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Disorder of pterin metabolism

MedGen UID:
1843207
Concept ID:
C5681034
Disease or Syndrome
Orphanet: ORPHA309819

Professional guidelines

PubMed

Hendriks E, Rosenberg R, Prine L
Am Fam Physician 2020 May 15;101(10):599-606. PMID: 32412215
Hellmich B, Agueda A, Monti S, Buttgereit F, de Boysson H, Brouwer E, Cassie R, Cid MC, Dasgupta B, Dejaco C, Hatemi G, Hollinger N, Mahr A, Mollan SP, Mukhtyar C, Ponte C, Salvarani C, Sivakumar R, Tian X, Tomasson G, Turesson C, Schmidt W, Villiger PM, Watts R, Young C, Luqmani RA
Ann Rheum Dis 2020 Jan;79(1):19-30. Epub 2019 Jul 3 doi: 10.1136/annrheumdis-2019-215672. PMID: 31270110
Devalia V, Hamilton MS, Molloy AM; British Committee for Standards in Haematology
Br J Haematol 2014 Aug;166(4):496-513. Epub 2014 Jun 18 doi: 10.1111/bjh.12959. PMID: 24942828

Recent clinical studies

Etiology

Green R, Miller JW
Vitam Horm 2022;119:405-439. Epub 2022 Mar 11 doi: 10.1016/bs.vh.2022.02.003. PMID: 35337628
Shulpekova Y, Nechaev V, Kardasheva S, Sedova A, Kurbatova A, Bueverova E, Kopylov A, Malsagova K, Dlamini JC, Ivashkin V
Molecules 2021 Jun 18;26(12) doi: 10.3390/molecules26123731. PMID: 34207319Free PMC Article
van Gool JD, Hirche H, Lax H, De Schaepdrijver L
Reprod Toxicol 2018 Sep;80:73-84. Epub 2018 May 16 doi: 10.1016/j.reprotox.2018.05.004. PMID: 29777755
Ebara S
Congenit Anom (Kyoto) 2017 Sep;57(5):138-141. Epub 2017 Jul 25 doi: 10.1111/cga.12233. PMID: 28603928
Scaglione F, Panzavolta G
Xenobiotica 2014 May;44(5):480-8. Epub 2014 Feb 4 doi: 10.3109/00498254.2013.845705. PMID: 24494987

Diagnosis

Sahu P, Thippeswamy H, Chaturvedi SK
Vitam Horm 2022;119:457-470. Epub 2022 Mar 3 doi: 10.1016/bs.vh.2022.01.001. PMID: 35337631
Green R, Miller JW
Vitam Horm 2022;119:405-439. Epub 2022 Mar 11 doi: 10.1016/bs.vh.2022.02.003. PMID: 35337628
Opladen T, López-Laso E, Cortès-Saladelafont E, Pearson TS, Sivri HS, Yildiz Y, Assmann B, Kurian MA, Leuzzi V, Heales S, Pope S, Porta F, García-Cazorla A, Honzík T, Pons R, Regal L, Goez H, Artuch R, Hoffmann GF, Horvath G, Thöny B, Scholl-Bürgi S, Burlina A, Verbeek MM, Mastrangelo M, Friedman J, Wassenberg T, Jeltsch K, Kulhánek J, Kuseyri Hübschmann O; International Working Group on Neurotransmitter related Disorders (iNTD)
Orphanet J Rare Dis 2020 May 26;15(1):126. doi: 10.1186/s13023-020-01379-8. PMID: 32456656Free PMC Article
Ebara S
Congenit Anom (Kyoto) 2017 Sep;57(5):138-141. Epub 2017 Jul 25 doi: 10.1111/cga.12233. PMID: 28603928
Naviaux RK
Mitochondrion 2014 May;16:7-17. Epub 2013 Aug 24 doi: 10.1016/j.mito.2013.08.006. PMID: 23981537

