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Primary polyarteritis nodosa

MedGen UID:
1842954
•Concept ID:
C5680052
•
Disease or Syndrome
Synonyms: Primary PAN; primary PAN; Primary periarteritis nodosa; primary periarteritis nodosa; primary polyarteritis nodosa
Modes of inheritance:
Not genetically inherited
MedGen UID:
988794
•Concept ID:
CN307044
•
Finding
Source: Orphanet
clinical entity without genetic inheritance.
See: This record
Not genetically inherited (Orphanet)
 
Monarch Initiative: MONDO:0018593
Orphanet: ORPHA439737

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPrimary polyarteritis nodosa

Professional guidelines

PubMed

Treatment Guidelines in Vasculitis.
Kermani TA, Warrington KJ, Dua AB
Rheum Dis Clin North Am 2022 Aug;48(3):705-724. Epub 2022 Jul 5 doi: 10.1016/j.rdc.2022.03.006. PMID: 35953232
Treatment of systemic necrotizing vasculitides: recent advances and important clinical considerations.
Pagnoux C, Mendel A
Expert Rev Clin Immunol 2019 Sep;15(9):939-949. Epub 2019 Aug 26 doi: 10.1080/1744666X.2019.1656527. PMID: 31414912
Therapeutic advances in the treatment of vasculitis.
Eleftheriou D, Brogan PA
Pediatr Rheumatol Online J 2016 Apr 26;14(1):26. doi: 10.1186/s12969-016-0082-8. PMID: 27112923Free PMC Article

Recent clinical studies

Etiology

Treatment Guidelines in Vasculitis.
Kermani TA, Warrington KJ, Dua AB
Rheum Dis Clin North Am 2022 Aug;48(3):705-724. Epub 2022 Jul 5 doi: 10.1016/j.rdc.2022.03.006. PMID: 35953232
Nonatherosclerotic Abdominal Vasculopathies.
Skeik N, Hyde JR, Olson SL, Thaler CM, Abuatiyeh W, Ahmed AK, Lyon DR, Witt DR, Garberich R, Sullivan T
Ann Vasc Surg 2019 Oct;60:128-146. Epub 2019 Jun 12 doi: 10.1016/j.avsg.2019.04.004. PMID: 31200053
The heart in vasculitis.
Miloslavsky E, Unizony S
Rheum Dis Clin North Am 2014 Feb;40(1):11-26. doi: 10.1016/j.rdc.2013.10.006. PMID: 24268007
CNS vasculitis.
Kelley RE
Front Biosci 2004 Jan 1;9:946-55. doi: 10.2741/1259. PMID: 14766421
Vasculitis.
Watts RA, Scott DG
Baillieres Clin Rheumatol 1995 Aug;9(3):529-54. doi: 10.1016/s0950-3579(05)80257-2. PMID: 7497537

Diagnosis

Polyarteritis nodosa: an evolving primary systemic vasculitis.
Springer JM, Byram K
Postgrad Med 2023 Jan;135(sup1):61-68. Epub 2022 Jun 22 doi: 10.1080/00325481.2022.2088940. PMID: 35709399
Treatment Guidelines in Vasculitis.
Kermani TA, Warrington KJ, Dua AB
Rheum Dis Clin North Am 2022 Aug;48(3):705-724. Epub 2022 Jul 5 doi: 10.1016/j.rdc.2022.03.006. PMID: 35953232
Polyarteritis nodosa revisited: a review of historical approaches, subphenotypes and a research agenda.
Karadag O, Jayne DJ
Clin Exp Rheumatol 2018 Mar-Apr;36 Suppl 111(2):135-142. Epub 2018 Feb 20 PMID: 29465365
The heart in vasculitis.
Miloslavsky E, Unizony S
Rheum Dis Clin North Am 2014 Feb;40(1):11-26. doi: 10.1016/j.rdc.2013.10.006. PMID: 24268007
Vasculitic neuropathy.
Vrancken AF, Said G
Handb Clin Neurol 2013;115:463-83. doi: 10.1016/B978-0-444-52902-2.00026-6. PMID: 23931796

