ZFYVE21 is a complement-induced Rab5 effector that activates non-canonical NF-κB via phosphoinosotide remodeling of endosomes

Nat Commun. 2019 May 21;10(1):2247. doi: 10.1038/s41467-019-10041-2.

Abstract

Complement promotes vascular inflammation in transplant organ rejection and connective tissue diseases. Here we identify ZFYVE21 as a complement-induced Rab5 effector that induces non-canonical NF-κB in endothelial cells (EC). In response to membrane attack complexes (MAC), ZFYVE21 is post-translationally stabilized on MAC+Rab5+ endosomes in a Rab5- and PI(3)P-dependent manner. ZFYVE21 promotes SMURF2-mediated polyubiquitinylation and proteasome-dependent degradation of endosome-associated PTEN to induce vesicular enrichment of PI(3,4,5)P3 and sequential recruitment of activated Akt and NF-κB-inducing kinase (NIK). Pharmacologic alteration of cellular phosphoinositide content with miltefosine reduces ZFYVE21 induction, EC activation, and allograft vasculopathy in a humanized mouse model. ZFYVE21 induction distinctly occurs in response to MAC and is detected in human renal and synovial tissues. Our data identifies ZFYVE21 as a Rab5 effector, defines a Rab5-ZFYVE21-SMURF2-pAkt axis by which it mediates EC activation, and demonstrates a role for this pathway in complement-mediated conditions.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Allografts / pathology
  • Animals
  • Carrier Proteins / metabolism*
  • Cell Line
  • Complement Membrane Attack Complex / metabolism
  • Coronary Vessels / pathology
  • Coronary Vessels / transplantation
  • Disease Models, Animal
  • Endosomes / metabolism*
  • Female
  • Graft Rejection / pathology*
  • Human Umbilical Vein Endothelial Cells
  • Humans
  • Intracellular Signaling Peptides and Proteins
  • Membrane Proteins
  • Mice
  • Mice, SCID
  • NF-kappa B / metabolism*
  • Phosphatidylinositol Phosphates / metabolism
  • Ubiquitin-Protein Ligases / metabolism
  • Vasculitis / pathology*
  • rab5 GTP-Binding Proteins / metabolism

Substances

  • Carrier Proteins
  • Complement Membrane Attack Complex
  • Intracellular Signaling Peptides and Proteins
  • Membrane Proteins
  • NF-kappa B
  • Phosphatidylinositol Phosphates
  • ZFYVE21 protein, human
  • SMURF2 protein, human
  • Ubiquitin-Protein Ligases
  • RAB5C protein, human
  • rab5 GTP-Binding Proteins