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GM20190 male affected Marveld2 sample

Identifiers
BioSample: SAMN00805716; Coriell: GM20190; Coriell: NA20190
Organism
Homo sapiens (human)
cellular organisms; Eukaryota; Opisthokonta; Metazoa; Eumetazoa; Bilateria; Deuterostomia; Chordata; Craniata; Vertebrata; Gnathostomata; Teleostomi; Euteleostomi; Sarcopterygii; Dipnotetrapodomorpha; Tetrapoda; Amniota; Mammalia; Theria; Eutheria; Boreoeutheria; Euarchontoglires; Primates; Haplorrhini; Simiiformes; Catarrhini; Hominoidea; Hominidae; Homininae; Homo
Attributes
cell lineGM20190
sexMale
cell typeB-Lymphocyte
family id2458
family roleproband
raceEast Indian
ethnicityPAKISTANI
age25 YR
DNA-IDNA20190
GeneMARVELD2
affected_byMarveld2
MutationIVS3-1G>A
collectionNIGMS Human Genetic Cell Repository
Tags
DFNB49
Marvel domain-containing protein 2
Deafness autosomal recessive 49
Marveld2
Description

Clinically affected;hearing loss confirmed by audiometry;product of consanguineous marriage;two affected siblings;father is GM20191;donor subject is homozygous for a splice site mutation: IVS3-1G>A causes the use of a cryptic splice-acceptor site within exon 4 of the MARVELD2 (TRIC) gene which results in the deletion of the first 17 nt of exon 4 and a nonsense mutation (p.C395fsX396)

Submission
Coriell; 2012-03-05
Accession:
SAMN00805716
ID:
805716

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