Therapy

Nonatherosclerotic Abdominal Vasculopathies.
Skeik N, Hyde JR, Olson SL, Thaler CM, Abuatiyeh W, Ahmed AK, Lyon DR, Witt DR, Garberich R, Sullivan T
Ann Vasc Surg 2019 Oct;60:128-146. Epub 2019 Jun 12 doi: 10.1016/j.avsg.2019.04.004. PMID: 31200053
Systemic vasculitis and the gut.
Hatemi I, Hatemi G, Çelik AF
Curr Opin Rheumatol 2017 Jan;29(1):33-38. doi: 10.1097/BOR.0000000000000344. PMID: 27684357
Therapeutic advances in the treatment of vasculitis.
Eleftheriou D, Brogan PA
Pediatr Rheumatol Online J 2016 Apr 26;14(1):26. doi: 10.1186/s12969-016-0082-8. PMID: 27112923Free PMC Article
Vasculitis in children.
Eleftheriou D, Brogan PA
Best Pract Res Clin Rheumatol 2009 Jun;23(3):309-23. doi: 10.1016/j.berh.2009.02.001. PMID: 19508940Free PMC Article
Vasculitic neuropathies.
Burns TM, Schaublin GA, Dyck PJ
Neurol Clin 2007 Feb;25(1):89-113. doi: 10.1016/j.ncl.2006.11.002. PMID: 17324722

Prognosis

Polyarteritis nodosa: an evolving primary systemic vasculitis.
Springer JM, Byram K
Postgrad Med 2023 Jan;135(sup1):61-68. Epub 2022 Jun 22 doi: 10.1080/00325481.2022.2088940. PMID: 35709399
Polyarteritis nodosa revisited: a review of historical approaches, subphenotypes and a research agenda.
Karadag O, Jayne DJ
Clin Exp Rheumatol 2018 Mar-Apr;36 Suppl 111(2):135-142. Epub 2018 Feb 20 PMID: 29465365
The heart in vasculitis.
Miloslavsky E, Unizony S
Rheum Dis Clin North Am 2014 Feb;40(1):11-26. doi: 10.1016/j.rdc.2013.10.006. PMID: 24268007
CNS vasculitis.
Kelley RE
Front Biosci 2004 Jan 1;9:946-55. doi: 10.2741/1259. PMID: 14766421
Polyarteritis nodosa.
Bonsib SM
Semin Diagn Pathol 2001 Feb;18(1):14-23. PMID: 11296989

Clinical prediction guides

New-onset autoimmune disease after COVID-19.
Hileman CO, Malakooti SK, Patil N, Singer NG, McComsey GA
Front Immunol 2024;15:1337406. Epub 2024 Feb 8 doi: 10.3389/fimmu.2024.1337406. PMID: 38390319Free PMC Article
Clusters in Pediatric Rheumatic Diseases.
Sag E, Demir S, Ozen S
Curr Rheumatol Rep 2020 May 20;22(7):28. doi: 10.1007/s11926-020-00908-5. PMID: 32436006
Measuring Vasculitis with Numbers: Outcome Scores.
Batu ED, Ozen S
Curr Rheumatol Rev 2020;16(1):21-28. doi: 10.2174/1573397115666191126093927. PMID: 31804163
Systemic vasculitis and the gut.
Hatemi I, Hatemi G, Çelik AF
Curr Opin Rheumatol 2017 Jan;29(1):33-38. doi: 10.1097/BOR.0000000000000344. PMID: 27684357
Vasculitis.
Watts RA, Scott DG
Baillieres Clin Rheumatol 1995 Aug;9(3):529-54. doi: 10.1016/s0950-3579(05)80257-2. PMID: 7497537

Recent systematic reviews

Systematic review of childhood-onset polyarteritis nodosa and DADA2.
Kasap Cuceoglu M, Sener S, Batu ED, Kaya Akca U, Demir S, Sag E, Atalay E, Balık Z, Basaran O, Bilginer Y, Ozen S
Semin Arthritis Rheum 2021 Jun;51(3):559-564. Epub 2021 Apr 19 doi: 10.1016/j.semarthrit.2021.04.009. PMID: 33901990
Haemophagocytic syndrome in rheumatic patients. A systematic review.
Atteritano M, David A, Bagnato G, Beninati C, Frisina A, Iaria C, Bagnato G, Cascio A
Eur Rev Med Pharmacol Sci 2012 Oct;16(10):1414-24. PMID: 23104659

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