Lmna G609G knock-in model of Hutchinson-Gilford Progeria Syndrome: liver
Summary:
Analysis of liver from Lmna Gly609Gly knock-in C57BL/6 females. These mice accumulate progerin and manifest the main clinical features of human Hutchinson-Gilford progeria syndrome (HGPS). Results provide insight into the molecular mechanisms underlying HGPS.
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