Angiomatosis, diffuse Corticomeningeal, of Divry and van Bogaert
- Synonyms
- Corticomeningeal angiomatosis, myelination of the white substance of the centrum ovale, hemianopsia and marbled skin; DIVRY-VAN BOGAERT SYNDROME
Clinical features
Help- Abnormality of the cardiovascular system
- Hypertensive disorder
Hypertensive disorder
- MedGen UID: 6969
- Concept ID: C0020538
- Finding: Disease or Syndrome
Abnormality of the cardiovascular system
- Hypertensive disorder
- Abnormality of the eye
- Hemianopia
Hemianopia
- MedGen UID: 9193
- Concept ID: C0018979
- Finding: Finding
Abnormality of the eye
- Visual field defect
Visual field defect
- MedGen UID: 854603
- Concept ID: C3887875
- Finding: Finding
Abnormality of the eye
- Hemianopia
- Abnormality of the integument
- Cutis marmorata
Cutis marmorata
- MedGen UID: 78093
- Concept ID: C0263401
- Finding: Disease or Syndrome
Abnormality of the integument
- Telangiectases producing 'marbled' skin
Telangiectases producing 'marbled' skin
- MedGen UID: 870394
- Concept ID: C4024839
- Finding: Finding
Abnormality of the integument
- Cutis marmorata
- Abnormality of the nervous system
- Aplasia/Hypoplasia involving the central nervous system
Aplasia/Hypoplasia involving the central nervous system
- MedGen UID: 871188
- Concept ID: C4025665
- Finding: Finding
Abnormality of the nervous system
- Brain atrophy
Brain atrophy
- MedGen UID: 1643639
- Concept ID: C4551584
- Finding: Disease or Syndrome
Abnormality of the nervous system
- Broad-based gait
Broad-based gait
- MedGen UID: 167799
- Concept ID: C0856863
- Finding: Finding
Abnormality of the nervous system
- Cerebellar ataxia
Cerebellar ataxia
- MedGen UID: 849
- Concept ID: C0007758
- Finding: Disease or Syndrome
Abnormality of the nervous system
- Dementia
Dementia
- MedGen UID: 99229
- Concept ID: C0497327
- Finding: Mental or Behavioral Dysfunction
Abnormality of the nervous system
- Dysarthria
Dysarthria
- MedGen UID: 8510
- Concept ID: C0013362
- Finding: Mental or Behavioral Dysfunction
Abnormality of the nervous system
- Emotional lability
Emotional lability
- MedGen UID: 39319
- Concept ID: C0085633
- Finding: Mental or Behavioral Dysfunction
Abnormality of the nervous system
- Migraine
Migraine
- MedGen UID: 57451
- Concept ID: C0149931
- Finding: Disease or Syndrome
Abnormality of the nervous system
- Pseudobulbar signs
Pseudobulbar signs
- MedGen UID: 374006
- Concept ID: C1838579
- Finding: Sign or Symptom
Abnormality of the nervous system
- Seizure
Seizure
- MedGen UID: 20693
- Concept ID: C0036572
- Finding: Sign or Symptom
Abnormality of the nervous system
- Ventriculomegaly
Ventriculomegaly
- MedGen UID: 480553
- Concept ID: C3278923
- Finding: Finding
Abnormality of the nervous system
- Aplasia/Hypoplasia involving the central nervous system
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