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Recurrent Severe Aplastic Anemia

MedGen UID:
1663591
Concept ID:
C4727149
Disease or Syndrome
Synonym: Relapsed Severe Aplastic Anemia

Definition

The reemergence of severe aplastic anemia after a period of remission. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVRecurrent Severe Aplastic Anemia

Professional guidelines

PubMed

Pierri F, Dufour C
Expert Rev Hematol 2019 Oct;12(10):809-819. Epub 2019 Jul 24 doi: 10.1080/17474086.2019.1645003. PMID: 31311355
Clucas DB, Fox LC, Wood EM, Hong FS, Gibson J, Bajel A, Szer J, Blombery P, McQuilten ZK, Hiwase D, Firkin F, Cole-Sinclair MF; Australian Aplastic Anaemia Registry Steering Committee
Intern Med J 2019 Feb;49(2):152-159. doi: 10.1111/imj.14140. PMID: 30324755
Georges GE, Doney K, Storb R
Blood Adv 2018 Aug 14;2(15):2020-2028. doi: 10.1182/bloodadvances.2018021162. PMID: 30108110Free PMC Article

Recent clinical studies

Etiology

Patel BA, Townsley DM, Scheinberg P
Semin Hematol 2022 Jan;59(1):21-29. Epub 2022 Jan 19 doi: 10.1053/j.seminhematol.2022.01.002. PMID: 35491055
Siddiqui S, Cox J, Herzig R, Palaniyandi S, Hildebrandt GC, Munker R
Indian J Med Res 2019 Sep;150(3):221-227. doi: 10.4103/ijmr.IJMR_752_19. PMID: 31719292Free PMC Article
Georges GE, Doney K, Storb R
Blood Adv 2018 Aug 14;2(15):2020-2028. doi: 10.1182/bloodadvances.2018021162. PMID: 30108110Free PMC Article
Desmond R, Townsley DM, Dunbar C, Young NS
Semin Hematol 2015 Jan;52(1):31-7. Epub 2014 Oct 31 doi: 10.1053/j.seminhematol.2014.10.002. PMID: 25578417Free PMC Article
Scaringi C, De Sanctis V, Minniti G, Enrici RM
Onkologie 2013;36(7-8):444-9. Epub 2013 Jul 8 doi: 10.1159/000353752. PMID: 23921765

Diagnosis

Wang ZJ, Chen HB, Zhou F, Yu H, Wu XY, Shen YQ, Qiu YN, Jin RM
Curr Med Sci 2022 Apr;42(2):379-386. Epub 2022 Mar 8 doi: 10.1007/s11596-022-2519-2. PMID: 35258748
Clucas DB, Fox LC, Wood EM, Hong FS, Gibson J, Bajel A, Szer J, Blombery P, McQuilten ZK, Hiwase D, Firkin F, Cole-Sinclair MF; Australian Aplastic Anaemia Registry Steering Committee
Intern Med J 2019 Feb;49(2):152-159. doi: 10.1111/imj.14140. PMID: 30324755
Georges GE, Doney K, Storb R
Blood Adv 2018 Aug 14;2(15):2020-2028. doi: 10.1182/bloodadvances.2018021162. PMID: 30108110Free PMC Article
Khincha PP, Savage SA
Semin Fetal Neonatal Med 2016 Feb;21(1):57-65. Epub 2015 Dec 24 doi: 10.1016/j.siny.2015.12.003. PMID: 26724991Free PMC Article
Scaringi C, De Sanctis V, Minniti G, Enrici RM
Onkologie 2013;36(7-8):444-9. Epub 2013 Jul 8 doi: 10.1159/000353752. PMID: 23921765

