Dandy-Walker Syndrome
A congenital abnormality of the central nervous system marked by failure of the midline structures of the cerebellum to develop, dilation of the fourth ventricle, and upward displacement of the transverse sinuses, tentorium, and torcula. Clinical features include occipital bossing, progressive head enlargement, bulging of anterior fontanelle, papilledema, ataxia, gait disturbances, nystagmus, and intellectual compromise. (From Menkes, Textbook of Child Neurology, 5th ed, pp294-5)
Year introduced: 1991(1970)
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Subheadings:
Tree Number(s): C10.228.140.252.300, C10.228.140.602.500, C10.500.205, C16.131.666.205
MeSH Unique ID: D003616
Entry Terms:
- Dandy Walker Syndrome
- Dandy-Walker Malformation
- Dandy Walker Malformation
- Malformation, Dandy-Walker
- Dandy-Walker Complex
- Dandy Walker Complex
- Dandy-Walker Complices
- Dandy-Walker Cyst
- Cyst, Dandy-Walker
- Cysts, Dandy-Walker
- Dandy-Walker Cysts
- Dandy-Walker Deformity
- Dandy-Walker Deformities
- Dandy Walker Deformity
- Hydrocephalus, Internal, Dandy-Walker Type
- Hydrocephalus, Noncommunicating, Dandy-Walker Type
- Luschka-Magendie Foramina Atresia
- Luschka Magendie Foramina Atresia
- Dandy-Walker Syndrome, Familial
- Dandy Walker Syndrome, Familial
- Familial Dandy-Walker Syndrome
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