pulmonary artery from aorta: Evaluation on computed tomography angiography.
Verma M, Pandey NN, Ramakrishnan S, Jagia P
J Card Surg 2022 Mar;37(3):483-491. Epub 2022 Jan 11 doi: 10.1111/jocs.16229. PMID: 35018673
Anomalous origin of left pulmonary artery from the ascending aorta: echocardiography assessment.
Atmani S, Bendris I
Cardiol Young 2020 Jan;30(1):145-147. Epub 2019 Dec 16 doi: 10.1017/S1047951119002804. PMID: 31840626
Prenatal diagnosis of anomalous origin of pulmonary artery.
Li X, Mu Z, Li X, Weng Z
Prenat Diagn 2018 Apr;38(5):310-317. Epub 2018 Mar 23 doi: 10.1002/pd.5235. PMID: 29451683
Diagnosis and prognosis of anomalous origin of the left coronary artery from the pulmonary artery.
Holst LM, Helvind M, Andersen HØ
Dan Med J 2015 Sep;62(9) PMID: 26324080
Pulmonary sequestration.
O'Mara CS, Baker RR, Jeyasingham K
Surg Gynecol Obstet 1978 Oct;147(4):609-16. PMID: 360452

Therapy

Surgical Results of Anomalous Origin of One Pulmonary Artery Branch from the Ascending Aorta.
Cho S, Kim WH, Choi ES, Lee JR, Kim YJ
Pediatr Cardiol 2015 Oct;36(7):1532-8. Epub 2015 May 27 doi: 10.1007/s00246-015-1197-2. PMID: 26008763
Abnormal origins of the coronary arteries from the aortic root.
Hoffman JI
Cardiol Young 2014 Oct;24(5):774-91. Epub 2014 Apr 23 doi: 10.1017/S1047951114000250. PMID: 24758740
Repair of anomalous origin of the left coronary artery from the pulmonary artery in infants.
Kazmierczak PA, Ostrowska K, Dryzek P, Moll JA, Moll JJ
Interact Cardiovasc Thorac Surg 2013 Jun;16(6):797-801. Epub 2013 Feb 26 doi: 10.1093/icvts/ivt061. PMID: 23442939Free PMC Article
The anomalous origin of the branch pulmonary artery from the ascending aorta.
Garg P, Talwar S, Kothari SS, Saxena A, Juneja R, Choudhary SK, Airan B
Interact Cardiovasc Thorac Surg 2012 Jul;15(1):86-92. Epub 2012 Mar 30 doi: 10.1093/icvts/ivs110. PMID: 22467006Free PMC Article
Anomalous origin of the left pulmonary artery from the aorta. Our experience and literature review.
Prifti E, Bonacchi M, Murzi B, Crucean A, Bernabei M, Luisi VS, Bartolozzi F, Vanini V
Heart Vessels 2003 May;18(2):79-84. doi: 10.1007/s10380-002-0684-7. PMID: 12756604

Prognosis

Coronary unroofing does not fits all anomalous aortic origin of coronary arteries.
Arcieri L, Colaneri M, Bianco F, Merlino E, Santoro G, Silvano R, Baldinelli A, Pozzi M
J Card Surg 2022 Nov;37(11):3536-3542. Epub 2022 Aug 21 doi: 10.1111/jocs.16876. PMID: 35989538
Anomalous origin of left pulmonary artery from the ascending aorta: echocardiography assessment.
Atmani S, Bendris I
Cardiol Young 2020 Jan;30(1):145-147. Epub 2019 Dec 16 doi: 10.1017/S1047951119002804. PMID: 31840626
Diagnosis and prognosis of anomalous origin of the left coronary artery from the pulmonary artery.
Holst LM, Helvind M, Andersen HØ
Dan Med J 2015 Sep;62(9) PMID: 26324080
Abnormal origins of the coronary arteries from the aortic root.
Hoffman JI
Cardiol Young 2014 Oct;24(5):774-91. Epub 2014 Apr 23 doi: 10.1017/S1047951114000250. PMID: 24758740
Anomalous origin of the right pulmonary artery from the ascending aorta.
Prifti E, Bonacchi M, Murzi B, Crucean A, Leacche M, Bernabei M, Bartolozzi F, Nathan NS, Vanini V
J Card Surg 2004 Mar-Apr;19(2):103-12. doi: 10.1111/j.0886-0440.2004.04023.x. PMID: 15016045

Clinical prediction guides

Surgical repair of the anomalous aortic origin of the coronary arteries: a single-center experience.
Cicek M, Onalan MA, Ilker Y, Ozkok S, Ozdemir F, Yurdakok O, Aydemir NA, Sasmazel A
Cardiol Young 2023 Sep;33(9):1700-1705. Epub 2023 Apr 13 doi: 10.1017/S1047951123000860. PMID: 37045608
Coronary unroofing does not fits all anomalous aortic origin of coronary arteries.
Arcieri L, Colaneri M, Bianco F, Merlino E, Santoro G, Silvano R, Baldinelli A, Pozzi M
J Card Surg 2022 Nov;37(11):3536-3542. Epub 2022 Aug 21 doi: 10.1111/jocs.16876. PMID: 35989538
Anomalous origin of one pulmonary artery from aorta: Evaluation on computed tomography angiography.
Verma M, Pandey NN, Ramakrishnan S, Jagia P
J Card Surg 2022 Mar;37(3):483-491. Epub 2022 Jan 11 doi: 10.1111/jocs.16229. PMID: 35018673
Congenital abnormalities of the aortic arch: revisiting the 1964 Stewart classification.
Li S, Wen H, Liang M, Luo D, Qin Y, Liao Y, Ouyang S, Bi J, Tian X, Norwitz ER, Luo G
Cardiovasc Pathol 2019 Mar-Apr;39:38-50. Epub 2018 Dec 6 doi: 10.1016/j.carpath.2018.11.004. PMID: 30623879
Repair of anomalous coronary artery from the pulmonary artery: A-signal center 20-year experience.
Qiu J, Li S, Yan J, Wang Q, Song Y, Sun H, Li D
Int J Cardiol 2016 Nov 15;223:625-629. Epub 2016 Aug 13 doi: 10.1016/j.ijcard.2016.08.221. PMID: 27565839

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