Therapy

DeZern AE, Eapen M, Wu J, Talano JA, Solh M, Dávila Saldaña BJ, Karanes C, Horwitz ME, Mallhi K, Arai S, Farhadfar N, Hexner E, Westervelt P, Antin JH, Deeg HJ, Leifer E, Brodsky RA, Logan BR, Horowitz MM, Jones RJ, Pulsipher MA
Lancet Haematol 2022 Sep;9(9):e660-e669. Epub 2022 Jul 27 doi: 10.1016/S2352-3026(22)00206-X. PMID: 35907408Free PMC Article
Röth A, Bertram S, Schroeder T, Haverkamp T, Voigt S, Holtkamp C, Klump H, Wörmann B, Reinhardt HC, Alashkar F
Eur J Haematol 2022 Aug;109(2):186-194. Epub 2022 Jun 1 doi: 10.1111/ejh.13788. PMID: 35592930Free PMC Article
Siddiqui S, Cox J, Herzig R, Palaniyandi S, Hildebrandt GC, Munker R
Indian J Med Res 2019 Sep;150(3):221-227. doi: 10.4103/ijmr.IJMR_752_19. PMID: 31719292Free PMC Article
Desmond R, Townsley DM, Dunbar C, Young NS
Semin Hematol 2015 Jan;52(1):31-7. Epub 2014 Oct 31 doi: 10.1053/j.seminhematol.2014.10.002. PMID: 25578417Free PMC Article
Scaringi C, De Sanctis V, Minniti G, Enrici RM
Onkologie 2013;36(7-8):444-9. Epub 2013 Jul 8 doi: 10.1159/000353752. PMID: 23921765

Prognosis

Röth A, Bertram S, Schroeder T, Haverkamp T, Voigt S, Holtkamp C, Klump H, Wörmann B, Reinhardt HC, Alashkar F
Eur J Haematol 2022 Aug;109(2):186-194. Epub 2022 Jun 1 doi: 10.1111/ejh.13788. PMID: 35592930Free PMC Article
Siddiqui S, Cox J, Herzig R, Palaniyandi S, Hildebrandt GC, Munker R
Indian J Med Res 2019 Sep;150(3):221-227. doi: 10.4103/ijmr.IJMR_752_19. PMID: 31719292Free PMC Article
Pierri F, Dufour C
Expert Rev Hematol 2019 Oct;12(10):809-819. Epub 2019 Jul 24 doi: 10.1080/17474086.2019.1645003. PMID: 31311355
Scaringi C, De Sanctis V, Minniti G, Enrici RM
Onkologie 2013;36(7-8):444-9. Epub 2013 Jul 8 doi: 10.1159/000353752. PMID: 23921765
Scheinberg P
Int J Hematol 2013 May;97(5):553-7. Epub 2013 May 1 doi: 10.1007/s12185-013-1332-x. PMID: 23636667

Clinical prediction guides

Aggarwal N, Manley AL, Shalhoub R, Durrani J, Rios O, Lotter J, Patel BA, Wu CO, Young NS, Groarke EM
Am J Hematol 2023 Jun;98(6):932-939. Epub 2023 Apr 6 doi: 10.1002/ajh.26924. PMID: 37021397Free PMC Article
DeZern AE, Eapen M, Wu J, Talano JA, Solh M, Dávila Saldaña BJ, Karanes C, Horwitz ME, Mallhi K, Arai S, Farhadfar N, Hexner E, Westervelt P, Antin JH, Deeg HJ, Leifer E, Brodsky RA, Logan BR, Horowitz MM, Jones RJ, Pulsipher MA
Lancet Haematol 2022 Sep;9(9):e660-e669. Epub 2022 Jul 27 doi: 10.1016/S2352-3026(22)00206-X. PMID: 35907408Free PMC Article
Röth A, Bertram S, Schroeder T, Haverkamp T, Voigt S, Holtkamp C, Klump H, Wörmann B, Reinhardt HC, Alashkar F
Eur J Haematol 2022 Aug;109(2):186-194. Epub 2022 Jun 1 doi: 10.1111/ejh.13788. PMID: 35592930Free PMC Article
Liu L, Xu G, Zhang Y, Jiao W, Lei M, Zhou H, Wang Q, Qiu H, Tang X, Han Y, Fu C, Jin Z, Chen S, Sun A, Miao M, Wu D
Transplant Cell Ther 2021 Feb;27(2):186.e1-186.e3. Epub 2020 Aug 21 doi: 10.1016/j.bbmt.2020.08.020. PMID: 32829081
Scheinberg P
Int J Hematol 2013 May;97(5):553-7. Epub 2013 May 1 doi: 10.1007/s12185-013-1332-x. PMID: 23636667

Recent systematic reviews

Martí-Carvajal AJ, Anand V, Cardona AF, Solà I
Cochrane Database Syst Rev 2014 Oct 30;(10):CD010340. doi: 10.1002/14651858.CD010340.pub2. PMID: 25356860

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