Wilms tumor 6

Synonyms: WILMS TUMOR 6, SUSCEPTIBILITY TO

Summary

Wilms tumor is the most common renal tumor of childhood, occurring with an incidence of 1 in 10,000. It is often described as an embryonal tumor, as it arises from embryonal cells in which growth and/or differentiation have become dysregulated during development (summary by Mahamdallie et al., 2015). For a general phenotypic description and discussion of genetic heterogeneity of Wilms tumor, see WT1 (194070). [from OMIM]

Available tests

12 tests are in the database for this condition.

Check Related conditions for additional relevant tests.

Clinical tests (12 available)

Molecular Genetics Tests

Genes See tests for all associated and related genes

Associated genes Help
Genes reported to contribute to the condition.

REST
Also known as: DFNA27, GINGF5, HGF5, NRSF, WT6, XBR, REST
Summary: RE1 silencing transcription factor

Imported from Human Phenotype Ontology (HPO)

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Neoplasm
- Nephroblastoma
  Nephroblastoma
  - MedGen UID: 10221
  - Concept ID: C0027708
  - Finding: Neoplastic Process
  Neoplasm
  See: Feature record | Search on this feature

Reviews

Clinical resources

Practice guidelines

NCCN, 2023
NCCN Clinical Practice Guidelines in Oncology (NCCN Guidelines®), Wilms Tumor (Nephroblastoma), 2023

Molecular resources

Consumer resources

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