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Metastatic Fibrolamellar Carcinoma

MedGen UID:
1652119
Concept ID:
C4727458
Neoplastic Process
Synonyms: Metastatic Fibrolamellar Hepatocellular Carcinoma; Metastatic FLC

Definition

A fibrolamellar carcinoma that has spread from the liver to another anatomic site. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVMetastatic Fibrolamellar Carcinoma

Professional guidelines

PubMed

Aziz H, Brown ZJ, Panid Madani S, Kamel IR, Pawlik TM
J Am Coll Surg 2023 Feb 1;236(2):399-410. Epub 2022 Nov 4 doi: 10.1097/XCS.0000000000000476. PMID: 36648268
Hackl C, Schlitt HJ, Kirchner GI, Knoppke B, Loss M
World J Gastroenterol 2014 May 14;20(18):5331-44. doi: 10.3748/wjg.v20.i18.5331. PMID: 24833863Free PMC Article
Lee WJ, Lim HK, Jang KM, Kim SH, Lee SJ, Lim JH, Choo IW
Radiographics 2001 Oct;21 Spec No:S97-S116. doi: 10.1148/radiographics.21.suppl_1.g01oc12s97. PMID: 11598251

Recent clinical studies

Etiology

Cooney T, Wei MC, Rangaswami A, Xu L, Sage J, Hazard FK
Ann Clin Lab Sci 2017 Aug;47(4):395-402. PMID: 28801364
Do RK, McErlean A, Ang CS, DeMatteo RP, Abou-Alfa GK
Br J Radiol 2014 Aug;87(1040):20140024. Epub 2014 Jun 4 doi: 10.1259/bjr.20140024. PMID: 24896196Free PMC Article
Eghtesad B, Aucejo F
J Gastrointest Cancer 2014 Sep;45(3):353-62. doi: 10.1007/s12029-014-9590-2. PMID: 24604263
Guest J, Blumgart LH
Baillieres Clin Gastroenterol 1987 Jan;1(1):131-50. doi: 10.1016/0950-3528(87)90037-6. PMID: 3034356
Schiff L
Semin Roentgenol 1983 Apr;18(2):71-4. doi: 10.1016/0037-198x(83)90004-4. PMID: 6191395

Diagnosis

Aziz H, Brown ZJ, Panid Madani S, Kamel IR, Pawlik TM
J Am Coll Surg 2023 Feb 1;236(2):399-410. Epub 2022 Nov 4 doi: 10.1097/XCS.0000000000000476. PMID: 36648268
O'Neill AF, Church AJ, Perez-Atayde AR, Shaikh R, Marcus KJ, Vakili K
Curr Probl Cancer 2021 Aug;45(4):100770. Epub 2021 Jul 1 doi: 10.1016/j.currproblcancer.2021.100770. PMID: 34272087
Matsukuma KE, Yeh MM
Ann Diagn Pathol 2019 Feb;38:126-137. Epub 2018 Oct 12 doi: 10.1016/j.anndiagpath.2018.10.005. PMID: 30597357
Kamaya A, Maturen KE, Tye GA, Liu YI, Parti NN, Desser TS
Semin Ultrasound CT MR 2009 Oct;30(5):387-407. doi: 10.1053/j.sult.2009.06.001. PMID: 19842564
Guest J, Blumgart LH
Baillieres Clin Gastroenterol 1987 Jan;1(1):131-50. doi: 10.1016/0950-3528(87)90037-6. PMID: 3034356

