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Benign peripheral nerve sheath tumor

MedGen UID:
1843306
Concept ID:
C5577926
Neoplastic Process
Synonyms: benign peripheral nerve sheath tumor; BPNST
 
Monarch Initiative: MONDO:0016752
Orphanet: ORPHA252131

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVBenign peripheral nerve sheath tumor

Professional guidelines

PubMed

Ferner RE, Gutmann DH
Handb Clin Neurol 2013;115:939-55. doi: 10.1016/B978-0-444-52902-2.00053-9. PMID: 23931823

Recent clinical studies

Etiology

Kresbach C, Dottermusch M, Eckhardt A, Ristow I, Paplomatas P, Altendorf L, Wefers AK, Bockmayr M, Belakhoua S, Tran I, Pohl L, Neyazi S, Bode H, Farschtschi S, Well L, Friedrich RE, Reuss D, Snuderl M, Hagel C, Mautner VF, Schüller U
Neuro Oncol 2023 Sep 5;25(9):1644-1655. doi: 10.1093/neuonc/noad053. PMID: 36866403Free PMC Article
Lee SK, Kim JY, Jeong HS
PLoS One 2020;15(3):e0230816. Epub 2020 Mar 26 doi: 10.1371/journal.pone.0230816. PMID: 32214392Free PMC Article
Stone JJ, Boland JM, Spinner RJ
World Neurosurg 2018 Nov;119:e986-e990. Epub 2018 Aug 13 doi: 10.1016/j.wneu.2018.08.022. PMID: 30114537
Guha D, Davidson B, Nadi M, Alotaibi NM, Fehlings MG, Gentili F, Valiante TA, Tator CH, Tymianski M, Guha A, Zadeh G
J Neurosurg 2018 Apr;128(4):1226-1234. Epub 2017 Jul 7 doi: 10.3171/2017.1.JNS162292. PMID: 28686119
James AW, Shurell E, Singh A, Dry SM, Eilber FC
Surg Oncol Clin N Am 2016 Oct;25(4):789-802. doi: 10.1016/j.soc.2016.05.009. PMID: 27591499

Diagnosis

Uerschels AK, Dengler NF, Chihi M, Lenkeit A, Dinger TF, Jabbarli R, Sure U, Hagenacker T, Wrede KH, Gembruch O
Neurosurg Rev 2023 Aug 18;46(1):205. doi: 10.1007/s10143-023-02107-z. PMID: 37594583Free PMC Article
Colizza A, Covello R, Greco A, Ralli M, Coppola G, Gilardi A, Riminucci M, de Vincentiis M, Corsi A
Ear Nose Throat J 2023 Sep;102(9):NP436-NP439. Epub 2021 Jun 1 doi: 10.1177/01455613211020539. PMID: 34074156
Larque AB, Bredella MA, Nielsen GP, Chebib I
Skeletal Radiol 2017 Nov;46(11):1463-1468. Epub 2017 Jul 8 doi: 10.1007/s00256-017-2710-x. PMID: 28689338
James AW, Shurell E, Singh A, Dry SM, Eilber FC
Surg Oncol Clin N Am 2016 Oct;25(4):789-802. doi: 10.1016/j.soc.2016.05.009. PMID: 27591499
Ferner RE, Gutmann DH
Handb Clin Neurol 2013;115:939-55. doi: 10.1016/B978-0-444-52902-2.00053-9. PMID: 23931823

Therapy

Jain PV, Squires C, Gasparri M, Sheinin Y
Ann Diagn Pathol 2022 Apr;57:151880. Epub 2021 Dec 27 doi: 10.1016/j.anndiagpath.2021.151880. PMID: 34972037
Las Heras F, Martuza R, Caruso P, Rincon S, Stemmer-Rachamimov A
Brain Pathol 2013 May;23(3):361-2. doi: 10.1111/bpa.12055. PMID: 23587143Free PMC Article

Prognosis

Doğukan FM, Erdem ZB
Int J Surg Pathol 2023 Oct;31(7):1225-1231. Epub 2022 Dec 7 doi: 10.1177/10668969221143456. PMID: 36475929
Martin E, Geitenbeek RTJ, Coert JH, Hanff DF, Graven LH, Grünhagen DJ, Verhoef C, Taal W
Neuro Oncol 2021 Apr 12;23(4):557-571. doi: 10.1093/neuonc/noaa280. PMID: 33326583Free PMC Article
Guha D, Davidson B, Nadi M, Alotaibi NM, Fehlings MG, Gentili F, Valiante TA, Tator CH, Tymianski M, Guha A, Zadeh G
J Neurosurg 2018 Apr;128(4):1226-1234. Epub 2017 Jul 7 doi: 10.3171/2017.1.JNS162292. PMID: 28686119
Yu YH, Wu JT, Ye J, Chen MX
World J Surg Oncol 2016 May 10;14:142. doi: 10.1186/s12957-016-0899-0. PMID: 27159980Free PMC Article
Pekmezci M, Reuss DE, Hirbe AC, Dahiya S, Gutmann DH, von Deimling A, Horvai AE, Perry A
Mod Pathol 2015 Feb;28(2):187-200. Epub 2014 Sep 5 doi: 10.1038/modpathol.2014.109. PMID: 25189642Free PMC Article

Clinical prediction guides

Doğukan FM, Erdem ZB
Int J Surg Pathol 2023 Oct;31(7):1225-1231. Epub 2022 Dec 7 doi: 10.1177/10668969221143456. PMID: 36475929
Lee SK, Kim JY, Jeong HS
PLoS One 2020;15(3):e0230816. Epub 2020 Mar 26 doi: 10.1371/journal.pone.0230816. PMID: 32214392Free PMC Article
Guha D, Davidson B, Nadi M, Alotaibi NM, Fehlings MG, Gentili F, Valiante TA, Tator CH, Tymianski M, Guha A, Zadeh G
J Neurosurg 2018 Apr;128(4):1226-1234. Epub 2017 Jul 7 doi: 10.3171/2017.1.JNS162292. PMID: 28686119
Yu YH, Wu JT, Ye J, Chen MX
World J Surg Oncol 2016 May 10;14:142. doi: 10.1186/s12957-016-0899-0. PMID: 27159980Free PMC Article
Pekmezci M, Reuss DE, Hirbe AC, Dahiya S, Gutmann DH, von Deimling A, Horvai AE, Perry A
Mod Pathol 2015 Feb;28(2):187-200. Epub 2014 Sep 5 doi: 10.1038/modpathol.2014.109. PMID: 25189642Free PMC Article

Recent systematic reviews

Peraza Labrador AJ, Valdez LHM, Marin NRG, Ibazetta KAR, Villacis M, Chacon JL, Huaman HO, Pariahuamán HC, Angulo HB, Woo V
Head Neck Pathol 2023 Dec;17(4):984-999. Epub 2023 Dec 6 doi: 10.1007/s12105-023-01595-1. PMID: 38055108Free PMC Article
Martin E, Geitenbeek RTJ, Coert JH, Hanff DF, Graven LH, Grünhagen DJ, Verhoef C, Taal W
Neuro Oncol 2021 Apr 12;23(4):557-571. doi: 10.1093/neuonc/noaa280. PMID: 33326583Free PMC Article
Boyanton BL Jr, Jones JK, Shenaq SM, Hicks MJ, Bhattacharjee MB
Arch Pathol Lab Med 2007 Sep;131(9):1382-92. doi: 10.5858/2007-131-1382-IPASRW. PMID: 17824794

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