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Advanced Primary Cutaneous T-Cell Non-Hodgkin Lymphoma

MedGen UID:
1735144
Concept ID:
C5419664
Neoplastic Process

Definition

Primary cutaneous T-cell non-Hodgkin lymphoma that has spread extensively to other anatomic sites or is no longer responding to treatment. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAdvanced Primary Cutaneous T-Cell Non-Hodgkin Lymphoma

Professional guidelines

PubMed

Latzka J, Assaf C, Bagot M, Cozzio A, Dummer R, Guenova E, Gniadecki R, Hodak E, Jonak C, Klemke CD, Knobler R, Morrris S, Nicolay JP, Ortiz-Romero PL, Papadavid E, Pimpinelli N, Quaglino P, Ranki A, Scarisbrick J, Stadler R, Väkevä L, Vermeer MH, Wehkamp U, Whittaker S, Willemze R, Trautinger F
Eur J Cancer 2023 Dec;195:113343. Epub 2023 Sep 18 doi: 10.1016/j.ejca.2023.113343. PMID: 37890355
Hristov AC, Tejasvi T, Wilcox RA
Am J Hematol 2023 Jan;98(1):193-209. Epub 2022 Oct 20 doi: 10.1002/ajh.26760. PMID: 36226409Free PMC Article
Cook LB, Fuji S, Hermine O, Bazarbachi A, Ramos JC, Ratner L, Horwitz S, Fields P, Tanase A, Bumbea H, Cwynarski K, Taylor G, Waldmann TA, Bittencourt A, Marcais A, Suarez F, Sibon D, Phillips A, Lunning M, Farid R, Imaizumi Y, Choi I, Ishida T, Ishitsuka K, Fukushima T, Uchimaru K, Takaori-Kondo A, Tokura Y, Utsunomiya A, Matsuoka M, Tsukasaki K, Watanabe T
J Clin Oncol 2019 Mar 10;37(8):677-687. Epub 2019 Jan 18 doi: 10.1200/JCO.18.00501. PMID: 30657736Free PMC Article

Recent clinical studies

Etiology

de Leval L, Feldman AL, Pileri S, Nakamura S, Gaulard P
Virchows Arch 2023 Jan;482(1):245-264. Epub 2022 Nov 7 doi: 10.1007/s00428-022-03434-0. PMID: 36336765Free PMC Article
Goodlad JR, Cerroni L, Swerdlow SH
Virchows Arch 2023 Jan;482(1):281-298. Epub 2022 Oct 24 doi: 10.1007/s00428-022-03421-5. PMID: 36278991Free PMC Article
Hristov AC, Tejasvi T, Wilcox RA
Am J Hematol 2023 Jan;98(1):193-209. Epub 2022 Oct 20 doi: 10.1002/ajh.26760. PMID: 36226409Free PMC Article
Cook LB, Fuji S, Hermine O, Bazarbachi A, Ramos JC, Ratner L, Horwitz S, Fields P, Tanase A, Bumbea H, Cwynarski K, Taylor G, Waldmann TA, Bittencourt A, Marcais A, Suarez F, Sibon D, Phillips A, Lunning M, Farid R, Imaizumi Y, Choi I, Ishida T, Ishitsuka K, Fukushima T, Uchimaru K, Takaori-Kondo A, Tokura Y, Utsunomiya A, Matsuoka M, Tsukasaki K, Watanabe T
J Clin Oncol 2019 Mar 10;37(8):677-687. Epub 2019 Jan 18 doi: 10.1200/JCO.18.00501. PMID: 30657736Free PMC Article
Kim YH, Bagot M, Pinter-Brown L, Rook AH, Porcu P, Horwitz SM, Whittaker S, Tokura Y, Vermeer M, Zinzani PL, Sokol L, Morris S, Kim EJ, Ortiz-Romero PL, Eradat H, Scarisbrick J, Tsianakas A, Elmets C, Dalle S, Fisher DC, Halwani A, Poligone B, Greer J, Fierro MT, Khot A, Moskowitz AJ, Musiek A, Shustov A, Pro B, Geskin LJ, Dwyer K, Moriya J, Leoni M, Humphrey JS, Hudgens S, Grebennik DO, Tobinai K, Duvic M; MAVORIC Investigators
Lancet Oncol 2018 Sep;19(9):1192-1204. Epub 2018 Aug 9 doi: 10.1016/S1470-2045(18)30379-6. PMID: 30100375

