Hamman-Rich Syndrome
Acute idiopathic interstitial pneumonitis characterized by diffuse PULMONARY ALVEOLI damage with uniform edematous connective tissue proliferation. It is often associated with extensive fibroblastic distortion of the lung parenchyma and leads to ADULT RESPIRATORY DISTRESS SYNDROME in later stages.
Year introduced: 2020
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Subheadings:
Tree Number(s): C08.381.483.652.500.500
MeSH Unique ID: D000080203
Entry Terms:
- Hamman Rich Syndrome
- Acute Interstitial Pneumonia
- Acute Interstitial Pneumonias
- Interstitial Pneumonia, Acute
- Pneumonia, Acute Interstitial
- Acute Interstitial Pneumonitis
- Acute Interstitial Pneumonitides
- Interstitial Pneumonitis, Acute
- Pneumonitis, Acute Interstitial
- Hamman-Rich Disease
- Hamman Rich Disease