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Sinonasal Malignant Peripheral Nerve Sheath Tumor

MedGen UID:
1753079
•Concept ID:
C5420049
•
Neoplastic Process

Definition

A malignant peripheral nerve sheath tumor that arises from the nasal cavity and paranasal sinuses. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVSinonasal Malignant Peripheral Nerve Sheath Tumor

Professional guidelines

PubMed

Malignant peripheral nerve sheath tumors of the head and neck: management of 10 cases and literature review.
Minovi A, Basten O, Hunter B, Draf W, Bockmühl U
Head Neck 2007 May;29(5):439-45. doi: 10.1002/hed.20537. PMID: 17163467

Recent clinical studies

Etiology

A malignant peripheral nerve-sheath tumor: A CARE case report.
Bartier S, Boyez A, Fath L, Fieux M
Eur Ann Otorhinolaryngol Head Neck Dis 2023 Nov;140(6):309-311. Epub 2023 Oct 19 doi: 10.1016/j.anorl.2023.10.005. PMID: 37865533
Radical Exenteration of the Skull Base for End-Stage, Locally Advanced Sinonasal Malignancies: Challenging the Dictum of Unresectability.
Yeung JT, Caminer DM, Young IM, Sughrue ME, Teo C
World Neurosurg 2021 Jun;150:e102-e107. Epub 2021 Feb 26 doi: 10.1016/j.wneu.2021.02.092. PMID: 33647490
Malignant peripheral nerve sheath tumors of the head and neck: management of 10 cases and literature review.
Minovi A, Basten O, Hunter B, Draf W, Bockmühl U
Head Neck 2007 May;29(5):439-45. doi: 10.1002/hed.20537. PMID: 17163467
Endoscopic power-assisted orbital exenteration.
Batra PS, Lanza DC
Am J Rhinol 2005 May-Jun;19(3):297-301. PMID: 16011138

Diagnosis

A malignant peripheral nerve-sheath tumor: A CARE case report.
Bartier S, Boyez A, Fath L, Fieux M
Eur Ann Otorhinolaryngol Head Neck Dis 2023 Nov;140(6):309-311. Epub 2023 Oct 19 doi: 10.1016/j.anorl.2023.10.005. PMID: 37865533
PRAME immunohistochemistry in soft tissue tumors and mimics: a study of 350 cases highlighting its imperfect specificity but potentially useful diagnostic applications.
Cammareri C, Beltzung F, Michal M, Vanhersecke L, Coindre JM, Velasco V, Le Loarer F, Vergier B, Perret R
Virchows Arch 2023 Aug;483(2):145-156. Epub 2023 Jul 21 doi: 10.1007/s00428-023-03606-6. PMID: 37477762
SMARCB1-deficient Tumors of Childhood: A Practical Guide.
Pawel BR
Pediatr Dev Pathol 2018 Jan-Feb;21(1):6-28. Epub 2017 Dec 27 doi: 10.1177/1093526617749671. PMID: 29280680
Low-Grade Sinonasal Sarcoma With Neural and Myogenic Features: A Recently Discovered Entity With Unique Features and Diagnostic Challenge.
Triki M, Ayadi L
Arch Pathol Lab Med 2017 May;141(5):718-721. doi: 10.5858/arpa.2016-0133-RS. PMID: 28447903
Hemangiopericytoma: histopathological pattern or clinicopathologic entity?
Nappi O, Ritter JH, Pettinato G, Wick MR
Semin Diagn Pathol 1995 Aug;12(3):221-32. PMID: 8545589

Prognosis

Radical Exenteration of the Skull Base for End-Stage, Locally Advanced Sinonasal Malignancies: Challenging the Dictum of Unresectability.
Yeung JT, Caminer DM, Young IM, Sughrue ME, Teo C
World Neurosurg 2021 Jun;150:e102-e107. Epub 2021 Feb 26 doi: 10.1016/j.wneu.2021.02.092. PMID: 33647490
Expression of PAX3 Distinguishes Biphenotypic Sinonasal Sarcoma From Histologic Mimics.
Jo VY, Mariño-Enríquez A, Fletcher CDM, Hornick JL
Am J Surg Pathol 2018 Oct;42(10):1275-1285. doi: 10.1097/PAS.0000000000001092. PMID: 29863547
SMARCB1-deficient Tumors of Childhood: A Practical Guide.
Pawel BR
Pediatr Dev Pathol 2018 Jan-Feb;21(1):6-28. Epub 2017 Dec 27 doi: 10.1177/1093526617749671. PMID: 29280680
Novel PAX3-NCOA1 Fusions in Biphenotypic Sinonasal Sarcoma With Focal Rhabdomyoblastic Differentiation.
Huang SC, Ghossein RA, Bishop JA, Zhang L, Chen TC, Huang HY, Antonescu CR
Am J Surg Pathol 2016 Jan;40(1):51-9. doi: 10.1097/PAS.0000000000000492. PMID: 26371783Free PMC Article
Malignant peripheral nerve sheath tumors of the head and neck: management of 10 cases and literature review.
Minovi A, Basten O, Hunter B, Draf W, Bockmühl U
Head Neck 2007 May;29(5):439-45. doi: 10.1002/hed.20537. PMID: 17163467

Clinical prediction guides

Expression of PAX3 Distinguishes Biphenotypic Sinonasal Sarcoma From Histologic Mimics.
Jo VY, Mariño-Enríquez A, Fletcher CDM, Hornick JL
Am J Surg Pathol 2018 Oct;42(10):1275-1285. doi: 10.1097/PAS.0000000000001092. PMID: 29863547
Claudin-4 expression distinguishes SWI/SNF complex-deficient undifferentiated carcinomas from sarcomas.
Schaefer IM, Agaimy A, Fletcher CD, Hornick JL
Mod Pathol 2017 Apr;30(4):539-548. Epub 2017 Jan 13 doi: 10.1038/modpathol.2016.230. PMID: 28084340
Novel PAX3-NCOA1 Fusions in Biphenotypic Sinonasal Sarcoma With Focal Rhabdomyoblastic Differentiation.
Huang SC, Ghossein RA, Bishop JA, Zhang L, Chen TC, Huang HY, Antonescu CR
Am J Surg Pathol 2016 Jan;40(1):51-9. doi: 10.1097/PAS.0000000000000492. PMID: 26371783Free PMC Article
Hemangiopericytoma: histopathological pattern or clinicopathologic entity?
Nappi O, Ritter JH, Pettinato G, Wick MR
Semin Diagn Pathol 1995 Aug;12(3):221-32. PMID: 8545589

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