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Retrocochlear disease

MedGen UID:
11216
•Concept ID:
C0035352
•
Disease or Syndrome
Synonyms: Disease, Retrocochlear; Diseases, Retrocochlear; Retrocochlear Disease; Retrocochlear Diseases
 
Monarch Initiative: MONDO:0002453

Definition

Pathological processes involving the vestibulocochlear nerve; brainstem; or central nervous system. When hearing loss is due to retrocochlear pathology, it is called retrocochlear hearing loss. [from MONDO]

Professional guidelines

PubMed

Clinical Utility of the Standardized Word Recognition Score.
Zapala DA, Stamper GC, Bogle JM, Jagger SL, Lundy LB
Ear Hear 2024 Jan-Feb 01;45(1):94-105. Epub 2023 Jun 30 doi: 10.1097/AUD.0000000000001404. PMID: 37386698
Oral steroid treatment of sudden sensorineural hearing loss: a ten year retrospective analysis.
Chen CY, Halpin C, Rauch SD
Otol Neurotol 2003 Sep;24(5):728-33. doi: 10.1097/00129492-200309000-00006. PMID: 14501447
A practical approach to the patient with vertigo: an outline of diagnosis and management for the nonspecialist.
Turner JS Jr
South Med J 1975 Feb;68(2):241-5. doi: 10.1097/00007611-197502000-00027. PMID: 1118759

Recent clinical studies

Etiology

Clinical Utility of the Standardized Word Recognition Score.
Zapala DA, Stamper GC, Bogle JM, Jagger SL, Lundy LB
Ear Hear 2024 Jan-Feb 01;45(1):94-105. Epub 2023 Jun 30 doi: 10.1097/AUD.0000000000001404. PMID: 37386698
Hearing rehabilitation outcomes in cochlear implant recipients with vestibular schwannoma in observation or radiotherapy groups: A systematic review.
Borsetto D, Hammond-Kenny A, Tysome JR, Axon PR, Donnelly NP, Vijendren A, Phillips V, Bance ML
Cochlear Implants Int 2020 Jan;21(1):9-17. Epub 2019 Sep 8 doi: 10.1080/14670100.2019.1662161. PMID: 31496442
Effects of type 1 diabetes mellitus on efferent auditory system in children and adolescents.
Braite N, da Cruz Fernandes L, Rissatto Lago MR, de Aragão Dantas Alves C
Int J Pediatr Otorhinolaryngol 2019 Dec;127:109660. Epub 2019 Aug 25 doi: 10.1016/j.ijporl.2019.109660. PMID: 31487561
Outcomes of cochlear implantation in patients with neurofibromatosis type 2.
North HJ, Mawman D, O'Driscoll M, Freeman SR, Rutherford SA, King AT, Hammerbeck-Ward C, Evans DG, Lloyd SK
Cochlear Implants Int 2016 Jul;17(4):172-177. doi: 10.1080/14670100.2016.1197587. PMID: 27691934
Intratympanic dexamethasone for sudden sensorineural hearing loss after failure of systemic therapy.
Haynes DS, O'Malley M, Cohen S, Watford K, Labadie RF
Laryngoscope 2007 Jan;117(1):3-15. doi: 10.1097/01.mlg.0000245058.11866.15. PMID: 17202923

Diagnosis

Clinical Utility of the Standardized Word Recognition Score.
Zapala DA, Stamper GC, Bogle JM, Jagger SL, Lundy LB
Ear Hear 2024 Jan-Feb 01;45(1):94-105. Epub 2023 Jun 30 doi: 10.1097/AUD.0000000000001404. PMID: 37386698
Effects of type 1 diabetes mellitus on efferent auditory system in children and adolescents.
Braite N, da Cruz Fernandes L, Rissatto Lago MR, de Aragão Dantas Alves C
Int J Pediatr Otorhinolaryngol 2019 Dec;127:109660. Epub 2019 Aug 25 doi: 10.1016/j.ijporl.2019.109660. PMID: 31487561
Pseudo-sudden deafness.
Song JE, Sapthavee A, Cager GR, Saadia-Redleaf MI
Ann Otol Rhinol Laryngol 2012 Feb;121(2):96-9. doi: 10.1177/000348941212100204. PMID: 22397217
Oral steroid treatment of sudden sensorineural hearing loss: a ten year retrospective analysis.
Chen CY, Halpin C, Rauch SD
Otol Neurotol 2003 Sep;24(5):728-33. doi: 10.1097/00129492-200309000-00006. PMID: 14501447
Analysis of the efficiency of retrocochlear screening.
Kotlarz JP, Eby TL, Borton TE
Laryngoscope 1992 Oct;102(10):1108-12. doi: 10.1288/00005537-199210000-00004. PMID: 1405961