Therapy

Fardous AM, Heydari AR
Nutrients 2023 Nov 6;15(21) doi: 10.3390/nu15214699. PMID: 37960352Free PMC Article
Opladen T, López-Laso E, Cortès-Saladelafont E, Pearson TS, Sivri HS, Yildiz Y, Assmann B, Kurian MA, Leuzzi V, Heales S, Pope S, Porta F, García-Cazorla A, Honzík T, Pons R, Regal L, Goez H, Artuch R, Hoffmann GF, Horvath G, Thöny B, Scholl-Bürgi S, Burlina A, Verbeek MM, Mastrangelo M, Friedman J, Wassenberg T, Jeltsch K, Kulhánek J, Kuseyri Hübschmann O; International Working Group on Neurotransmitter related Disorders (iNTD)
Orphanet J Rare Dis 2020 May 26;15(1):126. doi: 10.1186/s13023-020-01379-8. PMID: 32456656Free PMC Article
Bedoui Y, Guillot X, Sélambarom J, Guiraud P, Giry C, Jaffar-Bandjee MC, Ralandison S, Gasque P
Int J Mol Sci 2019 Oct 10;20(20) doi: 10.3390/ijms20205023. PMID: 31658782Free PMC Article
van Gool JD, Hirche H, Lax H, De Schaepdrijver L
Reprod Toxicol 2018 Sep;80:73-84. Epub 2018 May 16 doi: 10.1016/j.reprotox.2018.05.004. PMID: 29777755
Ebara S
Congenit Anom (Kyoto) 2017 Sep;57(5):138-141. Epub 2017 Jul 25 doi: 10.1111/cga.12233. PMID: 28603928

Prognosis

Wang L, Li X, Montazeri A, MacFarlane AJ, Momoli F, Duthie S, Senekal M, Eguiagaray IM, Munger R, Bennett D, Campbell H, Rubini M, McNulty H, Little J, Theodoratou E
Am J Clin Nutr 2023 Mar;117(3):564-575. Epub 2023 Jan 13 doi: 10.1016/j.ajcnut.2023.01.005. PMID: 36811473Free PMC Article
Green R, Miller JW
Vitam Horm 2022;119:405-439. Epub 2022 Mar 11 doi: 10.1016/bs.vh.2022.02.003. PMID: 35337628
Wu HHL, Wang AY
Vitam Horm 2022;119:325-353. Epub 2022 Feb 25 doi: 10.1016/bs.vh.2022.01.011. PMID: 35337625
Pezza M, Carlomagno V, Casucci G
G Ital Dermatol Venereol 2015 Dec;150(6):649-53. Epub 2014 Jul 31 PMID: 25077885
Vockley J, Andersson HC, Antshel KM, Braverman NE, Burton BK, Frazier DM, Mitchell J, Smith WE, Thompson BH, Berry SA; American College of Medical Genetics and Genomics Therapeutics Committee
Genet Med 2014 Feb;16(2):188-200. Epub 2013 Oct 10 doi: 10.1038/gim.2013.157. PMID: 24385074

Clinical prediction guides

Green R, Miller JW
Vitam Horm 2022;119:405-439. Epub 2022 Mar 11 doi: 10.1016/bs.vh.2022.02.003. PMID: 35337628
Wu HHL, Wang AY
Vitam Horm 2022;119:325-353. Epub 2022 Feb 25 doi: 10.1016/bs.vh.2022.01.011. PMID: 35337625
Hoxha B, Hoxha M, Domi E, Gervasoni J, Persichilli S, Malaj V, Zappacosta B
Cells 2021 Aug 3;10(8) doi: 10.3390/cells10081976. PMID: 34440744Free PMC Article
Shulpekova Y, Nechaev V, Kardasheva S, Sedova A, Kurbatova A, Bueverova E, Kopylov A, Malsagova K, Dlamini JC, Ivashkin V
Molecules 2021 Jun 18;26(12) doi: 10.3390/molecules26123731. PMID: 34207319Free PMC Article
Kay J, Upchurch KS
Rheumatology (Oxford) 2012 Dec;51 Suppl 6:vi5-9. doi: 10.1093/rheumatology/kes279. PMID: 23221588

Recent systematic reviews

Hoxha B, Hoxha M, Domi E, Gervasoni J, Persichilli S, Malaj V, Zappacosta B
Cells 2021 Aug 3;10(8) doi: 10.3390/cells10081976. PMID: 34440744Free PMC Article
Tam E, Keats EC, Rind F, Das JK, Bhutta AZA
Nutrients 2020 Jan 21;12(2) doi: 10.3390/nu12020289. PMID: 31973225Free PMC Article
Alfaro-Lara R, Espinosa-Ortega HF, Arce-Salinas CA; PRECIS study group, all physicians belong to Division of Internal Medicine. Hospital Central Sur de Pemex
Reumatol Clin (Engl Ed) 2019 May-Jun;15(3):133-139. Epub 2017 Sep 1 doi: 10.1016/j.reuma.2017.07.020. PMID: 28867467
Wang W, Zhou H, Liu L
Eur J Med Chem 2018 Oct 5;158:502-516. Epub 2018 Sep 13 doi: 10.1016/j.ejmech.2018.09.027. PMID: 30243154
Cooper C, Sommerlad A, Lyketsos CG, Livingston G
Am J Psychiatry 2015 Apr;172(4):323-34. Epub 2015 Feb 20 doi: 10.1176/appi.ajp.2014.14070878. PMID: 25698435

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