Cardiac sarcoidosis

Clin Chest Med. 2008 Sep;29(3):493-508, ix. doi: 10.1016/j.ccm.2008.03.005.

Abstract

Sarcoidosis is a systemic disease with a favorable prognosis, high remission rate, and low mortality. Cardiac involvement alters this prognosis. Clinical manifestations most commonly include arrhythmias, conduction abnormalities, and congestive heart failure. Treatment includes immunosuppressant therapy, permanent pacemakers in the setting of conduction abnormalities, and implantable cardioverter-defibrillators in patients at risk for sudden cardiac death. Risk stratification for sudden cardiac death is essential in otherwise asymptomatic patients who have suspected cardiac sarcoidosis.

Publication types

  • Review

MeSH terms

  • Cardiac Pacing, Artificial / methods
  • Cardiomyopathies* / diagnosis
  • Cardiomyopathies* / epidemiology
  • Cardiomyopathies* / therapy
  • Catheter Ablation / methods
  • Diagnostic Techniques, Cardiovascular
  • Global Health
  • Humans
  • Immunosuppressive Agents / therapeutic use
  • Morbidity / trends
  • Prognosis
  • Sarcoidosis* / diagnosis
  • Sarcoidosis* / epidemiology
  • Sarcoidosis* / therapy

Substances

  • Immunosuppressive Agents