Therapy

Pseudo-sudden deafness.
Song JE, Sapthavee A, Cager GR, Saadia-Redleaf MI
Ann Otol Rhinol Laryngol 2012 Feb;121(2):96-9. doi: 10.1177/000348941212100204. PMID: 22397217
Intratympanic dexamethasone for sudden sensorineural hearing loss after failure of systemic therapy.
Haynes DS, O'Malley M, Cohen S, Watford K, Labadie RF
Laryngoscope 2007 Jan;117(1):3-15. doi: 10.1097/01.mlg.0000245058.11866.15. PMID: 17202923
Oral steroid treatment of sudden sensorineural hearing loss: a ten year retrospective analysis.
Chen CY, Halpin C, Rauch SD
Otol Neurotol 2003 Sep;24(5):728-33. doi: 10.1097/00129492-200309000-00006. PMID: 14501447
Mass screening for retrocochlear disorders: low-field-strength (0.2-T) versus high-field-strength (1.5-T) MR imaging.
Dubrulle F, Delomez J, Kiaei A, Berger P, Vincent C, Vaneecloo FM, Lemaitre L
AJNR Am J Neuroradiol 2002 Jun-Jul;23(6):918-23. PMID: 12063216Free PMC Article
A practical approach to the patient with vertigo: an outline of diagnosis and management for the nonspecialist.
Turner JS Jr
South Med J 1975 Feb;68(2):241-5. doi: 10.1097/00007611-197502000-00027. PMID: 1118759

Prognosis

Clinical Utility of the Standardized Word Recognition Score.
Zapala DA, Stamper GC, Bogle JM, Jagger SL, Lundy LB
Ear Hear 2024 Jan-Feb 01;45(1):94-105. Epub 2023 Jun 30 doi: 10.1097/AUD.0000000000001404. PMID: 37386698
Intratympanic dexamethasone for sudden sensorineural hearing loss after failure of systemic therapy.
Haynes DS, O'Malley M, Cohen S, Watford K, Labadie RF
Laryngoscope 2007 Jan;117(1):3-15. doi: 10.1097/01.mlg.0000245058.11866.15. PMID: 17202923
Oral steroid treatment of sudden sensorineural hearing loss: a ten year retrospective analysis.
Chen CY, Halpin C, Rauch SD
Otol Neurotol 2003 Sep;24(5):728-33. doi: 10.1097/00129492-200309000-00006. PMID: 14501447
Management of vestibular schwannomas (acoustic neuromas): the value of neurophysiology for evaluation and prediction of auditory function in 420 cases.
Matthies C, Samii M
Neurosurgery 1997 May;40(5):919-29; discussion 929-30. doi: 10.1097/00006123-199705000-00007. PMID: 9149249
Analysis of the efficiency of retrocochlear screening.
Kotlarz JP, Eby TL, Borton TE
Laryngoscope 1992 Oct;102(10):1108-12. doi: 10.1288/00005537-199210000-00004. PMID: 1405961

Clinical prediction guides

Clinical Utility of the Standardized Word Recognition Score.
Zapala DA, Stamper GC, Bogle JM, Jagger SL, Lundy LB
Ear Hear 2024 Jan-Feb 01;45(1):94-105. Epub 2023 Jun 30 doi: 10.1097/AUD.0000000000001404. PMID: 37386698
Effects of type 1 diabetes mellitus on efferent auditory system in children and adolescents.
Braite N, da Cruz Fernandes L, Rissatto Lago MR, de Aragão Dantas Alves C
Int J Pediatr Otorhinolaryngol 2019 Dec;127:109660. Epub 2019 Aug 25 doi: 10.1016/j.ijporl.2019.109660. PMID: 31487561
Outcomes of cochlear implantation in patients with neurofibromatosis type 2.
North HJ, Mawman D, O'Driscoll M, Freeman SR, Rutherford SA, King AT, Hammerbeck-Ward C, Evans DG, Lloyd SK
Cochlear Implants Int 2016 Jul;17(4):172-177. doi: 10.1080/14670100.2016.1197587. PMID: 27691934
Pseudo-sudden deafness.
Song JE, Sapthavee A, Cager GR, Saadia-Redleaf MI
Ann Otol Rhinol Laryngol 2012 Feb;121(2):96-9. doi: 10.1177/000348941212100204. PMID: 22397217
Analysis of the efficiency of retrocochlear screening.
Kotlarz JP, Eby TL, Borton TE
Laryngoscope 1992 Oct;102(10):1108-12. doi: 10.1288/00005537-199210000-00004. PMID: 1405961

Recent systematic reviews

Hearing rehabilitation outcomes in cochlear implant recipients with vestibular schwannoma in observation or radiotherapy groups: A systematic review.
Borsetto D, Hammond-Kenny A, Tysome JR, Axon PR, Donnelly NP, Vijendren A, Phillips V, Bance ML
Cochlear Implants Int 2020 Jan;21(1):9-17. Epub 2019 Sep 8 doi: 10.1080/14670100.2019.1662161. PMID: 31496442

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