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Invasive Sarcomatoid Urothelial Carcinoma

MedGen UID:
1713564
Concept ID:
C5236092
Neoplastic Process
Synonyms: Infiltrating Urothelial Carcinoma, Sarcomatoid Variant; Invasive Urothelial Carcinoma, Sarcomatoid Variant

Definition

An invasive urothelial carcinoma that exhibits spindle cell sarcomatoid features. [from NCI]

Professional guidelines

PubMed

Vlachou E, Johnson BA 3rd, Baraban E, Nadal R, Hoffman-Censits J
Am Soc Clin Oncol Educ Book 2024 Jun;44(3):e438640. doi: 10.1200/EDBK_438640. PMID: 38870453
Veskimäe E, Espinos EL, Bruins HM, Yuan Y, Sylvester R, Kamat AM, Shariat SF, Witjes JA, Compérat EM
Eur Urol Oncol 2019 Nov;2(6):625-642. Epub 2019 Oct 8 doi: 10.1016/j.euo.2019.09.003. PMID: 31601522
Porten SP, Willis D, Kamat AM
Curr Opin Urol 2014 Sep;24(5):517-23. doi: 10.1097/MOU.0000000000000089. PMID: 24921905

Recent clinical studies

Etiology

Claps F, van de Kamp MW, Mayr R, Bostrom PJ, Shariat SF, Hippe K, Bertz S, Neuzillet Y, Sanders J, Otto W, van der Heijden MS, Jewett MAS, Stöhr R, Zlotta AR, Trombetta C, Eckstein M, Mertens LS, Burger M, Soorojebally Y, Wullich B, Bartoletti R, Radvanyi F, Pavan N, Sirab N, Mir MC, Pouessel D, van der Kwast TH, Hartmann A, Lotan Y, Bussani R, Allory Y, van Rhijn BWG
BJU Int 2023 Aug;132(2):170-180. Epub 2023 Feb 20 doi: 10.1111/bju.15984. PMID: 36748180
Diamantopoulos LN, Korentzelos D, Alevizakos M, Wright JL, Grivas P, Appleman LJ
Clin Genitourin Cancer 2022 Apr;20(2):139-147. Epub 2021 Dec 24 doi: 10.1016/j.clgc.2021.12.015. PMID: 35101380
Hoffman-Censits JH, Lombardo KA, Parimi V, Kamanda S, Choi W, Hahn NM, McConkey DJ, McGuire BM, Bivalacqua TJ, Kates M, Matoso A
Appl Immunohistochem Mol Morphol 2021 Sep 1;29(8):619-625. doi: 10.1097/PAI.0000000000000938. PMID: 33901032Free PMC Article
Lobo N, Shariat SF, Guo CC, Fernandez MI, Kassouf W, Choudhury A, Gao J, Williams SB, Galsky MD, Taylor JA 3rd, Roupret M, Kamat AM
Eur Urol Focus 2020 Jul 15;6(4):653-663. Epub 2019 Sep 15 doi: 10.1016/j.euf.2019.09.003. PMID: 31530497
Amin MB
Mod Pathol 2009 Jun;22 Suppl 2:S96-S118. doi: 10.1038/modpathol.2009.26. PMID: 19494856

Diagnosis

Guo CC, Lee S, Lee JG, Chen H, Zaleski M, Choi W, McConkey DJ, Wei P, Czerniak B
Nat Rev Urol 2024 Jul;21(7):391-405. Epub 2024 Feb 6 doi: 10.1038/s41585-023-00847-7. PMID: 38321289
Claps F, van de Kamp MW, Mayr R, Bostrom PJ, Shariat SF, Hippe K, Bertz S, Neuzillet Y, Sanders J, Otto W, van der Heijden MS, Jewett MAS, Stöhr R, Zlotta AR, Trombetta C, Eckstein M, Mertens LS, Burger M, Soorojebally Y, Wullich B, Bartoletti R, Radvanyi F, Pavan N, Sirab N, Mir MC, Pouessel D, van der Kwast TH, Hartmann A, Lotan Y, Bussani R, Allory Y, van Rhijn BWG
BJU Int 2023 Aug;132(2):170-180. Epub 2023 Feb 20 doi: 10.1111/bju.15984. PMID: 36748180
Gandhi J, Chen JF, Al-Ahmadie H
Surg Pathol Clin 2022 Dec;15(4):641-659. Epub 2022 Oct 13 doi: 10.1016/j.path.2022.07.003. PMID: 36344181Free PMC Article
Lobo N, Shariat SF, Guo CC, Fernandez MI, Kassouf W, Choudhury A, Gao J, Williams SB, Galsky MD, Taylor JA 3rd, Roupret M, Kamat AM
Eur Urol Focus 2020 Jul 15;6(4):653-663. Epub 2019 Sep 15 doi: 10.1016/j.euf.2019.09.003. PMID: 31530497
Amin MB
Mod Pathol 2009 Jun;22 Suppl 2:S96-S118. doi: 10.1038/modpathol.2009.26. PMID: 19494856

