Extracorporeal membrane oxygenation support of a severe metabolic crisis in a child with methylmalonic acidemia

Ryan J Stark; Bindi J Naik-Mathuria; Fong W Lam; Oluyinka O Olutoye; V Reid Sutton; Lara S Shekerdemian

doi:10.1097/MAT.0b013e31825a223c

Extracorporeal membrane oxygenation support of a severe metabolic crisis in a child with methylmalonic acidemia

ASAIO J. 2012 Jul-Aug;58(4):438-9. doi: 10.1097/MAT.0b013e31825a223c.

Authors

Ryan J Stark¹, Bindi J Naik-Mathuria, Fong W Lam, Oluyinka O Olutoye, V Reid Sutton, Lara S Shekerdemian

Affiliation

¹ Department of Critical Care, Texas Children's Hospital, Houston, 77030, USA.

PMID: 22711065
DOI: 10.1097/MAT.0b013e31825a223c

Abstract

A 9-year-old female, with mut phenotype of methylmalonic acidemia who developed severe vasoplegic shock during a metabolic crisis, was successfully supported with venoarterial extracorporeal membrane oxygenation.

Publication types

Case Reports

MeSH terms

Amino Acid Metabolism, Inborn Errors / genetics*
Amino Acid Metabolism, Inborn Errors / pathology*
Child
Extracorporeal Membrane Oxygenation*
Female
Humans
Methylmalonic Acid / metabolism
Phenotype
Respiratory Insufficiency / etiology
Treatment Outcome
Vasoplegia / etiology

Substances

Methylmalonic Acid

Supplementary concepts

Methylmalonic acidemia