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Biliary cystadenocarcinoma

MedGen UID:
473526
Concept ID:
C2064409
Neoplastic Process
Synonyms: biliary cystadenocarcinoma; Intrahepatic Bile Duct Cystadenocarcinoma; Intrahepatic bile duct cystadenocarcinoma; intrahepatic bile duct cystadenocarcinoma; Intrahepatic Bile Duct MCN with an Associated Invasive Carcinoma; Intrahepatic Bile Duct Mucinous Cystic Neoplasm with an Associated Invasive Carcinoma
Modes of inheritance:
Not genetically inherited
MedGen UID:
988794
Concept ID:
CN307044
Finding
Source: Orphanet
clinical entity without genetic inheritance.
 
Monarch Initiative: MONDO:0018535
Orphanet: ORPHA424982

Definition

A mucinous cystic neoplasm that arises from the intrahepatic bile ducts and it is associated with an invasive carcinomatous component. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVBiliary cystadenocarcinoma

Professional guidelines

PubMed

Zhang FB, Zhang AM, Zhang ZB, Huang X, Wang XT, Dong JH
World J Gastroenterol 2014 Sep 21;20(35):12595-601. doi: 10.3748/wjg.v20.i35.12595. PMID: 25253963Free PMC Article
Thomas KT, Welch D, Trueblood A, Sulur P, Wise P, Gorden DL, Chari RS, Wright JK Jr, Washington K, Pinson CW
Ann Surg 2005 May;241(5):769-73; discussion 773-5. doi: 10.1097/01.sla.0000161982.57360.1b. PMID: 15849512Free PMC Article
Lee WJ, Lim HK, Jang KM, Kim SH, Lee SJ, Lim JH, Choo IW
Radiographics 2001 Oct;21 Spec No:S97-S116. doi: 10.1148/radiographics.21.suppl_1.g01oc12s97. PMID: 11598251

Recent clinical studies

Etiology

El-Magd EA, El-Shobari M, Abdelsalam RA, Abbas A, Elmahdy Y, Hamed H
Langenbecks Arch Surg 2023 Jul 11;408(1):273. doi: 10.1007/s00423-023-02994-2. PMID: 37430153Free PMC Article
McIntyre CA, Girshman J, Goldman DA, Gonen M, Soares KC, Wei AC, Balachandran VP, Kingham TP, Drebin JA, Jarnagin WR, Gluskin JS, D'Angelica MI, Gerst SR
Abdom Radiol (NY) 2022 Apr;47(4):1333-1340. Epub 2022 Feb 21 doi: 10.1007/s00261-022-03436-1. PMID: 35188592Free PMC Article
Wang C, Miao R, Liu H, Du X, Liu L, Lu X, Zhao H
Dig Liver Dis 2012 May;44(5):426-31. Epub 2011 Dec 9 doi: 10.1016/j.dld.2011.11.007. PMID: 22169273
Pojchamarnwiputh S, Na Chiangmai W, Chotirosniramit A, Lertprasertsuke N
Singapore Med J 2008 May;49(5):392-6. PMID: 18465049
Kimura H, Kagawa K, Deguchi T, Sumida Y, You K, Komaki T, Teramae N, Fukui S, Kawakami S, Fujita Y
J Gastroenterol 1998 Dec;33(6):895-8. doi: 10.1007/s005350050196. PMID: 9853568

Diagnosis

McIntyre CA, Girshman J, Goldman DA, Gonen M, Soares KC, Wei AC, Balachandran VP, Kingham TP, Drebin JA, Jarnagin WR, Gluskin JS, D'Angelica MI, Gerst SR
Abdom Radiol (NY) 2022 Apr;47(4):1333-1340. Epub 2022 Feb 21 doi: 10.1007/s00261-022-03436-1. PMID: 35188592Free PMC Article
Psaltis E, Prescott R, Chang D, Lapsia S
Br J Hosp Med (Lond) 2012 Oct;73(10):590-1. doi: 10.12968/hmed.2012.73.10.590. PMID: 23124292
Seo DW, Kang GH
Gastrointest Endosc 2000 Jan;51(1):66. doi: 10.1016/s0016-5107(00)70139-8. PMID: 10625799
Fernandez MP, Redvanly RD
Radiol Clin North Am 1998 Mar;36(2):333-48. doi: 10.1016/s0033-8389(05)70026-9. PMID: 9520986
Suh JI, Kim JH, Lee DJ, Kim KY, Park CW, Kim TN, Chung MK
Korean J Intern Med 1997 Jan;12(1):109-13. doi: 10.3904/kjim.1997.12.1.109. PMID: 9159050Free PMC Article

