Single-Stage Repair of an Unusual Association: Congenital Gerbode Defect, Hypoplastic Aortic Arch, and Partially Anomalous Pulmonary Venous Return in an Infant

World J Pediatr Congenit Heart Surg. 2016 Jul;7(4):502-5. doi: 10.1177/2150135115603331. Epub 2016 Feb 6.

Abstract

We present the case of a two-month-old male with congenital Gerbode defect, hypoplastic aortic arch, and left-sided partially anomalous pulmonary venous return. The patient underwent single-stage surgical repair, which consisted of aortic arch advancement with resection of the coarctation segment, pulmonary vein repair, and primary closure of the Gerbode defect. The anomalous pulmonary vein posed a particular challenge due to its size and distance from the left atrium, which we approached with a posterior atrial wall trapdoor baffle technique, without mobilizing the affected vein. Postoperatively and at one year follow-up, there was no evidence of residual lesions and there was unobstructed flow pattern across the aortic arch and the affected pulmonary vein.

Keywords: Gerbode defect; coarctation of the aorta; partially anomalous pulmonary venous return.

Publication types

  • Case Reports

MeSH terms

  • Aorta, Thoracic / abnormalities*
  • Aortic Coarctation / surgery*
  • Cardiac Surgical Procedures / methods*
  • Heart Septal Defects, Ventricular / surgery*
  • Humans
  • Infant
  • Male
  • Pulmonary Veins / abnormalities*
  • Scimitar Syndrome / surgery*
  • Treatment Outcome