EBV-Positive Inflammatory Follicular Dendritic Cell Sarcoma

MedGen UID:: 1776990
•Concept ID:: C5419896
•: Neoplastic Process

Synonyms:

EBV-Positive Inflammatory Follicular Dendritic Cell/Fibroblastic Reticular Cell Tumor; Epstein-Barr Virus Positive Inflammatory Follicular Dendritic Cell Sarcoma; Epstein-Barr Virus Positive Inflammatory Follicular Dendritic Cell/Fibroblastic Reticular Cell Tumor; Epstein-Barr Virus-Positive Inflammatory Follicular Dendritic Cell Sarcoma; Epstein-Barr Virus-Positive Inflammatory Follicular Dendritic Cell/Fibroblastic Reticular Cell Tumor; Inflammatory Pseudotumor-Like Follicular/Fibroblastic Dendritic Cell Sarcoma; IPT-Like FDCS

Definition

A rare, Epstein-Barr virus-associated variant of follicular dendritic cell sarcoma. It usually arises from the liver or spleen and has a favorable prognosis. The name of this entity has been changed from ""sarcoma"" to ""tumor"" because of its indolent nature. [from NCI]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

EBV-Positive Inflammatory Follicular Dendritic Cell Sarcoma

Neoplasm by Cause
- Infection-Related Neoplasm
  - Infection-Related Malignant Neoplasm
    - Virus-Related Malignant Neoplasm
      - EBV-Related Malignant Neoplasm
        EBV-Related Sarcoma
        EBV-Positive Inflammatory Follicular Dendritic Cell Sarcoma
        EBV-Positive Inflammatory Follicular Dendritic Cell/Fibroblastic Reticular Cell Tumor of the Digestive System

Recent clinical studies

Diagnosis

Clinicopathological Analysis of Epstein-Barr Virus-Positive Inflammatory Follicular Dendritic Cell Sarcoma of the Spleen: A Case Report.

Yang YH, Shi HQ, Cai JW, Wang SK
Ann Clin Lab Sci 2024 Mar;54(2):254-257. PMID: 38802163

Imaging findings of Epstein-Barr Virus-positive inflammatory follicular dendritic cell sarcoma of spleen: A case report.

Zhao X, Gai L, Wang L, Xu L
Technol Health Care 2024;32(S1):437-445. doi: 10.3233/THC-248038. PMID: 38759066 Free PMC Article

EBV-Positive Inflammatory Follicular Dendritic Cell Sarcoma of the Spleen: Report of an Aggressive Form With Molecular Characterization.

Baber A, Legendre P, Palmic P, Lupo-Mansuet A, Burroni B, Azoulay C, Szwebel TA, Costedoat-Chalumeau N, Leroy K, Blons H, Blay JY, Boudou-Rouquette P, Terrier B
Int J Surg Pathol 2024 Feb;32(1):150-154. Epub 2023 May 8 doi: 10.1177/10668969231168345. PMID: 37157817

Controversies in the Spleen: Histiocytic, Dendritic, and Stromal Cell Lesions.

Auerbach A, Girton M, Aguilera N
Surg Pathol Clin 2023 Jun;16(2):385-400. Epub 2023 Mar 8 doi: 10.1016/j.path.2023.01.004. PMID: 37149364

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