Therapy

Kodama R, Saegusa H, Ushimaru H, Ikeno T, Makino M, Kawaguchi K
Clin J Gastroenterol 2015 Oct;8(5):335-9. Epub 2015 Sep 28 doi: 10.1007/s12328-015-0607-6. PMID: 26412329
Yuefeng M, Weili F, Jing L, Wenxiang T, Tianqing L, Liming W
Turk J Gastroenterol 2012;23(6):795-8. doi: 10.4318/tjg.2012.0644. PMID: 23864459
Gómez-Martín C, Rodríguez A, Malón D, Cortés-Funes H
Clin Transl Oncol 2010 Mar;12(3):234-7. doi: 10.1007/s12094-010-0495-7. PMID: 20231130
Park JH, Oh JH, Yoon Y, Hong SH, Park SJ
J Vasc Interv Radiol 2005 Jun;16(6):885-8. doi: 10.1097/01.RVI.0000157778.48280.AD. PMID: 15947055
Murakami Y, Kanehiro T, Yokoyama Y, Uemura K, Sasaki M, Morifuji M, Hayashidani Y, Sudo T, Sueda T
Surgery 2005 May;137(5):577-9. doi: 10.1016/j.surg.2003.12.006. PMID: 15855934

Prognosis

Aziz H, Hamad A, Afyouni S, Kamel IR, Pawlik TM
J Gastrointest Surg 2023 Sep;27(9):1963-1970. Epub 2023 May 23 doi: 10.1007/s11605-023-05709-6. PMID: 37221388
Yamada S, Kato Y, Hada M, Kotake M, Oyama K, Hara T
Clin J Gastroenterol 2017 Dec;10(6):530-534. Epub 2017 Sep 14 doi: 10.1007/s12328-017-0775-7. PMID: 28913716
Psaltis E, Prescott R, Chang D, Lapsia S
Br J Hosp Med (Lond) 2012 Oct;73(10):590-1. doi: 10.12968/hmed.2012.73.10.590. PMID: 23124292
Facy O, Rode A, Mabrut JY
J Visc Surg 2012 Dec;149(6):423-5. Epub 2012 Jul 25 doi: 10.1016/j.jviscsurg.2012.06.007. PMID: 22841283
Kimura H, Kagawa K, Deguchi T, Sumida Y, You K, Komaki T, Teramae N, Fukui S, Kawakami S, Fujita Y
J Gastroenterol 1998 Dec;33(6):895-8. doi: 10.1007/s005350050196. PMID: 9853568

Clinical prediction guides

El-Magd EA, El-Shobari M, Abdelsalam RA, Abbas A, Elmahdy Y, Hamed H
Langenbecks Arch Surg 2023 Jul 11;408(1):273. doi: 10.1007/s00423-023-02994-2. PMID: 37430153Free PMC Article
Kodama R, Saegusa H, Ushimaru H, Ikeno T, Makino M, Kawaguchi K
Clin J Gastroenterol 2015 Oct;8(5):335-9. Epub 2015 Sep 28 doi: 10.1007/s12328-015-0607-6. PMID: 26412329
Zhang FB, Zhang AM, Zhang ZB, Huang X, Wang XT, Dong JH
World J Gastroenterol 2014 Sep 21;20(35):12595-601. doi: 10.3748/wjg.v20.i35.12595. PMID: 25253963Free PMC Article
Wang C, Miao R, Liu H, Du X, Liu L, Lu X, Zhao H
Dig Liver Dis 2012 May;44(5):426-31. Epub 2011 Dec 9 doi: 10.1016/j.dld.2011.11.007. PMID: 22169273
Kurashina M, Kozuka S, Nakasima N, Hirabayasi N, Ito M
Cancer 1988 Jun 15;61(12):2469-74. doi: 10.1002/1097-0142(19880615)61:12<2469::aid-cncr2820611214>3.0.co;2-y. PMID: 2835143

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