Therapy

Leiting JL, Hernandez MC, Bergquist JR, Yonkus JA, Abdelrahman AM, Torbenson MS, Tran NH, Halfdanarson TR, Graham RP, Smoot RL, Truty MJ
In Vivo 2023 Sep-Oct;37(5):1940-1950. doi: 10.21873/invivo.13290. PMID: 37652480Free PMC Article
Lalazar G, Requena D, Ramos-Espiritu L, Ng D, Bhola PD, de Jong YP, Wang R, Narayan NJC, Shebl B, Levin S, Michailidis E, Kabbani M, Vercauteren KOA, Hurley AM, Farber BA, Hammond WJ, Saltsman JA 3rd, Weinberg EM, Glickman JF, Lyons BA, Ellison J, Schadde E, Hertl M, Leiting JL, Truty MJ, Smoot RL, Tierney F, Kato T, Wendel HG, LaQuaglia MP, Rice CM, Letai A, Coffino P, Torbenson MS, Ortiz MV, Simon SM
Cancer Discov 2021 Oct;11(10):2544-2563. Epub 2021 Jun 14 doi: 10.1158/2159-8290.CD-20-0872. PMID: 34127480Free PMC Article
Al Zahrani A, Alfakeeh A
J Med Case Rep 2021 Mar 16;15(1):132. doi: 10.1186/s13256-021-02695-8. PMID: 33722275Free PMC Article
Eghtesad B, Aucejo F
J Gastrointest Cancer 2014 Sep;45(3):353-62. doi: 10.1007/s12029-014-9590-2. PMID: 24604263
Schiff L
Semin Roentgenol 1983 Apr;18(2):71-4. doi: 10.1016/0037-198x(83)90004-4. PMID: 6191395

Prognosis

Melehy A, Agopian V
Curr Opin Organ Transplant 2024 Feb 1;29(1):30-36. Epub 2023 Oct 18 doi: 10.1097/MOT.0000000000001118. PMID: 37851086
Aziz H, Brown ZJ, Panid Madani S, Kamel IR, Pawlik TM
J Am Coll Surg 2023 Feb 1;236(2):399-410. Epub 2022 Nov 4 doi: 10.1097/XCS.0000000000000476. PMID: 36648268
Al Zahrani A, Alfakeeh A
J Med Case Rep 2021 Mar 16;15(1):132. doi: 10.1186/s13256-021-02695-8. PMID: 33722275Free PMC Article
Cooney T, Wei MC, Rangaswami A, Xu L, Sage J, Hazard FK
Ann Clin Lab Sci 2017 Aug;47(4):395-402. PMID: 28801364
Guest J, Blumgart LH
Baillieres Clin Gastroenterol 1987 Jan;1(1):131-50. doi: 10.1016/0950-3528(87)90037-6. PMID: 3034356

Clinical prediction guides

Melehy A, Agopian V
Curr Opin Organ Transplant 2024 Feb 1;29(1):30-36. Epub 2023 Oct 18 doi: 10.1097/MOT.0000000000001118. PMID: 37851086
Hammond WJ, Lalazar G, Saltsman JA, Farber BA, Danzer E, Sherpa TC, Banda CD, Andolina JR, Karimi S, Brennan CW, Torbenson MS, La Quaglia MP, Simon SM
Pediatr Blood Cancer 2018 Apr;65(4) Epub 2017 Dec 29 doi: 10.1002/pbc.26919. PMID: 29286561Free PMC Article
Grossman EJ, Millis JM
Liver Transpl 2010 Aug;16(8):930-42. doi: 10.1002/lt.22106. PMID: 20677284
Heneghan MA, O'Grady JG
Baillieres Best Pract Res Clin Gastroenterol 1999 Dec;13(4):575-91. doi: 10.1053/bega.1999.0049. PMID: 10654921
Schlitt HJ, Neipp M, Weimann A, Oldhafer KJ, Schmoll E, Boeker K, Nashan B, Kubicka S, Maschek H, Tusch G, Raab R, Ringe B, Manns MP, Pichlmayr R
J Clin Oncol 1999 Jan;17(1):324-31. doi: 10.1200/JCO.1999.17.1.324. PMID: 10458250

Recent systematic reviews

Aziz H, Brown ZJ, Panid Madani S, Kamel IR, Pawlik TM
J Am Coll Surg 2023 Feb 1;236(2):399-410. Epub 2022 Nov 4 doi: 10.1097/XCS.0000000000000476. PMID: 36648268

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