Diagnosis

de Leval L, Feldman AL, Pileri S, Nakamura S, Gaulard P
Virchows Arch 2023 Jan;482(1):245-264. Epub 2022 Nov 7 doi: 10.1007/s00428-022-03434-0. PMID: 36336765Free PMC Article
Hristov AC, Tejasvi T, Wilcox RA
Am J Hematol 2023 Jan;98(1):193-209. Epub 2022 Oct 20 doi: 10.1002/ajh.26760. PMID: 36226409Free PMC Article
Hague C, Farquharson N, Menasce L, Parry E, Cowan R
Br J Hosp Med (Lond) 2022 Apr 2;83(4):1-7. Epub 2022 Apr 14 doi: 10.12968/hmed.2021.0149. PMID: 35506718
Kempf W, Mitteldorf C
Hematol Oncol 2021 Jun;39 Suppl 1:46-51. doi: 10.1002/hon.2850. PMID: 34105822
Larocca C, Kupper T
Hematol Oncol Clin North Am 2019 Feb;33(1):103-120. doi: 10.1016/j.hoc.2018.09.001. PMID: 30497668Free PMC Article

Therapy

Latzka J, Assaf C, Bagot M, Cozzio A, Dummer R, Guenova E, Gniadecki R, Hodak E, Jonak C, Klemke CD, Knobler R, Morrris S, Nicolay JP, Ortiz-Romero PL, Papadavid E, Pimpinelli N, Quaglino P, Ranki A, Scarisbrick J, Stadler R, Väkevä L, Vermeer MH, Wehkamp U, Whittaker S, Willemze R, Trautinger F
Eur J Cancer 2023 Dec;195:113343. Epub 2023 Sep 18 doi: 10.1016/j.ejca.2023.113343. PMID: 37890355
Kamijo H, Miyagaki T
Curr Treat Options Oncol 2021 Jan 7;22(2):10. doi: 10.1007/s11864-020-00809-w. PMID: 33415447
Hristov AC, Tejasvi T, Wilcox RA
Am J Hematol 2019 Sep;94(9):1027-1041. Epub 2019 Jul 31 doi: 10.1002/ajh.25577. PMID: 31313347
Kim YH, Bagot M, Pinter-Brown L, Rook AH, Porcu P, Horwitz SM, Whittaker S, Tokura Y, Vermeer M, Zinzani PL, Sokol L, Morris S, Kim EJ, Ortiz-Romero PL, Eradat H, Scarisbrick J, Tsianakas A, Elmets C, Dalle S, Fisher DC, Halwani A, Poligone B, Greer J, Fierro MT, Khot A, Moskowitz AJ, Musiek A, Shustov A, Pro B, Geskin LJ, Dwyer K, Moriya J, Leoni M, Humphrey JS, Hudgens S, Grebennik DO, Tobinai K, Duvic M; MAVORIC Investigators
Lancet Oncol 2018 Sep;19(9):1192-1204. Epub 2018 Aug 9 doi: 10.1016/S1470-2045(18)30379-6. PMID: 30100375
McClure JJ, Li X, Chou CJ
Adv Cancer Res 2018;138:183-211. Epub 2018 Mar 1 doi: 10.1016/bs.acr.2018.02.006. PMID: 29551127

Prognosis

Hristov AC, Tejasvi T, Wilcox RA
Am J Hematol 2023 Jan;98(1):193-209. Epub 2022 Oct 20 doi: 10.1002/ajh.26760. PMID: 36226409Free PMC Article
Hague C, Farquharson N, Menasce L, Parry E, Cowan R
Br J Hosp Med (Lond) 2022 Apr 2;83(4):1-7. Epub 2022 Apr 14 doi: 10.12968/hmed.2021.0149. PMID: 35506718
Kempf W, Mitteldorf C
Hematol Oncol 2021 Jun;39 Suppl 1:46-51. doi: 10.1002/hon.2850. PMID: 34105822
Kamijo H, Miyagaki T
Curr Treat Options Oncol 2021 Jan 7;22(2):10. doi: 10.1007/s11864-020-00809-w. PMID: 33415447
Larocca C, Kupper T
Hematol Oncol Clin North Am 2019 Feb;33(1):103-120. doi: 10.1016/j.hoc.2018.09.001. PMID: 30497668Free PMC Article