Therapy

Fuu T, Iijima K, Kusama Y, Otsuki T, Kato H
J Med Case Rep 2022 May 18;16(1):193. doi: 10.1186/s13256-022-03426-3. PMID: 35581611Free PMC Article
Au S, Keyes M, Black P, Villamil CF, Tavassoli P
Pathol Res Pract 2020 Mar;216(3):152822. Epub 2020 Jan 10 doi: 10.1016/j.prp.2020.152822. PMID: 31982182
Nagumo Y, Kojima T, Shiga M, Kandori S, Kimura T, Takaoka EI, Onozawa M, Miyazaki J, Kawai K, Ishikawa H, Sakurai H, Nishiyama H
Int J Clin Oncol 2020 Feb;25(2):354-361. Epub 2019 Oct 8 doi: 10.1007/s10147-019-01553-4. PMID: 31595343
Berg S, D'Andrea D, Vetterlein MW, Cole AP, Fletcher SA, Krimphove MJ, Marchese M, Lipsitz SR, Sonpavde G, Noldus J, Shariat SF, Kibel AS, Trinh QD, Mossanen M
Cancer 2019 May 1;125(9):1449-1458. Epub 2019 Jan 8 doi: 10.1002/cncr.31952. PMID: 30620387
Behzatoğlu K, Yörükoğlu K, Demir H, Bal N
Eur Urol Focus 2018 Apr;4(3):399-404. Epub 2016 Jun 21 doi: 10.1016/j.euf.2016.06.007. PMID: 28753766

Prognosis

Claps F, van de Kamp MW, Mayr R, Bostrom PJ, Shariat SF, Hippe K, Bertz S, Neuzillet Y, Sanders J, Otto W, van der Heijden MS, Jewett MAS, Stöhr R, Zlotta AR, Trombetta C, Eckstein M, Mertens LS, Burger M, Soorojebally Y, Wullich B, Bartoletti R, Radvanyi F, Pavan N, Sirab N, Mir MC, Pouessel D, van der Kwast TH, Hartmann A, Lotan Y, Bussani R, Allory Y, van Rhijn BWG
BJU Int 2023 Aug;132(2):170-180. Epub 2023 Feb 20 doi: 10.1111/bju.15984. PMID: 36748180
Sanguedolce F, Calò B, Mancini V, Zanelli M, Palicelli A, Zizzo M, Ascani S, Carrieri G, Cormio L
Oncology 2021;99(6):345-358. Epub 2021 Mar 18 doi: 10.1159/000514759. PMID: 33735905
Lobo N, Shariat SF, Guo CC, Fernandez MI, Kassouf W, Choudhury A, Gao J, Williams SB, Galsky MD, Taylor JA 3rd, Roupret M, Kamat AM
Eur Urol Focus 2020 Jul 15;6(4):653-663. Epub 2019 Sep 15 doi: 10.1016/j.euf.2019.09.003. PMID: 31530497
Porten SP, Willis D, Kamat AM
Curr Opin Urol 2014 Sep;24(5):517-23. doi: 10.1097/MOU.0000000000000089. PMID: 24921905
Amin MB
Mod Pathol 2009 Jun;22 Suppl 2:S96-S118. doi: 10.1038/modpathol.2009.26. PMID: 19494856

Clinical prediction guides

Matsuda A, Taoka R, Miki J, Saito R, Fukuokaya W, Hatakeyama S, Kawahara T, Fujii Y, Kato M, Sazuka T, Sano T, Urabe F, Kashima S, Naito H, Murakami Y, Miyake M, Daizumoto K, Matsushita Y, Hayashi T, Inokuchi J, Sugino Y, Shiga K, Yamaguchi N, Iio H, Yasue K, Abe T, Nakanishi S, Matsumura M, Fujii M, Nishihara K, Matsumoto H, Tatarano S, Wada K, Sekito S, Maruyama R, Nishiyama N, Nishiyama H, Kitamura H, Matsui Y; Japanese Urological Oncology Group
BJU Int 2024 Aug;134(2):207-218. Epub 2024 Feb 12 doi: 10.1111/bju.16296. PMID: 38344879
Claps F, van de Kamp MW, Mayr R, Bostrom PJ, Shariat SF, Hippe K, Bertz S, Neuzillet Y, Sanders J, Otto W, van der Heijden MS, Jewett MAS, Stöhr R, Zlotta AR, Trombetta C, Eckstein M, Mertens LS, Burger M, Soorojebally Y, Wullich B, Bartoletti R, Radvanyi F, Pavan N, Sirab N, Mir MC, Pouessel D, van der Kwast TH, Hartmann A, Lotan Y, Bussani R, Allory Y, van Rhijn BWG
BJU Int 2023 Aug;132(2):170-180. Epub 2023 Feb 20 doi: 10.1111/bju.15984. PMID: 36748180
Hoffman-Censits JH, Lombardo KA, Parimi V, Kamanda S, Choi W, Hahn NM, McConkey DJ, McGuire BM, Bivalacqua TJ, Kates M, Matoso A
Appl Immunohistochem Mol Morphol 2021 Sep 1;29(8):619-625. doi: 10.1097/PAI.0000000000000938. PMID: 33901032Free PMC Article
Sanguedolce F, Calò B, Mancini V, Zanelli M, Palicelli A, Zizzo M, Ascani S, Carrieri G, Cormio L
Oncology 2021;99(6):345-358. Epub 2021 Mar 18 doi: 10.1159/000514759. PMID: 33735905
Shah TS, Kaag M, Raman JD, Chan W, Tran T, Kunchala S, Shuman L, DeGraff DJ, Chen G, Warrick JI
Hum Pathol 2017 Mar;61:90-96. Epub 2016 Nov 4 doi: 10.1016/j.humpath.2016.10.021. PMID: 27818288

Recent systematic reviews

Yu Y, Wang Y, Wu Q, Zhao X, Liu D, Zhao Y, Li Y, Wang G, Xu J, Chen J, Zhang N, Tian X
Front Endocrinol (Lausanne) 2021;12:793718. Epub 2021 Dec 15 doi: 10.3389/fendo.2021.793718. PMID: 34975762Free PMC Article
Veskimäe E, Espinos EL, Bruins HM, Yuan Y, Sylvester R, Kamat AM, Shariat SF, Witjes JA, Compérat EM
Eur Urol Oncol 2019 Nov;2(6):625-642. Epub 2019 Oct 8 doi: 10.1016/j.euo.2019.09.003. PMID: 31601522

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