Purpose: To present a case of retrobulbar optic nerve and chiasm sarcoidosis that mimicked pseudotumor cerebri.
Methods: A 34-year-old, thin, black woman presented with transient visual obscurations, normal visual acuity, bilateral optic disk edema, and enlarged blind spots. Clinical, medical, and radiologic evaluations were consistent with pseudotumor cerebri. The patient improved while taking acetazolamide, but 6 months later her symptoms worsened. Neuroimaging disclosed enhancement of the optic nerve and chiasm.
Results: Despite administration of intravenous corticosteroids, the patient's vision worsened. Bilateral optic nerve sheath fenestrations were performed, and pathology disclosed sarcoidosis.
Conclusion: Sarcoidosis of the optic nerves and chiasm may mimic pseudotumor cerebri.