Clinical prediction guides

de Masson A, Beylot-Barry M, Ram-Wolff C, Mear JB, Dalle S, d'Incan M, Ingen-Housz-Oro S, Orvain C, Abraham J, Dereure O, Charbonnier A, Cornillon J, Longvert C, Barete S, Boulinguez S, Wierzbicka-Hainaut E, Aubin F, Rubio MT, Bernard M, Schmidt-Tanguy A, Houot R, Pham-Ledard A, Michonneau D, Brice P, Labussière-Wallet H, Bouaziz JD, Grange F, Moins-Teisserenc H, Jondeau K, Michel L, Mourah S, Battistella M, Daguindau E, Loschi M, Picard A, Franck N, Maillard N, Huynh A, Nguyen S, Marçais A, Chaby G, Ceballos P, Le Corre Y, Maury S, Bay JO, Adamski H, Bachy E, Forcade E, Socié G, Bagot M, Chevret S, Peffault de Latour R; CUTALLO Investigators; Groupe Français d'Etude des Lymphomes Cutanés; Société Française de Greffe de Moëlle et Thérapie Cellulaire
Lancet 2023 Jun 10;401(10392):1941-1950. Epub 2023 Apr 24 doi: 10.1016/S0140-6736(23)00329-X. PMID: 37105210
Du Y, Cai Y, Lv Y, Zhang L, Yang H, Liu Q, Hong M, Teng Y, Tang W, Ma R, Wu J, Wu J, Wang Q, Chen H, Li K, Feng J
Cancer Lett 2022 Dec 28;551:215972. Epub 2022 Oct 17 doi: 10.1016/j.canlet.2022.215972. PMID: 36265653
Phillips D, Matusiak M, Gutierrez BR, Bhate SS, Barlow GL, Jiang S, Demeter J, Smythe KS, Pierce RH, Fling SP, Ramchurren N, Cheever MA, Goltsev Y, West RB, Khodadoust MS, Kim YH, Schürch CM, Nolan GP
Nat Commun 2021 Nov 18;12(1):6726. doi: 10.1038/s41467-021-26974-6. PMID: 34795254Free PMC Article
Rindler K, Jonak C, Alkon N, Thaler FM, Kurz H, Shaw LE, Stingl G, Weninger W, Halbritter F, Bauer WM, Farlik M, Brunner PM
Mol Cancer 2021 Sep 28;20(1):124. doi: 10.1186/s12943-021-01419-2. PMID: 34583709Free PMC Article
Kim YH, Bagot M, Pinter-Brown L, Rook AH, Porcu P, Horwitz SM, Whittaker S, Tokura Y, Vermeer M, Zinzani PL, Sokol L, Morris S, Kim EJ, Ortiz-Romero PL, Eradat H, Scarisbrick J, Tsianakas A, Elmets C, Dalle S, Fisher DC, Halwani A, Poligone B, Greer J, Fierro MT, Khot A, Moskowitz AJ, Musiek A, Shustov A, Pro B, Geskin LJ, Dwyer K, Moriya J, Leoni M, Humphrey JS, Hudgens S, Grebennik DO, Tobinai K, Duvic M; MAVORIC Investigators
Lancet Oncol 2018 Sep;19(9):1192-1204. Epub 2018 Aug 9 doi: 10.1016/S1470-2045(18)30379-6. PMID: 30100375

Recent systematic reviews

Travaglino A, Varricchio S, Pace M, Russo D, Picardi M, Baldo A, Staibano S, Mascolo M
J Dtsch Dermatol Ges 2020 Dec;18(12):1379-1384. Epub 2020 Oct 8 doi: 10.1111/ddg.14289. PMID: 33029842
Gangemi S, Quartuccio S, Casciaro M, Trapani G, Minciullo PL, Imbalzano E
Allergy Asthma Proc 2017 Nov 1;38(6):401-408. doi: 10.2500/aap.2017.38.4080. PMID: 29046191
Schlaak M, Pickenhain J, Theurich S, Skoetz N, von Bergwelt-Baildon M, Kurschat P
Cochrane Database Syst Rev 2013 Aug 29;2013(8):CD008908. doi: 10.1002/14651858.CD008908.pub3. PMID: 23986525Free PMC Article
Schlaak M, Theurich S, Pickenhain J, Skoetz N, Kurschat P, von Bergwelt-Baildon M
Crit Rev Oncol Hematol 2013 Jan;85(1):21-31. Epub 2012 Jul 18 doi: 10.1016/j.critrevonc.2012.06.002. PMID: 22819279
Schlaak M, Pickenhain J, Theurich S, Skoetz N, von Bergwelt-Baildon M, Kurschat P
Cochrane Database Syst Rev 2012 Jan 18;1:CD008908. doi: 10.1002/14651858.CD008908.pub2. PMID: 22258991

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